Results 171 to 180 of about 7,037 (201)

Sporadic Creutzfeldt-Jakob disease

The American Journal of Emergency Medicine, 2022
Being considered among the most fatal neurological conditions, Creutzfeldt-Jakob disease is a transmissible spongiform encephalopathy characterized by its unknown etiology and rapidly progressive neurodegenerative symptoms that often lead to a mean survival of 6 to 12 months.
Parnia, Salehi, Mark, Clark, Jeffer, Pinzon, Abhijit, Patil   +3 more
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MRI of sporadic Creutzfeldt–Jakob disease

Journal of Medical Imaging and Radiation Oncology, 2008
SummaryThe key MRI findings in five cases of sporadic Creutzfeldt–Jakob disease (CJD) are illustrated with four ‘definite’ and one ‘probable’ according to World Health Organization criteria. Close attention to fluid‐attenuation inversion recovery and diffusion‐weighted imaging sequences are important for diagnosis, noting especially restricted ...
A, Kong, T, Kleinig, A, Van der Vliet, P, Bergin, C, Coscia, S, Ring, R, Brooder   +6 more
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Sporadic Creutzfeldt–Jakob Disease—A Review

International Journal of Neuroscience, 2009
The objective is to study a patient with sporadic Creutzfeldt-Jakob disease (CJD). The patient, a 70-year-old woman with a history spanning over 1 month, with acute onset, progressive abnormal behavior, and cognitive decline with generalized asymmetrical myoclonic jerking, startle phenomenon, and cortical blindness, was referred to the hospital.
Stuti, Sharma, Madhurima, Mukherjee, Vivekananda, Kedage, Manjunatha S, Muttigi, Anjali, Rao, Suryanarayana, Rao   +5 more
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Cerebrospinal Fluid Markers in Sporadic Creutzfeldt-Jakob Disease

International Journal of Molecular Sciences, 2011
Sporadic Creutzfeldt-Jakob disease (sCJD) is the commonest form of human prion diseases, accounting for about 85% of all cases. Current criteria for intra vitam diagnosis include a distinct phenotype, periodic sharp and slow-wave complexes at electroencephalography (EEG), and a positive 14-3-3-protein assay in the cerebrospinal fluid (CSF).
Gianluigi Zanusso, Michele Fiorini, Sérgio Ferrari   +2 more
exaly   +3 more sources

Diagnostic Criteria for Sporadic Creutzfeldt-Jakob Disease

Archives of Neurology, 1996
Making a clinical diagnosis of sporadic Creutzfeldt-Jakob disease relies on the evaluation of rapidly progressive dementia, ataxia, myoclonus, changes on the electroencephalogram, and other neurological signs. A definite diagnosis, however, is confined to cases that have been evaluated neuropathologically or by equivalent diagnostic techniques.
H A, Kretzschmar, J W, Ironside, S J, DeArmond, J, Tateishi   +3 more
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Risk factors for sporadic Creutzfeldt–Jakob disease

Annals of Neurology, 2008
AbstractObjectiveAlthough surgical transmission of Creutzfeldt–Jakob disease (CJD) has been demonstrated, these iatrogenic cases account for only a small proportion of all CJD cases. The majority are sporadic CJD (sCJD) cases of unknown cause. This study investigated whether some cases classified as sCJD might have an unrecognized iatrogenic basis ...
Hester J T, Ward, Dawn, Everington, Simon N, Cousens, Blaire, Smith-Bathgate, Michelle, Gillies, Katy, Murray, Richard S G, Knight, Peter G, Smith, Robert G, Will   +8 more
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First symptom in sporadic Creutzfeldt–Jakob disease

Neurology, 2006
Established clinical criteria for diagnosing sporadic Creutzfeldt–Jakob disease (sCJD) rely heavily on symptoms that appear late in the disease, such as myoclonus or akinetic mutism.1,2 Previous studies identified cognitive, cerebellar, and behavioral symptoms as common early symptoms of CJD (table).3-6 These studies designated symptoms as “early ...
G D, Rabinovici, P N, Wang, J, Levin, L, Cook, M, Pravdin, J, Davis, S J, DeArmond, N M, Barbaro, J, Martindale, B L, Miller, M D, Geschwind   +10 more
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Sporadic Creutzfeldt Jakob disease in two adolescents

Journal of Neurology, Neurosurgery & Psychiatry, 2008
Sporadic Creutzfeldt-Jakob disease (CJD) is a condition predominantly affecting older age groups, with cases aged less than 45 years rare and an age at onset or death of less than 20 years exceptional.Data from the systematic study of sporadic CJD in the UK are available from 1970 onwards.
K, Murray, D L, Ritchie, M, Bruce, C A, Young, M, Doran, J W, Ironside, R G, Will   +6 more
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Sporadic Creutzfeldt‐Jakob disease in two coworkers

Neurology, 1986
We report the coincidence of pathologically confirmed sporadic CJD in two unrelated schoolteachers who shared a school wing for 9 months. The first developed ataxia, tremulousness, and dementia 5 months after his last contact with his colleague. Diagnosis of CJD was made 2 months later by brain biopsy.
D B, Leiderman, K P, Decker, J, Borcich, D W, Choi   +3 more
openaire   +2 more sources