Results 101 to 110 of about 155,517 (152)

Isolated sulfite oxidase deficiency: a founder mutation. [PDF]

Cold Spring Harb Mol Case Stud, 2020
Mhanni AA, Greenberg CR, Spriggs EL, Agatep R, Sisk RR, Prasad C.   +5 more
europepmc   +1 more source

The sulfite oxidase family of molybdenum enzymes

, 2016
The sulfite oxidase enzyme superfamily is a large enzyme family of molybdenum-containing enzymes dominated by bacterial systems. Most of the characterized representatives of this enzyme family convert S- or N-containing substrates, and at least one of ...
Kappler, Ulrike, Schwarz, Guenter, Ulrike Kappler, Guenter Schwarz   +3 more
core   +1 more source

Kinetic studies on the reaction of formaldehyde with amines in the presence of sulfite [PDF]

, 1999
The reaction of formaldehyde with amines with and without sulfite has been studied using anilines (RC(_6)H(_4)NH(_2)) and benzylamines (RC(_6)H(_4)CH(_2)NH(_2)). Reaction with anilines is known to produce aminomethanesulfonates, RC(_6)H(_4)NHCH(_2)SO(_3)(
Brown, Kathryn Helen
core  

Physical studies and synthetic modeling of the molybdenum-containing enzyme sulfite oxidase.

, 1988
This research has been directed at the study of both the enzyme sulfite oxidase and molybdenum model chemistry. A modification of a previously published procedure has been used to purify sulfite oxidase in high yield which is well-suited for experiments ...
Kipke, Cary Alan.
core   +3 more sources

Sulfite-mediated oxidative stress in kidney cells

, 2004
Background. Chronic renal failure has been associated with oxidative stress. Serum sulfite, sulfate, cysteine, homocysteine, cysteine sulfinic acid, and ƒÁ-glutamylcysteine are elevated in patients on hemodialysis, suggesting an accelerated catabolism of
Halliwell, B (15527180), Wong, KP (15527165), Lim, BG (15527174), Tan, J (15527177), Whiteman, M (15527168), Vincent, AS (15527171), Cheung, NS (15524789)   +6 more
core  

Delineating the phenotypic spectrum of sulfite oxidase and molybdenum cofactor deficiency. [PDF]

Neurol Genet, 2020
Misko AL, Liang Y, Kohl JB, Eichler F.
europepmc   +1 more source

Effect of sulfite treatment on total antioxidant capacity, total oxidant status, lipid hydroperoxide, and total free sulfydryl groups contents in normal and sulfite oxidase-deficient rat plasma

, 2009
Sulfites, which are commonly used as preservatives, are continuously formed in the body during the metabolism of sulfur-containing amino acids. Sulfite oxidase (SOX) is an essential enzyme in the pathway of the oxidative degradation of sulfite to sulfate
Erel, O., Celik, H., Herken, Emine Nur, Küçükatay, Vural, Kocamaz, Erdoğan, EREL, ÖZCAN, Celik, Hakim   +6 more
core   +1 more source

Internalization of the Aspergillus nidulans AstA Transporter into Mitochondria Depends on Growth Conditions, and Affects ATP Levels and Sulfite Oxidase Activity. [PDF]

Int J Mol Sci, 2020
Piłsyk S, Mieczkowski A, Golan MP, Wawrzyniak A, Kruszewska JS.   +4 more
europepmc   +1 more source

Ultra-orphan diseases: A cross-sectional quantitative analysis of the natural history of isolated sulfite oxidase deficiency. [PDF]

PLoS One
Göde L, Zielonka M, Garbade SF, Posset R.   +3 more
europepmc   +1 more source

Second-Coordination-Sphere Effects Reveal Electronic Structure Differences between the Mitochondrial Amidoxime Reducing Component and Sulfite Oxidase. [PDF]

Inorg Chem
Struwe MA, Yang J, Kolanji K, Mengell J, Scheidig AJ, Clement B, Kirk ML.   +6 more
europepmc   +1 more source