Results 101 to 110 of about 184 (130)

Neurologic Injury in Isolated Sulfite Oxidase Deficiency

Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques, 2014
Background:We review clinical, neuroimaging, and genetic information on six individuals with isolated sulfite oxidase deficiency (ISOD).Methods:All patients were examined, and clinical records, biochemistry, neuroimaging, and sulfite oxidase gene (SUOX) sequencing were reviewed.Results:Data was available on six individuals from four nuclear families ...
Thomas M, Bosley, Ibrahim A, Alorainy, Darren T, Oystreck, Ali M, Hellani, Mohammed Z, Seidahmed, Mohamed El Faki, Osman, Mohamed A, Sabry, Mohamed S, Rashed, Eiman A, Al-Yamani, Khaled K, Abu-Amero, Mustafa A, Salih   +10 more
openaire   +2 more sources

The reaction of chicken liver sulfite oxidase with dimethylsulfite

Biochimica et Biophysica Acta (BBA) - Protein Structure and Molecular Enzymology, 1995
We have undertaken a steady-state and rapid kinetic study of the reaction of enzyme with sulfite and dimethylsulfite. Methylation of sulfite results in a significant increase in Km and Kd for the substrate in the course of steady-state and rapid reaction kinetics, respectively, but kcat and the limiting rate constant for enzyme reduction (kred) are ...
M S, Brody, R, Hille
openaire   +2 more sources

The Kinetic Behavior of Chicken Liver Sulfite Oxidase

Biochemistry, 1999
A comprehensive kinetic study of sulfite oxidase has been undertaken over the pH range 6.0-10.0, including conventional steady-state work as well as rapid kinetic studies of both the reaction of oxidized enzyme with sulfite and reduced enzyme with cytochrome c (III).
M S, Brody, R, Hille
openaire   +2 more sources

A Hybrid Enzyme Biosensor Based on Sulfite Oxidase and Glucose Oxidase for the Analyzing of Sulfite and Glucose

2012
In this study, we developed a hybrid biosensor based on sulfite oxidase and glucose oxidase for determination of sulfite and glucose. The principle of the measurements was based on the determination of the decrease in the differentiation of oxygen level which had been caused by the catalytic reactions of the enzymes in the bioactive layer of the ...
Sezgintürk M.K., Alaçam S., Altug Ç., Akbayirli P., Dinçkaya E.   +4 more
openaire   +3 more sources

Hepatic sulfite oxidase

Biochimica et Biophysica Acta (BBA) - Enzymology, 1974
Dale L. Kessler, K.V. Rajagopalan
openaire   +1 more source

Sulfite oxidase

1994
D. Schomburg, M. Salzmann, D. Stephan
openaire   +1 more source

Isolated sulfite oxidase deficiency

2005
Isolated sulfite oxidase deficiency is a very rare autosomal recessive disorder associated with metabolism of sulfur containing amino acids. A 4-month-old girl with intractable seizures and feeding difficulty diagnosed as isolated sulfite oxidase deficiency is presented.
Gurer, Yahya Kemal Yavuz, Senbil, Nesrin, EZGÜ, FATİH SÜHEYL, Tosun, Mahya Sultan   +3 more
openaire   +1 more source

Isolated sulfite oxidase deficiency

2018
Isolated sulfite oxidase deficiency (ISOD) is a life-threatening, autosomal recessive disease characterized by severe neurological impairment. As no long-term effective treatment is available, distinction from other treatable diseases, such as molybdenum cofactor deficiency (MoCD) type A, should be made.
Claerhout, Helena, Witters, Peter, Régal, Luc, Jansen, Katrien, Van Hoestenberghe, Marie-Rose, Breckpot, Jeroen, Vermeersch, Pieter   +6 more
openaire   +1 more source

Adenosine 5′ phosphosulfate reductase and sulfite oxidase regulate sulfite-induced water loss in Arabidopsis

Journal of Experimental Botany, 2021
Assylay Kurmanbayeva, Aigerim Soltabayeva, Sudhakar Srivastava   +2 more
exaly  

Molybdenum Trioxide Nanoparticles with Intrinsic Sulfite Oxidase Activity

ACS Nano, 2014
Ruben Ragg, Filipe Natalio, Wolfgang Tremel   +2 more
exaly