Results 191 to 200 of about 11,518 (218)

MRI of sporadic Creutzfeldt–Jakob disease

Journal of Medical Imaging and Radiation Oncology, 2008
SummaryThe key MRI findings in five cases of sporadic Creutzfeldt–Jakob disease (CJD) are illustrated with four ‘definite’ and one ‘probable’ according to World Health Organization criteria. Close attention to fluid‐attenuation inversion recovery and diffusion‐weighted imaging sequences are important for diagnosis, noting especially restricted ...
A, Kong, T, Kleinig, A, Van der Vliet, P, Bergin, C, Coscia, S, Ring, R, Brooder   +6 more
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Sporadic Creutzfeldt Jakob disease in two adolescents

Journal of Neurology, Neurosurgery & Psychiatry, 2008
Sporadic Creutzfeldt-Jakob disease (CJD) is a condition predominantly affecting older age groups, with cases aged less than 45 years rare and an age at onset or death of less than 20 years exceptional.Data from the systematic study of sporadic CJD in the UK are available from 1970 onwards.
K, Murray, D L, Ritchie, M, Bruce, C A, Young, M, Doran, J W, Ironside, R G, Will   +6 more
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FLAIR MRI in sporadic Creutzfeldt–Jakob disease

Neurology, 2000
Creutzfeldt–Jakob disease (CJD) is a rapidly progressive and ultimately lethal dementing illness caused by an infectious protein named prion. Besides cognitive decline and psychiatric or behavioral abnormalities, various other neurologic deficits appear. Myoclonic jerking, in particular startle myoclonus, is seen most commonly.
A F, Vrancken, C J, Frijns, L M, Ramos
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Sporadic Creutzfeldt‐Jakob disease in two coworkers

Neurology, 1986
We report the coincidence of pathologically confirmed sporadic CJD in two unrelated schoolteachers who shared a school wing for 9 months. The first developed ataxia, tremulousness, and dementia 5 months after his last contact with his colleague. Diagnosis of CJD was made 2 months later by brain biopsy.
D B, Leiderman, K P, Decker, J, Borcich, D W, Choi   +3 more
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Risk factors for sporadic Creutzfeldt–Jakob disease

Annals of Neurology, 2008
AbstractObjectiveAlthough surgical transmission of Creutzfeldt–Jakob disease (CJD) has been demonstrated, these iatrogenic cases account for only a small proportion of all CJD cases. The majority are sporadic CJD (sCJD) cases of unknown cause. This study investigated whether some cases classified as sCJD might have an unrecognized iatrogenic basis ...
Hester J T, Ward, Dawn, Everington, Simon N, Cousens, Blaire, Smith-Bathgate, Michelle, Gillies, Katy, Murray, Richard S G, Knight, Peter G, Smith, Robert G, Will   +8 more
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Diagnostic Criteria for Sporadic Creutzfeldt-Jakob Disease

Archives of Neurology, 1996
Making a clinical diagnosis of sporadic Creutzfeldt-Jakob disease relies on the evaluation of rapidly progressive dementia, ataxia, myoclonus, changes on the electroencephalogram, and other neurological signs. A definite diagnosis, however, is confined to cases that have been evaluated neuropathologically or by equivalent diagnostic techniques.
H A, Kretzschmar, J W, Ironside, S J, DeArmond, J, Tateishi   +3 more
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First symptom in sporadic Creutzfeldt–Jakob disease

Neurology, 2006
Established clinical criteria for diagnosing sporadic Creutzfeldt–Jakob disease (sCJD) rely heavily on symptoms that appear late in the disease, such as myoclonus or akinetic mutism.1,2 Previous studies identified cognitive, cerebellar, and behavioral symptoms as common early symptoms of CJD (table).3-6 These studies designated symptoms as “early ...
G D, Rabinovici, P N, Wang, J, Levin, L, Cook, M, Pravdin, J, Davis, S J, DeArmond, N M, Barbaro, J, Martindale, B L, Miller, M D, Geschwind   +10 more
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Variant or sporadic Creutzfeldt-Jakob disease?

The Lancet, 2010
1raises a major question for the future of variant Creutzfeldt-Jakob disease (vCJD) epidemics and suggests the occurrence of a second wave in the heterozygous population. In the reported case, diagnosis was based on clinical fi ndings and the results of magnetic resonance imaging (MRI).
J-P Brandel, D Galanaud, L Freeman, JL Laplanche, S Haik   +4 more
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Sporadic Creutzfeldt-Jakob Disease.

2011
The book chapter describes the epidemiology, genetics, clinical features, imaging and laboratory findings, histopathology (including immunohistochemistry and ultrastructure), molecular pathology, subtype classification and differential diagnosis of sporadic Creutzfeldt-Jakob disease, the most common human prion disease.
Budka H., Head M. W., Ironside J. W., Gambetti P., PARCHI, PIERO, Tagliavini F.   +5 more
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Sporadic Creutzfeldt–Jakob Disease Appears to Be Sporadic Fatal Insomnia: A Case Report and Review of the Literature

Nature and Science of Sleep, 2021
Li Cui
exaly