Results 21 to 30 of about 35,690 (223)
Pulmonary Vein Stenosis Associated with Germline PIK3CA Mutation
Pulmonary vein stenosis is a rare and frequently lethal childhood disease. There are few known genetic associations, and the pathophysiology is not well known. Current treatments include surgery, interventional cardiac catheterization, and more recently,
Delphine Yung +5 more
core +1 more source
Outcomes in Establishing Individual Vessel Patency for Pediatric Pulmonary Vein Stenosis
The purpose of this study was to determine what patient and pulmonary vein characteristics at the diagnosis of intraluminal pulmonary vein stenosis (PVS) are predictive of individual vein outcomes.
Christopher W. Baird +9 more
core +1 more source
Pulmonary Vein Stenosis: A Rare Disease with a Global Reach
Pulmonary vein stenosis (PVS) is a rare, but high mortality and resource intensive disease caused by mechanical obstruction or intraluminal myofibroproliferation, which can be post-surgical or idiopathic.
Jennifer Schramm +6 more
core +1 more source
Management of Pediatric Pulmonary Vein Stenosis
Pediatric intraluminal pulmonary vein stenosis has evolved into a chronic illness, with improving survival. Although significant knowledge gaps remain, medical providers have found success in the management of patients with pulmonary vein stenosis using a comprehensive multimodality treatment strategy. This review discusses the core principles employed
Ryan Callahan +3 more
openaire +2 more sources
Congenital Stenosis of Individual Pulmonary Veins [PDF]
The case is reported of an infant with congenital stenosis of each of the four individual pulmonary veins near the left atrium. The characteristic features were failure to thrive, increasing cyanosis and dyspnea, and death in congestive cardiac failure at 7 months of age. A precordial systolic murmur and an early systolic ejection click were heard; the
J D, SHONE +4 more
openaire +2 more sources
Atrial Flutter as a Late Presentation of Scimitar Vein in an Adult With Prior ASD Repair. [PDF]
ABSTRACT Adult patients with unexplained atrial arrhythmias and right heart dilation should prompt consideration of congenital anomalies such as scimitar vein, even decades after atrial septal defect repair. Early recognition using multi‐modality imaging may prevent delayed diagnosis and progressive cardiopulmonary complications.
Rastegarnasab F +3 more
europepmc +2 more sources
Aspiration Is Associated with Poor Treatment Response in Pediatric Pulmonary Vein Stenosis
Intraluminal pulmonary vein stenosis is a disease with significant morbidity and mortality, though recent progress has been made using multimodal therapy with antiproliferative agents.
Kathy J. Jenkins +3 more
core +1 more source
Pulmonary vein stenosis: Challenges ahead [PDF]
In this issue of the Journal, Quinonez and colleagues 1 report their experience with and treatment of 49 patients with pulmonary vein stenosis. This article takes on the very difficult challenge to map out the ‘‘relentless’’ nature of multivessel pulmonary vein stenosis and the multidisciplinary commitments that are required for its treatment.
Victor T, Tsang, Phan-Kiet, Tran
openaire +2 more sources
Background—Pulmonary vein stenosis (PVST) is a well-known complication of pulmonary vein isolation (PVI). Specific anatomically designed ablation catheters for antral PVI have not been evaluated with regard to the incidence of PVST.
Hamer, Okka W +18 more
core +1 more source
Congenital pulmonary vein stenosis (PVnS) can happen as a focal stenosis at the atrial connection site or complete hypoplasia in one or more of the pulmonary veins. Indeed, the primary form of PVnS with a pathological appearance similar to that in childhood cases has been reported rarely in unoperated adult patients [1, 2].
Arash Gohari, Adina Haramati
+4 more sources

