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Atypical Scleromyxedema with Dramatic Response to Low Dose Prednisolone and Thalidomide
MedS Alliance Journal of Medicine and Medical SciencesScleromyxedema is a rare condition which is clinically characterized by asymptomatic to itchy generalized papular and sclerodermoid eruption with histological findings which include mucin deposition and fibroblast proliferation. It can be associated with
Satyendra Kumar Singh +6 more
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Journal of Neurology, 2019
Scleromyxedema is a chronic, idiopathic disorder associated with monoclonal gammopathy, and characterized by dermal mucin deposition. However, systemic manifestations are frequent, including neuromuscular symptoms. We herein present a 71-year-old man who developed a vacuolar myopathy in a context of a known scleromyxedema, and we compare our ...
Antoine Soulages +9 more
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Scleromyxedema is a chronic, idiopathic disorder associated with monoclonal gammopathy, and characterized by dermal mucin deposition. However, systemic manifestations are frequent, including neuromuscular symptoms. We herein present a 71-year-old man who developed a vacuolar myopathy in a context of a known scleromyxedema, and we compare our ...
Antoine Soulages +9 more
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Archives of Dermatology, 1966
Two patients with typical skin lesions of scleromyxedema (lichen myxedematosus) are described. The disorder is characterized by proliferation of fibroblasts and excessive deposition of acid mucopolysaccharides in the dermis. Quantitative elevated levels of acid mucopolysaccharides were demonstrated in the serum and skin of one patient.
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Two patients with typical skin lesions of scleromyxedema (lichen myxedematosus) are described. The disorder is characterized by proliferation of fibroblasts and excessive deposition of acid mucopolysaccharides in the dermis. Quantitative elevated levels of acid mucopolysaccharides were demonstrated in the serum and skin of one patient.
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Thalidomide as a Key Therapeutic Agent in a Pediatric Case of Generalized Cutaneous Scleromyxedema
Clinical Dermatology ReviewGeneralized cutaneous scleromyxedema (GCS) is a rare chronic mucinosis characterized by shiny, firm papules, typically measuring 2–3 mm in diameter, which can appear in a linear distribution.
Nikita Singh, P. Tiwary, Anupama Singh
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Encephalopathy in scleromyxedema
Neurology, 1999The authors monitored CSF findings for over 5 months in a patient with a fatal case of scleromyxedema and two episodes of encephalopathy. During both encephalopathy episodes, CSF protein and immunoglobulin G (IgG) levels were elevated without an increased IgG index or IgG synthesis rate. A CSF-dominant increase in the concentration of interleukin-6 (IL-
K, Johkura +4 more
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Cosmoderma
Scleromyxedema (SM) is a rare fibromucinous disorder typically associated with monoclonal gammopathy, but atypical variants without paraproteinemia and with coexistent thyroid dysfunction challenge traditional diagnostic criteria.
Prateek Nayak +3 more
semanticscholar +1 more source
Scleromyxedema (SM) is a rare fibromucinous disorder typically associated with monoclonal gammopathy, but atypical variants without paraproteinemia and with coexistent thyroid dysfunction challenge traditional diagnostic criteria.
Prateek Nayak +3 more
semanticscholar +1 more source
Scleromyxedema and Severe Myositis
International Journal of Dermatology, 1989A case of scleromyxedema with associated rhabdomyolysis is reported. This appears to be a well-documented, although rare complication of scleromyxedema. This case is unique in that mucin was demonstrated in the muscle as well as the skin, and spontaneous resolution of the rhabdomyolysis occurred with the implementation of IV fluids and bed rest.
M J, Rothe +3 more
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Scleromyxedema with Corneal Deposits
Ophthalmology, 1987Scleromyxedema (Arndt-Gottron syndrome) is a rare cutaneous disease in which hyaluronic acid is deposited in the dermis. The authors describe a patient with scleromyxedema and corneal deposits. A corneal biopsy demonstrated hyaluronic acid deposition in the corneal stroma and amyloid P component in Bowman's membrane.
H M, Goldin +5 more
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Cutis, 1980
Scleromyxedema (also known as lichen myxedematosus or papular mucinosis) is a rare cutaneous disorder characterized by lichenoid waxy papules, sclerosis, and a characteristic paraproteinemia. Rarely, if ever, is there systemic involvement. The cause and pathogenesis remain a mystery, however, a recent report has linked a serum factor with fibroblast ...
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Scleromyxedema (also known as lichen myxedematosus or papular mucinosis) is a rare cutaneous disorder characterized by lichenoid waxy papules, sclerosis, and a characteristic paraproteinemia. Rarely, if ever, is there systemic involvement. The cause and pathogenesis remain a mystery, however, a recent report has linked a serum factor with fibroblast ...
openaire +1 more source