An Unexpected Hepatic Hydrothorax After a Successful Kasai Portoenterostomy: A Case Report [PDF]
Frontiers in Pediatrics, 2021 Hepatic hydrothorax (HH) represents a rare complication of portal hypertension among adult cirrhotic patients. Here, we describe a pediatric case of HH, observed in a biliary atresia infant. The child presented with recurrent right-sided pleural effusion,
Giulia Ranucci +5 more
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Upregulated beta-defensin-1 in murine and human biliary atresia associates with human native liver survival [PDF]
Scientific ReportsBiliary atresia (BA) is a neonatal cholangiopathy that often progresses to cirrhosis despite timely Kasai portoenterostomy (KPE), and prognostic biomarkers remain undefined.
Christoph Slavetinsky +10 more
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Early Kasai portoenterostomy in a 9-day-old newborn with extrahepatic biliary atresia: a case report highlighting improved prognosis with prompt intervention [PDF]
Journal of International Medical ResearchExtrahepatic biliary atresia (EHBA) is a leading cause of neonatal cholestasis, often resulting in end-stage cirrhosis and portal hypertension without early diagnosis and treatment. This report highlights the importance of timely intervention, describing
Mortada H.F. El-Shabrawi +8 more
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PostKasai Portoenterostomy Dissection of a Branch of the Right Hepatic Artery – A Rare Complication
Journal of Indian Association of Pediatric SurgeonsHepatic artery branch dissection is a lesser-known complication after biliary atresia surgery. The presentation is massive upper gastrointestinal bleeding and rapid drop in hemoglobin levels.
Charu Sharma +4 more
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Prognostic Outcomes by Ishak Fibrosis Score Grouping in Biliary Atresia After Kasai Surgery [PDF]
International Journal of General MedicineLu Huang,1,2 Yong-Xing Hao,1,2 Cheng-Yan Tang,1,2 Xing-Rong Xia,1,2 Ze-Bing Zheng,1,2 Qing Du,1,2 Yuan Gong,1,2 Wan-Kang Zhou,1,2 Dai-Wei Zhu,1,2 Ze-Ping Li,1,2 Meng-Dan Leng,1,2 Yuan-Mei Liu,1,2 Zhu Jin1,2 1Pediatric Surgery Department, Affiliated ...
Huang L +12 more
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Hepatology Communications, 2021 Successful portoenterostomy (SPE) improves the short‐term outcome of patients with biliary atresia (BA) by relieving cholestasis and extending survival with native liver. Despite SPE, hepatic fibrosis progresses in most patients, leading to cirrhosis and
Antti Kyrönlahti +11 more
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Cystic biliary anomaly in a newborn with features of choledochal cyst and cystic biliary atresia
Journal of Pediatric Surgery Case Reports, 2021 Cystic biliary atresia (CBA) and choledochal cysts (CDC) can present similarly with early onset jaundice, conjugated hyperbilirubinemia, and radiographic cystic biliary dilatations. We present the case of an infant antenatally diagnosed with a congenital
C.L. Berkowitz +5 more
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Current and emerging adjuvant therapies in biliary atresia
Frontiers in Pediatrics, 2022 Following Kasai hepatic portoenterostomy (HPE), most patients with biliary atresia will eventually require liver transplantation due to progressive cirrhosis and liver failure.
Scott C. Fligor +4 more
doaj +1 more source
Vanishing prenatal sub-hepatic cyst associated with biliary atresia: A case report
Journal of Pediatric Surgery Case Reports, 2023 Introduction: Biliary atresia (BA) is the result of a progressive obliterative cholangiopathy that begins in the perinatal period. Cystic BA (CBA) is a subtype of BA that can be misdiagnosed easily as a choledochal cyst (CC) during the prenatal period ...
Seung Won Burm +6 more
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Frontiers in Pediatrics, 2022 IntroductionThe accurate assessment of the stages of hepatic fibrosis in children with biliary atresia (BA) before performing Kasai portoenterostomy (KPE) is of utmost importance.
Xingxing Duan +7 more
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