Results 41 to 50 of about 40,981 (269)
由道 宮﨑+2 more
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Is Ross Syndrome a New Type of Synucleinopathy? A Brief Research Report
Ross syndrome (RS) is a rare peripheral autonomic system disorder characterized by tonic pupil, hyporeflexia, and segmental anhidrosis. Neuropathological studies show that RS results from the selective cholinergic nerve degeneration.
Mingming Ma+19 more
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Pure autonomic failure followed by amyotrophy [PDF]
Features of autonomic dysfunction may develop late in amyotrophic lateral sclerosis (ALS), but pure autonomic failure with subsequent amyotrophy has not been recognized. We report the rare combination of pure autonomic failure followed by gradually progressive, isolated anterior horn cell disease.
Irani, SR, Mathias, C, Orrell, R
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I-Metaiodobenzylguanidine Myocardial Scintigraphy in Lewy Body-Related Disorders: A Literature Review [PDF]
Lewy body-related disorders are characterized by the presence of Lewy bodies and Lewy neurites, which have abnormal aggregations of α-synuclein in the nigral and extranigral areas, including in the heart.
Eun Joo Chung, Sang Jin Kim
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Report of an early case of Shy-Drager syndrome in a 67 year-old woman patient. Autonomic failure was diagnosed by functional evaluation as well as laboratory tests. MR imaging disclosed a prominent putamina hypodensity in T2-weighted images at high field
Jayme A. Maciel Jr.+3 more
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Passive Immunization in Alpha-Synuclein Preclinical Animal Models
Alpha-synucleinopathies include Parkinson’s disease, dementia with Lewy bodies, pure autonomic failure and multiple system atrophy. These are all progressive neurodegenerative diseases that are characterized by pathological misfolding and accumulation of
Jonas Folke+4 more
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Background Discerning the mechanisms driving orthostatic symptoms in human beings remains challenging. Therefore, we developed a novel approach combining cardiac and cerebral real‐time magnetic resonance imaging, beat‐to‐beat physiological monitoring ...
Darius A. Gerlach+10 more
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Background Orthostatic hypotension (OH) in geriatric patients frequently involves a component of autonomic failure (AF). The combination of OH with nocturnal hypertension (NHT) is indicative of AF, which is described as pure (PAF), when neurologic ...
Siddhartha Lieten+3 more
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Congenital Insensitivity to Pain (HSNA type IV)
Investigators from New York University, NY, studied 14 patients with congenital insensitivity to pain with anhidrosis (CIPA), compared to 10 patients with chronically deficient sympathetic activity (pure autonomic failure), and 15 normal age-matched ...
J Gordon Millichap
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