Pulmonary artery pathologies in Alagille syndrome: a meta-analysis
Advances in Interventional Cardiology, 2022 Alagille syndrome, caused by mutations in the gene encoding Jagged1 (JAG1), a ligand in the Notch signaling pathway, is an autosomal dominant disorder with developmental abnormalities affecting the liver, heart, eyes, face and skeleton.
Shi-Min Yuan
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Arquivos Brasileiros de Cardiologia, 2003 OBJECTIVE: To evaluate the cardiovascular findings and clinical follow-up of patients with Williams-Beuren syndrome. METHODS: We studied 20 patients (11 males, mean age at diagnosis: 5.9 years old), assessed for cardiovascular abnormalities with ...
Sofia Mizuho Miura Sugayama +8 more
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Pulmonary Vein Stenosis in a Newborn: A Commonly Overlooked Diagnosis
Case Reports in Cardiology, 2015 The diagnosis of primary pulmonary vein stenosis is often overlooked because its symptoms overlap lung diseases and pulmonary arterial hypertension. Its diagnosis may be difficult because the condition is progressive and associated with other defects. We
Nathalie Jeanne Magioli Bravo-valenzuela +2 more
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The many faces and outcomes of pulmonary vein stenosis in early childhood. [PDF]
, 2021 Pulmonary vein stenosis is a rare and poorly understood condition causing obstruction of the large pulmonary veins and of blood flow from the lungs to the left atrium.
Tilman Humpl +5 more
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Interventional treatment for pulmonary venous stenosis due to fibrosing mediastinitis: a case report
Frontiers in Cardiovascular MedicineIntroductionFibrosing mediastinitis is a rare syndrome caused by the abnormal proliferation of mediastinal fibrous tissue. It often causes superior vena cava syndrome, bronchial stenosis, pulmonary vascular stenosis, etc.Patient presentationAn elderly ...
Runfeng Gao +4 more
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Cost-utility of transcatheter aortic valve implantation for inoperable patients with severe aortic stenosis treated by medical management: a UK cost-utility analysis based on patient-level data from the ADVANCE study. [PDF]
, 2014 OBJECTIVE: To use patient-level data from the ADVANCE study to evaluate the cost-effectiveness of transcatheter aortic valve implantation (TAVI) compared to medical management (MM) in patients with severe aortic stenosis from the perspective of the UK ...
Busca, R +32 more
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Dilatation of the Pulmonary Artery in Pulmonary Stenosis [PDF]
Circulation, 1956 Dilatation of the pulmonary artery occurs frequently in cases of valvular pulmonary stenosis and is often called "poststenotic." We determined the diameter of the pulmonary artery angiocardiographically and compared this with the data obtained by heart catheterization in cases of pulmonary stenosis and of idiopathic dilatation of the pulmonary artery ...
openaire +3 more sources
LES of non-Newtonian physiological blood flow in a model of arterial stenosis [PDF]
, 2012 Large Eddy Simulation (LES) is performed to study the physiological pulsatile transition-to-turbulent non-Newtonian blood flow through a 3D model of arterial stenosis by using five different blood viscosity models: (i) Power-law, (ii) Carreau, (iii ...
Molla, M.M. +3 more
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A case control investigation of the relation between hyperlipidaemia and calcific aortic valve stenosis [PDF]
, 1997 Objective To investigate the relation of hyperlipidaemia to calcific aortic valve stenosis. Design A case-control study designed to detect a clinically relevant difference in the fasting plasma concentrations of total cholesterol between the groups at ...
Stevenson, R N +3 more
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Acta Veterinaria Scandinavica, 2017 Background Congenital pulmonary valve stenosis and patent ductus arteriosus are common congenital heart defects in dogs. However, concurrence of atypical pulmonary valve stenosis and patent ductus arteriosus is uncommon.
Hakyoung Yoon +3 more
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