Results 91 to 100 of about 6,512 (195)
Extramedullary paraspinal hematopoiesis in hereditary spherocytosis
Hereditary spherocytosis (HS) is a common inherited hemolytic anemia due to red cell membrane defects. Extramedullary hematopoiesis is a compensatory response to insufficient bone marrow blood cell production.
Gogia P, Goel R, Nayar S
doaj
Partial deficiency of erythrocyte spectrin in hereditary spherocytosis.
Hereditary spherocytosis (HS) is a common, clinically heterogeneous haemolytic anaemia in which the primary erythrocyte defect is believed to be some abnormality in the spectrin-actin membrane skeleton, leading to loss of surface membrane.
William H. Zinkham +9 more
core +1 more source
Hereditary Spherocytosis: Recent Experience and Current Concepts of Pathophysiology
Hereditary spherocytosis is a clinically heterogeneous, genetically determined red blood cell membrane disorder resulting in hemolytic anemia. A deficiency of spectrin, the largest and most abundant structural protein of the erythrocyte membrane skeleton,
CROOM, ROBERT +3 more
core +1 more source
SCREENING TESTS FOR SPHEROCYTOSIS [PDF]
A, Zanella, G, Sirchia
openaire +2 more sources
The aim of the work was to study the peculiarities of the influence of bloodfactors on the development of spherocytosis in patients with coronary disease and arterial hypertension.
Y. I. Pivovarov +3 more
doaj
Open heart surgery in presence of hereditary spherocytosis
A patient with ostium secundum atrial septal defect was operated upon despite having hereditary spherocytosis, without any hemolytic effects of cardiopulmonary bypass.
core
Marked reduction of spectrinin hereditary spherocytosis in the common house mouse.
In contrast to the disease in humans, hereditary spherocytosis in the common house mouse produces an extreme spherocytosis. The cells show a broad distribution in size ranging from microcytic to macrocytic.
Shohet, S B +2 more
core
A novel <i>ANK1</i> gene mutation associated with hereditary spherocytosis: a case report. [PDF]
Lai M +7 more
europepmc +1 more source

