Cystic medial necrosis (CMN) is a disorder of large arteries, in particular the aorta, characterized by an accumulation of basophilic ground substance in the media with cyst-like lesions.
Shi-Min Yuan, Hua Jing
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Guidelines for surgery of aortic diseases from the Brazilian Society of Cardiovascular Surgery: updated in 2009 [PDF]
PUCRS Hospital São LucasFamerpUnicampUNIFESPUFRGS HCPA Faculdade de MedicinaUNIOESTE HUOPFAG Curso de MedicinaUNIFESP-EPMUNIFESP ...
Albuquerque, Luciano Cabral+6 more
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História de Saúde Familiar [PDF]
Brochura traduzida e adaptada de Genetic Alliance.O Instituto Nacional de Saúde Doutor Ricardo Jorge (INSA) desenvolve atividades de investigação, observação da saúde e vigilância epidemiológica, promovendo a difusão da cultura científica e a literacia ...
Bourbon, Mafalda+2 more
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Marfan syndrome with ascending aortic aneurysm: Value of cardiac computed tomography
We report the case of a 40-year-old man with known Marfan syndrome who presented with severe aortic valve regurgitation secondary to significant aortic root dilatation.
Pedro Jerónimo Sousa+9 more
doaj
Resultados perinatales en gestantes con cardiopatias atendidas en el servicio de alto riesgo obstetrico. Hospital Bertha Calderon Roque. Enero a Diciembre de 2014 [PDF]
El presente estudio es de tipo descriptivo, retrolectivo de serie de casos, realizado en el Hospital Bertha Calderón Roque en el período comprendido Enero - Diciembre de 2014.
Ruiz Flores, Roger Rafael
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A c.3037G > A mutation in FBN1 gene causing Marfan syndrome with an atypically severe phenotype. [PDF]
Marfan syndrome is a pleiotropic connective tissue disease inherited as an autosomal dominant trait, mostly caused by mutations in the FBN1 gene, which is located on chromosome 15q21.1 and encoding fibrillin 1.
Bellacchio, Emanuele+11 more
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Basilar ectasia and stroke: clinical aspects of 21 cases [PDF]
Ectasia of the basilar artery (EB) occurs when its diameter is greater than normal along all or part of its course, and/or when it is abnormally tortuous.
Cardeal, Jose Osmar+2 more
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Síndrome de Marfan de presentación atípica, reflejo de una nueva mutación
El síndrome de Marfan (SM) es un desorden del tejido conectivo que afecta a los sistemas musculoesquelético, cardiovascular y ocular. Presentamos el caso de una paciente diagnosticada de SM tras sufrir un cuadro de edema pulmonar agudo, objetivándose a ...
Cristina Sardiña-González+4 more
semanticscholar +1 more source
Tratamento Endovascular da Disseção Crónica Isolada da Aorta Abdominal [PDF]
Isolated acute abdominal aortic dissection is a relatively rare event. Its natural history is not fully understood and its optimal treatment is not established.
Almeida, R.+3 more
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Es el reimplante valvular mejor que el bentall biológico modificado para tratar aneurismas de la raíz asociados a insuficiencia? [PDF]
Es el reimplante valvular mejor que el Bentall Biológico Modificado para tratar aneurismas de la raíz asociados a insuficiencia? Obando CE; Gutiérrez HF; Santamaría G, Bresciani R; Camacho J; Sandoval N; Umaña J.
Obando López, Carlos Eduardo+6 more
core +2 more sources