Results 91 to 100 of about 74,735 (268)

Hearing Loss in Mucopolysaccharidoses: Current Knowledge and Future Directions

Diagnostics, 2020
Mucopolysaccharidoses (MPS) are a group of lysosomal storage disorders caused by a deficiency of one of the enzymes involved in the degradation of glycosaminoglycans. Hearing loss is a common clinical presentation in MPS.
Jeremy Wolfberg, Keerthana Chintalapati, Shunji Tomatsu, Kyoko Nagao   +3 more
doaj   +1 more source

Clinic manifestations in granulomatosis with polyangiitis [PDF]

, 2016
Granulomatosis with polyangiitis (GPA), formerly Wegener's granulomatosis (WG), is an uncommon immunologically mediated systemic small-vessel vasculitis that is pathologically characterised by an inflammatory reaction pattern (necrosis, granulomatous ...
De Vincentiis, Marco, De Virgilio, Armando, Fusconi, Massimo, Gallo, Andrea, Greco, Antonio, Macri, Gian Franco, Marinelli, Caterina, Zambetti, Giampietro   +7 more
core   +1 more source

Recurrent Maxillary Ameloblastoma Presenting as an External Auditory Canal Mass

The Laryngoscope, EarlyView.
Ameloblastoma with temporal bone involvement is exceedingly rare, with no prior reports of external auditory canal presentation. This case report demonstrates successful multidisciplinary management with extensive skull base resection and adjuvant radiation therapy, emphasizing the role of proton therapy in achieving tissue‐sparing treatment and long ...
Bailey H. Duhon, Adel K. El‐Naggar, Jeffrey N. Myers, William H. Morrison, Franco DeMonte, Paul W. Gidley   +5 more
wiley   +1 more source

Labyrinthine Abnormalities on MRI in Untreated Otosclerosis: Prevalence and Clinical Relevance

The Laryngoscope, EarlyView.
In untreated otosclerosis with labyrinthine symptoms, delayed 3D FLAIR MRI rarely demonstrates endolymphatic hydrops but frequently reveals blood–labyrinth barrier (BLB) disruption. BLB enhancement is spatially associated with cochlear endosteal and round window involvement and increases with the severity of the hearing loss phenotype.
Héléna Pencroffi, Sylvain Bourdoncle, Jean Fanet, Stéphane Gargula, Denis Ayache, Loïc Duron, Julien Savatovsky, Guillaume Poillon   +7 more
wiley   +1 more source

Classification and hearing evolution of patients with sudden sensorineural hearing loss [PDF]

, 2009
The aim of this study was to analyze clinical aspects, hearing evolution and efficacy of clinical treatment of patients with sudden sensorineural hearing loss (SSNHL).
Cruz, Oswaldo Laércio Mendonça, Inoue, Daniel Paganini, Penido, Norma de Oliveira, Zanoni, A.   +3 more
core   +2 more sources

Auditory Steady State Responses in children and adolescents with severe to profound and steeply sloping sensorineural hearing loss [PDF]

, 2014
PurposeTo verify the correlation between the electrophysiological thresholds in Auditory Evoked Potential Steady State (ASSR) and behavioral thresholds obtained with pure tone audiometry in children and adolescents with severe to profound sensorineural ...
Azevedo, Marisa Frasson de, Luiz, Cyntia Barbosa Laureano   +1 more
core   +2 more sources

Long‐Term Outcomes of Deep Brain Stimulation in Woodhouse–Sakati Syndrome

Movement Disorders, EarlyView.
Abstract Background Woodhouse–Sakati syndrome (WSS) is a rare autosomal recessive disease with distinctive neuroendocrine manifestations, with dystonia being the most common. No clear guidelines are available for the treatment of dystonia in WSS. Objective The aim was to analyze the impact of deep brain stimulation (DBS) on WSS‐associated dystonia ...
Hend Alhodaif, Yara Alkhodair, Faisal Alotaibi, Salma Alqahtani, Saeed Bohlega, Amaal Aldakheel   +5 more
wiley   +1 more source

Do Caloric Test Results Affect the Prognosis of Sudden Hearing Loss?

Ankara Üniversitesi Tıp Fakültesi Mecmuası, 2017
Aim: The aim of this study is to evaluate the prognostic value of caloric test results in patients with sudden hearing loss.Material -Method: We evaluated 23 patients with sudden hearing loss who were hospitalized.
Süha Beton, Muharrem Gerçeker
doaj   +1 more source

Rate of Hearing Loss in Platinum‐Naïve Patients Receiving Immune Checkpoint Inhibitors

Otolaryngology–Head and Neck Surgery, EarlyView.
Abstract Objective Hearing loss from immune checkpoint inhibitors (ICIs) has been documented in case reports and case series. We present the largest retrospective study investigating the rate of ICI‐related ototoxicity in a monitored cohort of platinum‐naïve patients. Study Design Retrospective cohort study. Setting Tertiary‐care center.
Kaitlyn A. Brooks, Christopher G. Gidley, Olivia Grimley, Catherine Wang, Shirin Jivani, Dianna Roberts, Aung Naing, Jack Phan, Katherine Hutcheson, Xin Wang, Paul W. Gidley, Marc‐Elie Nader   +11 more
wiley   +1 more source

The Auditory Steady-State Response and the Relationship between Electrophysiological and Behavioural Thresholds

Diagnostics
Background: This study examined the relationship between behavioural thresholds as measured by pure tone audiometry and electrophysiological thresholds measured by the Auditory Steady-State Response (ASSR) in children with normal hearing and ...
Cyntia Barbosa Laureano Luiz, Daniela Gil, Piotr Henryk Skarzynski, Magdalena Beata Skarżyńska, Milaine Dominici Sanfins, Marisa Frasson de Azevedo   +5 more
doaj   +1 more source