Progressive systemic sclerosis in a child
Indian Journal of Dermatology, 2013 Systemic sclerosis is a clinically heterogeneous systemic disease affecting the connective tissues of skin, walls of blood vessels and internal organs like lung, heart and kidneys. Systemic sclerosis is very unusual in pediatric population.
Arun K De +3 more
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Treatment of rapidly progressive systemic sclerosis: current and futures perspectives [PDF]
Expert Opin Orphan Drugs, 2015 Fabian A. Mendoza +2 more
europepmc +3 more sources
Autologous stem cell transplantation for progressive systemic sclerosis: a prospective non-interventional study from the European Society for Blood and Marrow Transplantation Autoimmune Disease Working Party. [PDF]
Haematologica, 2021 Three randomized controlled trials in early severe systemic sclerosis demonstrated that autologous hematopoietic stem cell transplantation was superior to standard cyclophosphamide therapy.
Henes J +22 more
europepmc +2 more sources
Pictorial review of intrathoracic manifestations of progressive systemic sclerosis
Annals of Thoracic Medicine, 2014 Intra-thoracic manifestations of progressive systemic sclerosis (PSS) are not well known particularly the imaging features, which forms the basis of accurate and timely diagnosis.
AliNawaz Khan +4 more
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Esophageal involvement in progressive systemic sclerosis [PDF]
Autopsy and Case Reports, 2013 Progressive systemic sclerosis (PSSc) is a chronic disease of unknown etiology characterized by progressive, abnormal accumulation of fibrous tissue in the skin and many organs.
Stephen A. Geller +1 more
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Favorable long term effects of intensified immunosuppression combined with therapeutic plasma exchange in patients with early-onset progressive systemic sclerosis-related interstitial lung disease [PDF]
J Transl Autoimmun, 2022 Judith Potjewijd +5 more
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Neuroaxial anesthesia in a patient with progressive systemic sclerosis : case presentation and review of the literature on systemic sclerosis [PDF]
BMC Anesthesiology, 2006 Background Systemic sclerosis (SSc), a progressive disease characterized by excessive accumulation of connective tissue components. Although most patients have long survival, some of them progress rapidly to death.
Gülcan Erk +3 more
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Severe Osteolysis of the Mandibular Angle and Total Condylolysis in Progressive Systemic Sclerosis [PDF]
Case Rep Dent, 2013 Amin Rahpeyma +2 more
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Acta Dermato-Venereologica, 2014 Angiopoietin-like protein 3 (ANGPTL3), which is part of a family of secreted glycoproteins that are structurally similar to angiopoietins, is principally expressed in the liver and is involved in lipid metabolism and angiogenesis.
Yohei Ichimura +14 more
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Therapeutic options for the treatment of interstitial lung diseases in systemic rheumatic diseases – systemic sclerosis as an example [PDF]
Liječnički vjesnik, 2022 Systemic sclerosis is a multisystem autoimmune disorder characterized by widespread fibrosis, primarily of the skin but also of the lung parenchyma. Interstitial lung disease is one of the most severe manifestations of the disease and a leading cause of ...
Marko Barešić, Branimir Anić
doaj +1 more source