Introduction Sinus histiocytosis with massive lymphadenopathy, also known as Rosai-Dorfman Disease, is a rare and benign source of lymphadenopathy first described in 1969, which mimics neoplastic processes.
Moore James C +2 more
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Rosai-Dorfman disease mimicking images of meningiomas: Two case reports and literature review
Background: Rosai-Dorfman disease (RDD) is a rare non-Langerhans cell histiocytic proliferative disorder classically as a massive cervical lymphadenopathy.
R. Tatit +6 more
semanticscholar +1 more source
NRAS Mutations May Be Involved in the Pathogenesis of Cutaneous Rosai Dorfman Disease: A Pilot Study
Background: Purely cutaneous Rosai-Dorfman disease (RDD) is a rare histiocytic proliferative disorder limited to the skin. To date, its pathogenesis remains unclear.
Kuan-Jou Wu +5 more
semanticscholar +1 more source
Rosai‐Dorfman disease in 6‐year‐old child: Presentation, diagnosis, and treatment
Rosai‐Dorfman disease is referred to as sinus histiocytosis massive lymphadenopathy. We are reporting a rare case of Rosai‐Dorfman disease, a case of 6‐year‐old boy with a history of multiple painless submandibular and cervical lymphadenopathy.
Kalpana Giri +3 more
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Rosai-Dorfman disease presenting as stridor and hoarseness in a young female patient
Rosai-Dorfman disease is a non-Langherans cell histiocytosis typically revealed by lymphadenopathy. Extranodal involvement occurs in 43% and most commonly involves the head and neck, skin, and bones. Few reports have described laryngeal lesions.
Vivianne Kokje, MD, PhD +6 more
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Clinicopathological and Gene Mutation Analysis of 27 Cases with Extranodal Rosai–Dorfman Disease
Objective To investigate the clinicopathological features, and mutations of NRAS, KRAS, BRAF and MAP2K1 genes in extranodal Rosai–Dorfman disease (RDD).
Ming Tang, X. Gu, P.C. Wu, Xuan Yang
semanticscholar +1 more source
Potential role of 18F-FDG PET/CT in a case of progressive Rosai Dorfman disease [PDF]
Rosai Dorfman disease is a rare form of nonlangerhans cell histiocytosis, presenting with extensive lymphadenopathies. Treatment in most cases of nodal disease, involves close observation; however, extranodal involvement requires a more definitive ...
Armaghan Fard-Esfahani +4 more
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Rosai–Dorfman Disease: Breast Involvement—Case Report and Literature Review
Background and objectives: Rosai–Dorfman disease (RDD) is a type of histiocytosis that usually appears in young adults or children as bilateral cervical lymphadenopathy, but extranodal involvement in not uncommon.
G. Iancu +5 more
semanticscholar +1 more source
Rosai-Dorfman disease. A legacy of Professor Rosai that is still not exploited completely
Summary Rosai-Dorfman disease (RDD) is a rare form of non-Langerhans cell histiocytosis described by Rosai and Dorfman in 1969. It is a fascinating disease characterized by accumulation of large, pale histiocytes, frequently showing the emperipolesis ...
C. Doglioni
semanticscholar +1 more source
Rosai Dorfman disease- A rare entity: Case report in North Indian male
Rosai Dorfman disease is a rare disease characterized by histiocytic proliferation of lymph node in young adults. We present here the case of a 67 years old Indian male presenting with lymphadenopathy and pyrexia of unknown origin for 16 months duration.
Ankur Baruah
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