Results 71 to 80 of about 5,131 (199)

Subtotal splenectomy in hereditary spherocytosis during childhood

, 2001
After splenectomy, the risk of patients with hereditary spherocytosis for sepsis and meningitis is increased for life (frequency 1.8% in our sample), in order to preserve the immunologic function of the spleen, we performed subtotal splenectomies in 18 ...
Langendorfer, C. M., Heidemann, P., Mex, G., Reinhardt, D., Eber, S. W., Riekhof, J., Bolkenius, M., Stohr, G.   +7 more
core   +1 more source

Giant right ventricular outflow tract thrombus in hereditary spherocytosis: a case report [PDF]

, 2016
Background: In hereditary spherocytosis with severe anemia, splenectomy is a recommended treatment. However, the spleen carries an important role both in immune function and coagulation.
Larsen, Terje H., Lønnebakken, Mai Tone, Terje Hjalmar Larsen, Eva Gerdts, Mai Tone Lønnebakken, Cedric Davidsen, Gerdts, Eva, Davidsen, Cedric   +7 more
core   +1 more source

Complications of delayed diagnosis and challenges: successfully managed SPTB gene variant hereditary spherocytosis with hepatocellular jaundice—a case report

Journal of Medical Case Reports
Background Hereditary spherocytosis is a rare genetic disorder of the red blood cell membrane that is characterized by anemia, jaundice, and splenomegaly; however, in the absence of family history and with unusual clinical presentation, the diagnosis ...
Sintayehu Mekonnen, Dereje Adefris, Belete Shikuro, Abdi Bati, Daniel Azmeraw, Temesegen Kassa, Eliud Teshome, Hawi Farris   +7 more
doaj   +1 more source

Simultaneous gallbladder-preserving cholecystolithotomy and laparoscopic splenectomy as a surgical option for hereditary spherocytosis in a child: A case report

Journal of Pediatric Surgery Case Reports, 2017
For hereditary spherocytosis complicated by cholelithiasis, cholecystectomy is simultaneously performed with splenectomy. However, jaundice promptly disappears after removing the spleen, and the risk for recurrent cholelithiasis decreases in majority of ...
Yutaka Yamada, Akinori Sekioka, Akiyoshi Nomura, Kei Oyama, Toshiaki Takahashi, Masaya Yamoto, Koji Fukumoto, Naoto Urushihara   +7 more
doaj   +1 more source

Hereditary spherocytosis.

, 2009
Hereditary spherocytosis (HS) is a familial hemolytic disorder with marked heterogeneity of clinical features, ranging from an asymptomatic condition to a fulminant hemolytic anemia.
Babadoko, AA, Hassan, A, Isa, AH, Abunimye, P   +3 more
core  

Spherocytosis - 5

, 2018
An image from a peripheral blood smear demonstrating marked spherocytosis and polychromasia in hereditary spherocytosis (100X oil immersion).
Kwon, Gloria
core   +1 more source

Human parvovirus infection and aplastic crisis in hereditary spherocytosis

Current Medicine Research and Practice, 2011
Parvovirus B19 is usually associated with an acute, self-limiting disease. In patients with congenital haemolytic anaemia, infection with this virus can cause an aplastic crisis.
A Gogia, A Kakar, S P Byotra, U Parakh, M Bhargava   +4 more
doaj  

Aplastic crisis in a child with hereditary spherocytosis with a strong family history resolving with supportive care

, 2018
Hereditary spherocytosis (HS) is a familial hemolytic disorder with marked heterogeneity. Clinical features range from asymptomatic to fulminant hemolytic anaemia.
Shankar Vangalpudi V., Balaji M. D., Vadlamudy Vinay   +2 more
core   +1 more source

An overview of hereditary spherocytosis and the curative effects of splenectomy

Frontiers in Physiology
Hereditary spherocytosis is a common hemolytic anemia with different severity. The causes of hereditary spherocytosis are mutations in genes that encode red blood cell (RBC) membrane and cytoskeletal proteins, including ankyrin-1, Band 3 (or AE1), α ...
Kyril Turpaev, Elizaveta Bovt, Elizaveta Bovt, Soslan Shakhidzhanov, Soslan Shakhidzhanov, Elena Sinauridze, Elena Sinauridze, Nataliya Smetanina, Larisa Koleva, Larisa Koleva, Nikita Kushnir, Nikita Kushnir, Anna Suvorova, Fazoil Ataullakhanov, Fazoil Ataullakhanov, Fazoil Ataullakhanov   +15 more
doaj   +1 more source

A rare case of post-splenectomy gastric volvulus managed by laparoscopic anterior gastropexy

Journal of Minimal Access Surgery, 2017
We report an extremely rare case of recurrent gastric volvulus after open splenectomy for hereditary spherocytosis. The initial episode was managed by endoscopic derotation.
Rahul Amreesh Gupta, Rinki Das, Ganga Ram Verma   +2 more
doaj   +1 more source