Results 71 to 80 of about 4,878 (159)

Think highly of immunoglobulin G4‐related chronic rhinosinusitis as a clinical entity in immunoglobulin G4‐related disease

Eye &ENT Research, Volume 2, Issue 3, Page 151-163, September 2025.
Abstract IgG4‐related chronic rhinosinusitis (IgG4‐related CRS) is gaining recognition among various specialized physicians. As a systemic disease involving multiple organs, IgG4‐related CRS is still not widely recognized as an independent clinical entity. Given the complexity of diagnosing autoimmune‐related multisystem diseases, early recognition and
Lianqi Wan, Luo Zhang, Yingshi Piao, Yuan Zhang   +3 more
wiley   +1 more source

Extranodal manifestation of Rosai-Dorfman disease with bilateral ocular involvement

Journal of Cytology, 2011
Rosai-Dorfman disease, that is, sinus histiocytosis with massive lymphadenopathy is a benign systemic proliferative disorder of histiocytes. The typical clinical presentation of the disease includes bilateral painless massive lymphadenopathy, fever and ...
Chayanika Kala, Asha Agarwal, Sanjay Kala   +2 more
doaj   +1 more source

Primary Rosai-Dorfman Disease in 39-Year-Old Woman With Osseous Tibial Lesion Manifestion: A Case Report and Literature Review

Foot & Ankle Orthopaedics, 2021
Rosai-Dorfman disease (RDD), otherwise known as sinus histiocytosis with massive lymphadenopathy (SHML), is a very rare and typically benign disorder of unknown etiology with
Jasmin Mansoori DPM, Olivia Fisher MD, MPH, Ivana O. Akinyeye DPM, Michael A. Sobolevsky DPM, Robert H. Quinn MD   +4 more
doaj   +1 more source

An unusual Erdheim-Chester disease with orbital involvement: A case report [PDF]

, 2016
Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis with multiorgan involvement and a specific tropism for perivascular and fatty connective tissue, of unclear origin, with poor response to therapy. Its identification is difficult because
Bencivinni, F., Brunori, G., Giannitrapani, L., Seidita, A., Serruto, A., Soresi, M.   +5 more
core   +2 more sources

Characteristics of histiocytic neoplasms presenting as breast masses

British Journal of Haematology, Volume 208, Issue 1, Page 358-362, January 2026.
Theodore Vougiouklakis, Marc K. Rosenblum, Matthew Cannavo, Kimberly Feigin, Andrew E. Rosenberg, Frederick Wittlin, Sonia Mahajan, Edi Brogi, Maria E. Arcila, Hannah Y. Wen, Eli L. Diamond   +10 more
wiley   +1 more source

Morphological, immunohistochemical and molecular analysis of follicular dendritic cell sarcomas: L1CAM as a new diagnostic marker

Histopathology, Volume 87, Issue 2, Page 258-269, August 2025.
Pathohistological analysis of FDCS revealed a morphological spectrum and led to the identification of the adhesion molecule L1CAM as a novel diagnostic immunomarker for FDCS. Sequencing identified NFKBIA as the most frequently altered gene, of note, exclusively in cases with a predominant epithelioid cytomorphology.
Selina Schelbert, Katja Maurus, Sabine Roth, German Ott, Katrin S Kurz, Carolin Mogler, Barbara Wollenberg, John Linde, Alberto Zamo, Ioannis Anagnostopoulos, Susanne Gramlich, Andreas Rosenwald, Elena Gerhard‐Hartmann   +12 more
wiley   +1 more source

Extranodal Rosai-Dorfman Disease presenting as an isolated epibulbar mass

Indian Journal of Ophthalmology, 2008
Rosai-Dorfman disease is a rare idiopathic disorder characterized by painless lymphadenopathy with cervical involvement in more than 80% cases. We report a case of Rosai-Dorfman disease presenting as an isolated epibulbar mass in a healthy young ...
Maheshwari Rajat, Shekde Satish
doaj  

Review and a case of rare Rosai-Dorfman disease

Biotechnology & Biotechnological Equipment
Rosai-Dorfman (RDD) is a rare histiocytic syndrome with variable clinical characteristics and extranodal involvement in more than 43% of the patients. This mini-review presents an overview of the literature on Rosai-Dorfman disease.
Dragomira Nikolova, Aleksandar Yordanov, Aleksandra Maslarova, Radka Hristoskova, Vera Damyanova, Savina Hadjidekova, Atanas Radinov   +6 more
doaj   +1 more source

Isolated unilateral eyelid Rosai–Dorfman disease

Oman Journal of Ophthalmology, 2018
Isolated eyelid Rosai–Dorfman disease without orbital disease or systemic involvement is very rare and needs a high degree of suspicion. In this report, we describe a 16-year-old boy who presented with isolated eyelid Rosai–Dorfman disease involving the ...
Nandini Bothra, Swathi Kaliki, Swarnalata Gowrishankar, S Anuradha   +3 more
doaj   +1 more source

Mass‐Forming Variants in Antineutrophil Cytoplasmic Antibody–Associated Vasculitis: Diagnostic Complexities in Granulomatous Disease. A Case Report

ACR Open Rheumatology, Volume 7, Issue 4, April 2025.
A middle‐aged woman presented with a granulomatous breast lesion in 2018. By 2021, antibiotic‐resistant pneumonia led to the discovery of granulomatous inflammation in the lung and thyroid. Initially misdiagnosed as Erdheim–Chester disease (ECD), she was treated with interferon without success.
Benedetta Fazzi, Elena Treppo, Simone Longhino, Maria Pillon, Luca Quartuccio   +4 more
wiley   +1 more source