Results 81 to 90 of about 9,189,306 (207)

The Neuroimaging Spectrum of Neurosarcoidosis

Clinical Neuroimaging, Volume 2, Issue 1, 2025.
ABSTRACT Among its many forms, involvement of the nervous system in sarcoidosis ranks as one of the most severe and potentially disabling manifestations of the disease, and timely recognition and accurate diagnosis are critical for its optimal treatment.
Spencer K. Hutto, Gabriela A. Bou
wiley   +1 more source

Steroid responsive cavernous sinus syndrome due to Rosai-Dorfman disease: beyond Tolosa-Hunt syndrome – a case report

BMC Neurology, 2021
Background The term “Tolosa-Hunt syndrome” (THS) has been used to refer to painful ophthalmoplegia associated with nonspecific inflammation of the cavernous sinus and many processes can result in a similar clinical picture, including infectious ...
Paulo Ribeiro Nóbrega, Pedro Gustavo Barros Rodrigues, Isabelle de Sousa Pereira, Carolina de Figueiredo Santos, Gunter Gerson, José Arnaldo Motta de Arruda, José Wagner Leonel Tavares Júnior, Pablo Picasso de Araújo Coimbra, Pedro Braga-Neto   +8 more
doaj   +1 more source

BRAF V600E mutation detected in a case of Rosai-Dorfman disease

Haematologica, 2018
Rosai-Dorfman Disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a rare, nonmalignant histiocytic proliferation of unknown etiology. According to the new classification, it belongs to the R group of histiocytoses.[1][1] The
G. Fatobene, J. Haroche, Zofia Hélias-Rodzwicz, F. Charlotte, V. Taly, A. M. Ferreira, A. Abdo, V. Rocha, J. Emile   +8 more
semanticscholar   +1 more source

A Rare Case of Primary Intraparenchymal Rosai‐Dorfman Disease

iRADIOLOGY, Volume 3, Issue 5, Page 370-371, October 2025.
Lin Chen, Rui Zhou
wiley   +1 more source

The Impact of Hybrid Therapy on Langerhans Cell Histiocytosis of the Mandible in an Older Male: A Case Report and Literature Review

Case Reports in Otolaryngology, Volume 2025, Issue 1, 2025.
Background The unusual disorder known as Langerhans cell histiocytosis (LCH), which is most frequently observed in children and young adults, is caused by the clonal proliferation of Langerhans cells. This disease is classified into several types depending on the extent of the lesion.
Yoshifumi Matsumoto, Maki Akamatsu, Shinichi Ohba, Fumihiko Matsumoto, Kenichi Takano   +4 more
wiley   +1 more source

Benign and malignant cutaneous nasal lesions

Eye &ENT Research, Volume 1, Issue 2, Page 65-91, December 2024.
Abstract The nose is a structure of both cosmetic and functional importance. Cutaneous lesions of the nose occasionally represent a diagnostic challenge and involve the expertise of several specialties from dermatology, otolaryngology—head and neck surgery, infectious disease, and pathology, among others.
Hamed Sarikhani, Karena Zhao, Marc A. Polacco, Charles Gropper, Samuel N. Helman   +4 more
wiley   +1 more source

Extranodal Rosai-Dorfman Disease presenting as an isolated epibulbar mass

Indian Journal of Ophthalmology, 2008
Rosai-Dorfman disease is a rare idiopathic disorder characterized by painless lymphadenopathy with cervical involvement in more than 80% cases. We report a case of Rosai-Dorfman disease presenting as an isolated epibulbar mass in a healthy young ...
Maheshwari Rajat, Shekde Satish
doaj  

Cutaneous Rosai–Dorfman disease with MAP2K1 mutation, initially mimicking an infection with parasitized histiocytes

Journal of Cutaneous Pathology, Volume 51, Issue 12, Page 942-947, December 2024.
Abstract Rarely, Rosai–Dorfman disease (RDD) manifests exclusively in the skin, typically as nodules on the trunk and extremities. Recognition of characteristic histopathologic features enables diagnosis of RDD. A 55‐year‐old female presented with a 7‐year history of cutaneous nodules involving the trunk and extremities. A prior skin biopsy specimen at
Joseph Gillam, Ruchi Desai, Raphael J. Louie, Scott A. Turner, Grace Y. Wang, Julio A. Diaz‐Perez, Mark C. Mochel   +6 more
wiley   +1 more source

Review and a case of rare Rosai-Dorfman disease

Biotechnology & Biotechnological Equipment
Rosai-Dorfman (RDD) is a rare histiocytic syndrome with variable clinical characteristics and extranodal involvement in more than 43% of the patients. This mini-review presents an overview of the literature on Rosai-Dorfman disease.
Dragomira Nikolova, Aleksandar Yordanov, Aleksandra Maslarova, Radka Hristoskova, Vera Damyanova, Savina Hadjidekova, Atanas Radinov   +6 more
doaj   +1 more source

Idiopathic multicentric Castleman disease with marrow fibrosis and extramedullary hematopoiesis

European Journal of Haematology, Volume 113, Issue 6, Page 833-841, December 2024.
Abstract Background Idiopathic multicentric Castleman disease (iMCD) is a rare inflammatory disorder mediated by excessive proinflammatory cytokine signaling, most notably by interleukin 6 (IL‐6). IL‐6‐induced extramedullary hematopoiesis (EMH) has been reported in murine models of iMCD. Herein we present four cases of iMCD with EMH in humans.
Marley Blommers, Sorin Selegean, Richard K. Wood, Mateo Sarmiento Bustamante, Saishravan Shyamsundar, E. Ashley Wiley, Emilie Comeau, Allam A. Shawwa, Stefan Rose‐John, David C. Fajgenbaum, Luke Y. C. Chen   +10 more
wiley   +1 more source