Results 151 to 160 of about 3,523,664 (305)

Mutation type‐specific transcriptomic signatures and readthrough therapy rescue in SMC1A‐related developmental and epileptic encephalopathy

open access: yesEpilepsia, EarlyView.
Abstract Objective This study was undertaken to investigate the molecular consequences of pathogenic variants in the SMC1A gene—particularly those associated with developmental and epileptic encephalopathy (DEE85)—and to evaluate the therapeutic potential of ataluren in restoring SMC1A function and mitigating disease‐related transcriptomic and genomic ...
Maddalena Di Nardo   +7 more
wiley   +1 more source

Design of HAWT Rotor for Non‐Uniform Inflow Conditions: A Theoretical and Experimental Approach for Shear Flow

open access: yesEnergy Science &Engineering, EarlyView.
This paper aims to provide a robust design approach for HAWTs operating in shear flow. This study fills a critical research gap by integrating BEM and vortex theories for blade design in non‐homogeneous inflow conditions. The authors of the paper made an effort to develop and test an experimentally unsophisticated model of a turbine working in shear ...
Agnieszka Dorota Woźniak   +2 more
wiley   +1 more source

Adaptive vector oriented control of doubly fed induction generator wind turbines using M5P model tree for robust dynamic performance. [PDF]

open access: yesSci Rep
Benyoucef K   +7 more
europepmc   +1 more source

Two‐Layer Optimal Control Strategy of Thermal Power Unit Coupled With Hybrid Energy Storage System in Frequency Regulation

open access: yesEnergy Science &Engineering, EarlyView.
An optimized two‐layer TPU‐HESS operation strategy enables adaptive power allocation, mitigates regulation delay, and enhances AGC performance by 6.4% over conventional control methods. ABSTRACT With the growing penetration of renewable energy, its intermittency and fluctuation have imposed increasingly stringent regulation requirements on thermal ...
Zhiwei Xing   +9 more
wiley   +1 more source

Wind Resource Evaluation With Atmospheric Stability Across Different Surface Types

open access: yesEnergy Science &Engineering, EarlyView.
Wind resource evaluation with atmospheric stability across different surface types. ABSTRACT This study investigates the influence of atmospheric stability on wind resource assessment across various surface conditions, focusing on wind shear and prevailing wind direction as key analytical parameters.
Zejia Hua, Wei Tao, Guanjun Wang
wiley   +1 more source

Optimized Dual ANN Control Technique for Efficient Energy Management System (EMS) of Microgrid

open access: yesEnergy Science &Engineering, EarlyView.
Proposed methodology. ABSTRACT The escalating global energy demand necessitates a shift towards sustainable and environmentally friendly alternatives. While renewable energy sources like solar and wind energy offer promising solutions, their intermittent nature poses significant challenges for grid integration.
Bin Li   +5 more
wiley   +1 more source

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