Results 141 to 150 of about 1,053 (167)
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Journal of the American Academy of Dermatology, 1995
Scleromyxedema is a rare fibromucinous disorder that is often difficult to treat and that is associated with significant morbidity and mortality.Our purpose was to study the natural history of the disease and its response to therapy with alkylating agents.A clinicopathologic review of 26 patients with scleromyxedema was performed, and the ...
A M, Dinneen, C H, Dicken
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Scleromyxedema is a rare fibromucinous disorder that is often difficult to treat and that is associated with significant morbidity and mortality.Our purpose was to study the natural history of the disease and its response to therapy with alkylating agents.A clinicopathologic review of 26 patients with scleromyxedema was performed, and the ...
A M, Dinneen, C H, Dicken
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Archives of Dermatology, 1969
A 65-year-old woman developed typical scleromyxedema, with the associated M-type abnormal serum protein and marrow plasmacytosis. Treatment with systemic melphalan resulted in a dramatic response. The dermatosis improved noticeably after one month and a biopsy taken after five months of therapy showed almost total restitution to normal. The response of
T, Horio, I, Yonezawa
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A 65-year-old woman developed typical scleromyxedema, with the associated M-type abnormal serum protein and marrow plasmacytosis. Treatment with systemic melphalan resulted in a dramatic response. The dermatosis improved noticeably after one month and a biopsy taken after five months of therapy showed almost total restitution to normal. The response of
T, Horio, I, Yonezawa
+7 more sources
International Journal of Dermatology, 2003
AbstractScleromyxedema is a rare disease characterized by papular mucinous deposits, dermal fibroblast proliferation, and a monoclonal paraproteinemia. Its chronic course tends to be complicated by gastrointestinal, muscular, pulmonary, and neurologic disorders.
John J, Pomann, Earl J, Rudner
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AbstractScleromyxedema is a rare disease characterized by papular mucinous deposits, dermal fibroblast proliferation, and a monoclonal paraproteinemia. Its chronic course tends to be complicated by gastrointestinal, muscular, pulmonary, and neurologic disorders.
John J, Pomann, Earl J, Rudner
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Ophthalmic Plastic & Reconstructive Surgery, 2015
Scleromyxedema is characterized by cutaneous mucinosis and rarely presents to oculoplastic surgeons with bilateral upper and lower eyelid swelling. The authors present 2 case reports with a review of the literature and discuss the ophthalmic manifestations of scleromyxedema and the management of these cases.
Farhan, Qureshi +2 more
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Scleromyxedema is characterized by cutaneous mucinosis and rarely presents to oculoplastic surgeons with bilateral upper and lower eyelid swelling. The authors present 2 case reports with a review of the literature and discuss the ophthalmic manifestations of scleromyxedema and the management of these cases.
Farhan, Qureshi +2 more
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Archives of dermatology, 1976
An unusual, nodulocystic form of scleromyxedema (lichen myxedematosus) developed in a 48-year-old man with a six-year history of psoriasis. The scleromyxedema responded to intermittent therapy with melphalan and prednisone. Dermabrasion smoothed and softened the skin and increased the mobility of the perioral skin.
R C, Wright +3 more
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An unusual, nodulocystic form of scleromyxedema (lichen myxedematosus) developed in a 48-year-old man with a six-year history of psoriasis. The scleromyxedema responded to intermittent therapy with melphalan and prednisone. Dermabrasion smoothed and softened the skin and increased the mobility of the perioral skin.
R C, Wright +3 more
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Journal of Neurology, 2019
Scleromyxedema is a chronic, idiopathic disorder associated with monoclonal gammopathy, and characterized by dermal mucin deposition. However, systemic manifestations are frequent, including neuromuscular symptoms. We herein present a 71-year-old man who developed a vacuolar myopathy in a context of a known scleromyxedema, and we compare our ...
Antoine Soulages +9 more
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Scleromyxedema is a chronic, idiopathic disorder associated with monoclonal gammopathy, and characterized by dermal mucin deposition. However, systemic manifestations are frequent, including neuromuscular symptoms. We herein present a 71-year-old man who developed a vacuolar myopathy in a context of a known scleromyxedema, and we compare our ...
Antoine Soulages +9 more
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Archives of Dermatology, 1966
Two patients with typical skin lesions of scleromyxedema (lichen myxedematosus) are described. The disorder is characterized by proliferation of fibroblasts and excessive deposition of acid mucopolysaccharides in the dermis. Quantitative elevated levels of acid mucopolysaccharides were demonstrated in the serum and skin of one patient.
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Two patients with typical skin lesions of scleromyxedema (lichen myxedematosus) are described. The disorder is characterized by proliferation of fibroblasts and excessive deposition of acid mucopolysaccharides in the dermis. Quantitative elevated levels of acid mucopolysaccharides were demonstrated in the serum and skin of one patient.
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Encephalopathy in scleromyxedema
Neurology, 1999The authors monitored CSF findings for over 5 months in a patient with a fatal case of scleromyxedema and two episodes of encephalopathy. During both encephalopathy episodes, CSF protein and immunoglobulin G (IgG) levels were elevated without an increased IgG index or IgG synthesis rate. A CSF-dominant increase in the concentration of interleukin-6 (IL-
K, Johkura +4 more
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New England Journal of Medicine, 2023
Soumya Chatterjee, Anthony P. Fernandez
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Soumya Chatterjee, Anthony P. Fernandez
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