Wells syndrome: clinical findings and management in a large cohort of 48 patients
JDDG: Journal der Deutschen Dermatologischen Gesellschaft, EarlyView.Summary Background and Objectives: Wells syndrome (WS) is a rare inflammatory skin disorder typically characterized by erythematous, edematous, and pruritic plaques. Despite its distinct histopathological features, WS remains an underdiagnosed disease due to its variable clinical presentations and overlap with other dermatological conditions.
Marco Adriano Chessa +8 more
wiley +1 more source
Pemphigus vegetans with isolated involvement of the nose and chest: rare variant of pemphigus vulgaris [PDF]
Anais Brasileiros de Dermatologia, 2019 : Pemphigus vulgaris is chronic bullous disease that manifests as bullae and erosions of skin and mucosas, with intraepidermal suprabasal cleft formation seen in the histological examination.
Raisa Ilena Caranhas Feitoza +3 more
doaj +2 more sources
Histomorphologic and Direct Immunofluorescence Findings of Autoimmune Bullous Disease [PDF]
, 2018 Autoimmune bullous diseases mainly present with vesiculobullous reaction pattern. First algorithm to approach skin biopsy of autoimmune vesiculobullous disease should be localization of the anatomic level of the split, which could be either ...
Ates, Deniz
core +2 more sources
Omalizumab for Pediatric Cutaneous Mastocytosis: Case Report and Review
Pediatric Dermatology, EarlyView.ABSTRACT We report an 11‐month‐old boy with diffuse cutaneous mastocytosis whose severe pruritus and steroid dependence resolved following off‐label treatment with omalizumab. A literature review identified five additional pediatric cases in which omalizumab led to complete symptom resolution in an average of 2 months and permitted discontinuation of ...
Janis Chang +3 more
wiley +1 more source
Snapshot Look at Castleman Disease
Journal of Cellular and Molecular Medicine, Volume 30, Issue 3, February 2026.ABSTRACT Castleman disease (CD) is a rare and heterogeneous group of lymphoproliferative disorders characterised by abnormal proliferation of lymphoid tissue. First described in the 1950s, it has since been classified into two major clinical forms: unicentric CD (UCD), involving a single lymph node region and multicentric CD (MCD), which affects ...
Ciprian Jitaru +17 more
wiley +1 more source
A Case of Blistering Eruptions in Systemic Lupus Erythematosus [PDF]
Journal of Clinical and Diagnostic Research, 2019 Cutaneous vesiculobullous lesions have a wide aetiological spectrum ranging from autoimmunity to medications and infections. Systemic Lupus Erythematosus (SLE) is one of most frequent autoimmune diseases with its cutaneous form being very uncommonly ...
Sarojini Raman +3 more
doaj +1 more source
Diffuse systemic sclerosis with bullous lesions without systemic manifestations [PDF]
Anais Brasileiros de Dermatologia, 2013 Here, we describe an atypical case of systemic sclerosis in its diffuse cutaneous form with acute and rapid progression of the cutaneous condition, without any systemic manifestations and the infrequent formation of bullae, showing the importance of ...
Paula Renaux Wanderley Caratta Macedo +4 more
doaj +1 more source
Mucocutaneous Manifestation of Systemic Lupus Erythematosus Patients at Rheumatology Outpatient Clinic in Dr. Hasan Sadikin General Hospital [PDF]
, 2017 Background: Systemic Lupus Erythematosus (SLE) is an autoimmune systemic disease which symptoms induced by Ultraviolet rays exposure. It commonly affects women and causes wide range of symptoms. One of the organs affected is mucocutaneous. Our study aims
Dharmadji, H. P. (Hartati) +3 more
core
Cytoskeletal regulation of inflammation and its impact on skin blistering disease epidermolysis bullosa acquisita [PDF]
, 2016 Actin remodelling proteins regulate cytoskeletal cell responses and are important in both innate and adaptive immunity. These responses play a major role in providing a fine balance in a cascade of biological events that results in either protective ...
Cowin, A., Kopecki, Z., Ludwig, R.
core +2 more sources
A Two Year Retrospective Study of Direct Immunofluorescence in Autoimmune Vesiculobullous Lesions with Clinical Correlation [PDF]
National Journal of Laboratory Medicine, 2019 Introduction: Autoimmune bullous lesions are diverse group of diseases characterised by blisters in the skin with or without mucosal lesions. They present with great degree of clinical and histopathological overlap; hence, advanced immunological ...
SAROJINI RAMAN, CHANDRA SEKHAR SIRKA
doaj +1 more source