Variably Protease‐Sensitive Prionopathy: Two New Cases With Motor Neuron‐Dementia Syndrome
ABSTRACT We describe two patients with variably protease‐sensitive prionopathy (VPSPr) who developed progressive upper motor neuron symptoms, insomnia, behavioral and cognitive decline, compatible with primary lateral sclerosis associated with frontotemporal dementia (FTD).
María Elena Erro +10 more
wiley +1 more source
Brasil: Globalização e Regionalização
Resumo O processo de globalização não é um processo recente, e vem sempre associado a distintas dinâmicas de regionalização. No caso brasileiro, sua inserção aos circuitos globais começa no período colonial, e diferentes regionalizações vão se ...
Manuel Correia de Andrade
doaj +1 more source
REGIONAL THEORY AND REGIONAL MODELS
The ideas outlined in this paper are tentative and only partially developed. They have arisen very much as a response to the deficiencies in existing regional models. Whether this particular structure can lead to added order and power in such models remains to be demonstrated.
openaire +1 more source
Reorganizing Corrections: Revisiting the Recommendations of the National Advisory Commission [PDF]
In 1973 the National Advisory Commission on Standards and Goals recommended that correctional services be consolidated under a single state agency, arguing that cost efficiencies, improved communication, and greater employee professionalism would result.
Schafer, N. E.
core
Neuropsychiatric Symptoms Mimicking Dementia in a Patient Treated With Imatinib
ABSTRACT Tyrosine kinase inhibitors are the cornerstone of chronic myeloid leukemia treatment. Newer agents have more potency and a broader spectrum of action, but also a higher potential for neuropsychiatric side effects. We present a case of a patient on imatinib who developed progressive cognitive, mood, and behavioral alterations.
Ashley Jones +3 more
wiley +1 more source
Reducing uncertainty in the american community survey through data-driven regionalization.
The American Community Survey (ACS) is the largest survey of US households and is the principal source for neighborhood scale information about the US population and economy.
Seth E Spielman, David C Folch
doaj +1 more source
Predicting Loss of Ambulation in Limb Girdle Muscular Dystrophy R9
ABSTRACT Background Limb girdle muscular dystrophy type R9 (LGMDR9) results from biallelic variants in FKRP. There is limited data to predict loss of ambulation (LOA) among those with LGMDR9. Methods Participants in an ongoing dystroglycanopathy natural history study (NCT00313677) with FKRP variants who had achieved ambulation and were more than 3 ...
Chandra L. Miller +6 more
wiley +1 more source
Latihan mengajar : Keberkesanannya terhadap pelajar Diploma Kejuruteraan serta Pendidikan di KUiTTHO (Kolej Universiti Teknologi Tun Hussein Onn) menurut persepsi pelajar [PDF]
Kajian yang dijaiankan adaiah bertajuk "Latihan Mengajar : Kebersanannya Terhadap Pelajar Diploma Kejuruteraan berserta Pendidikan di KUiTTHO (Kolej Universiti Teknologi Tun Hussein Onn Menurut Persepsi Pelajar.
Jamian, Yuhani
core
Real‐World Performance of CSF Kappa Free Light Chains in the 2024 McDonald Criteria
ABSTRACT Objective Kappa free light chains (KFLCs) in the cerebrospinal fluid (CSF) have a similar performance to CSF‐restricted oligoclonal bands (OCB) for multiple sclerosis (MS) diagnosis. To help with implementation, we set out to resolve several remaining uncertainties: (1) performance in a real‐world cohort and the 2024 McDonald criteria; (2 ...
Maya M. Leibowitz +11 more
wiley +1 more source
Whole‐Body Pattern of Muscle Degeneration and Progression in Sarcoglycanopathies
ABSTRACT Objective To characterize whole‐body intramuscular fat distribution pattern in patients with sarcoglycanopathies and explore correlations with disease severity, duration and age at onset. Methods Retrospective, cross‐sectional, multicentric study enrolling patients with variants in one of the four sarcoglycan genes who underwent whole‐body ...
Laura Costa‐Comellas +39 more
wiley +1 more source

