Results 11 to 20 of about 1,752 (171)

The Clinicopathologic Spectrum of Rosai-Dorfman-Destombes Disease in Adults: An Analysis of 16 Cases. [PDF]

Eur J Haematol
ABSTRACT Rosai–Dorfman–Destombes disease (RDD) is a rare histiocytic proliferation with protean clinical manifestations, resulting from the accumulation of activated histiocytes within nodal and extra‐nodal tissues. The diagnosis can be missed, particularly when biopsies are obtained from extra‐nodal sites, where histological features may be less ...
Trinder M, Pryma C, Leung E, Slack GW, Farinha P, Young S, Ozkaya N, Carruthers M, Chen LYC.   +8 more
europepmc   +2 more sources

A comparison of the International Consensus and 5th WHO classifications of T‐cell lymphomas and histiocytic/dendritic cell tumours

British Journal of Haematology, Volume 203, Issue 3, Page 369-383, November 2023., 2023
The simultaneous existence of two classifications of haemato‐lymphoid tumours poses problems not only for diagnosis formulation but also for patients' management and design of clinical trials. Summary Since the publication in 2017 of the revised 4th Edition of the World Health Organization (WHO) classification of haematolymphoid tumours, here referred ...
Brunangelo Falini, Stefano Lazzi, Stefano Pileri   +2 more
wiley   +1 more source

Rosai-Dorfman Disease, Presenting as a Mass in the Trachea: A Case Report. [PDF]

Respirol Case Rep
We present a rare case of Rosai–Dorfman disease (RDD) confined solely to the trachea. After initial bronchoscopic resection, systemic corticosteroid therapy was initiated due to lesion progression, successfully stabilizing the disease for 4 years. ABSTRACT A 45‐year‐old woman was referred to our clinic for evaluation of a 17 mm tracheal mass detected ...
Youn T, Lee B, Han J, Jeong BH.
europepmc   +2 more sources

A case of disseminated extranodal Rosai–Dorfman disease diagnosed by skin manifestations

Journal of Cutaneous Immunology and Allergy, Volume 6, Issue 3, Page 105-107, June 2023., 2023
We present a case of disseminated extranodal RDD, where the initial symptoms were cutaneous manifestations. Immunohistochemistry revealed that the infiltrating macrophages were positive for CD68, S100‐protein, Cyclin D1, OCT2, and phospho‐ERK, but negative for CD1a and langerin.
Shintaro Saito, Akihiko Uchiyama, Yayoi Shibusawa, Sei‐ichiro Motegi   +3 more
wiley   +1 more source

Bilateral breast Rosai‐Dorfman disease screen detected by mammography

Clinical Case Reports, Volume 11, Issue 3, March 2023., 2023
Rosai‐Dorfman disease (RDD) is a rare proliferative disorder of histiocytes typically found in nodal sites, however, it can also present initially as an asymptomatic mass in the breast. Presenting symptoms may include fever, lymphadenopathy, and weight loss. Tissue sampling is definitive for diagnosis and close surveillance is recommended.
Christina Sumner, Karma Salem, Luma Abunimer, Abdulwahab Ewaz, Linsheng Zhang, Ashley Monsrud, Nabil Calisi   +6 more
wiley   +1 more source

Langerhans Cell Histiocytosis of the Uvea with a Ciliochoroidal Mass: A Case Report of Management with Systemic Therapy

Case Reports in Ophthalmological Medicine, Volume 2023, Issue 1, 2023., 2023
Background. This study is aimed at exploring a case of choroidal Langerhans cell histiocytosis (LCH) successfully treated with systemic corticosteroid and immunosuppressant. Case presentation. A 24‐year‐old man with known multisystem LCH developed loss of vision, ocular pain, conjunctival injection, panuveitis, and a ciliochoroidal mass.
Fariba Ghassemi, Hamid Riazi-Esfahani, Nazanin Ebrahimiadib, Abdulrahim Amini, Zahra Mahdizad, Stephen G. Schwartz   +5 more
wiley   +1 more source

Asymptomatic flow of Rosai-Dorfman disease [PDF]

, 2014
Introduction. Sinus histiocytosis with massive lymphadenopathy is a rare benign self-limiting disease of unknown etiology. The salivary gland involvement, indicating the extranodal character of the disease, often presents a diagnostic dilemma ...
Bjelaković Bojko, Kesić Ljiljana, Kostić Miloš, Mihailović Dragan, Mijovićć Žaklina, Petrović Dragan, Petrović Milica, Petrović Slađana, Stanković Ana, Vučković Ivica, Živković Nikola   +10 more
core   +1 more source

Prednisone and Vincristine for the Treatment of Pediatric Rosai-Dorfman Disease: A Case Report. [PDF]

Case Rep Med
Purpose Pediatric Rosai–Dorfman disease (RDD) is extremely rare, and the current treatment plan is not unified. We hope that our study provides new ideas for the clinical treatment of RDD. Methods We report a case in which RDD was successfully treated with prednisone and vincristine, resulting in regression of enlarged lymph nodes.
Dun J, Hu Q, Liu A, Wang Y, Zhang A.
europepmc   +2 more sources

A Rare Case of a Systemic Non-Langerhans Histiocytosis Presenting with Diabetes Insipidus and a Tentorial Mass [PDF]

, 2015
Introduction The histiocytoses are a group of clinically diverse diseases distinguished from one another based on the specific immunophenotype of the lesional cells, implying derivation from the same precursor cell.
Barros, MS, Guilherme, Farrell, MD, Christopher J, Kenyon, MD, PhD, Lawrence C, Krupa, BS, Kelly, Krupa, BS, Kristin, Madineni, MD, Ravichandra   +5 more
core   +2 more sources

A Rare Cause of Lymphadenopathy in a Young Hispanic Female: Unmasking Recurrent Nodal Rosai-Dorfman Disease [PDF]

, 2023
Rosai-Dorfman disease (RDD) is a rare histiocytic disorder that can present with painless bilateral symmetrical cervical lymphadenopathy, mimicking lymphomas.
Alfarooq Alshaikhli, Blesset Alexander, Emilia C Dulgheru, Mery Bartl, Yilen K Ng-Wong   +4 more
core   +2 more sources