Results 61 to 70 of about 524 (73)

ALS/FTD-Linked Mutation in FUS Suppresses Intra-axonal Protein Synthesis and Drives Disease Without Nuclear Loss-of-Function of FUS

Neuron, 2018
Takahiro Tadokoro, Michael Baughn, Jinsong Qiu   +2 more
exaly  

ALS‐associated fused in sarcoma (FUS) mutations disrupt Transportin‐mediated nuclear import

EMBO Journal, 2010
Dorothee Dörmann, Dieter Edbauer, Manuel E Than   +2 more
exaly  

Pathological heterogeneity in amyotrophic lateral sclerosis with FUS mutations: two distinct patterns correlating with disease severity and mutation

Acta Neuropathologica, 2011
Ian R Mackenzie, Olaf Ansorge, Michael J Strong   +2 more
exaly  

FUS pathology defines the majority of tau- and TDP-43-negative frontotemporal lobar degeneration

Acta Neuropathologica, 2010
Keith A Josephs, Jonathan D Rohrer, Ian R Mackenzie   +2 more
exaly  

FUS Regulates Activity of MicroRNA-Mediated Gene Silencing

Molecular Cell, 2018
Yon Ju Ji, Honghe Liu, Amit Arora
exaly  

De novo truncating FUS gene mutation as a cause of sporadic amyotrophic lateral sclerosis

Human Mutation, 2010
Mariely Dejesus-Hernandez, Matt Baker, Aleksandra Wojtas   +2 more
exaly  

Toxic gain of function from mutant FUS protein is crucial to trigger cell autonomous motor neuron loss

EMBO Journal, 2016
Stéphane Dieterle, Jinsong Qiu, Yu Zhou   +2 more
exaly  

FUS interacts with ATP synthase beta subunit and induces mitochondrial unfolded protein response in cellular and animal models

Proceedings of the National Academy of Sciences of the United States of America, 2018
Jianwen Deng, Kazuo Fushimi, Li Zhu
exaly  

FUS stimulates microRNA biogenesis by facilitating co‐transcriptional Drosha recruitment

EMBO Journal, 2012
Mariangela Morlando, Alessandro Rosa, Valerio Di Carlo   +2 more
exaly  

Nuclear localization sequence of FUS and induction of stress granules by ALS mutants

Neurobiology of Aging, 2011
József Gal, Hongge Jia, Jianhang Jia
exaly