Results 31 to 40 of about 9,331 (171)

Guía de profilaxia y tratamiento antitrombótico para pacientes con COVID-19. Consenso del Grupo Cooperativo Latinoamericano en Hemostasia y Trombosis (CLAHT)

open access: yesArchivos de Cardiología de México, 2021
La coagulopatía y la trombosis asociadas a la enfermedad por coronavirus 2019 (COVID-19) representan un problema importante en el manejo de esta enfermedad.
Cecilia Guillermo-Esposito   +7 more
doaj   +1 more source

Impact of Family History of Haemophilia on Diagnosis, Management and Outcomes in Severe Haemophilia

open access: yesHaemophilia, Volume 31, Issue 4, Page 679-686, July 2025.
ABSTRACT Introduction Patients with severe haemophilia A (HA) with no family history of haemophilia will be diagnosed upon their first bleeding event. Methods Herein, we studied the effects of lack of family history in HA and the subsequent delay of diagnosis on bleeding pattern and early treatment, as well as on the risk of inhibitor development.
Ana Mendoza   +9 more
wiley   +1 more source

Arteritis de Takayasu y aneurisma gigante en escolar. Reporte de caso

open access: yesRevista Colombiana de Cardiología, 2012
La arteritis de Takayasu es una vasculitis de grandes vasos que afecta a la aorta y sus ramas principales, llevando a estenosis y trombosis, así como a la formación de aneurismas.
Ernesto Vallejo, MD   +2 more
doaj   +1 more source

Hughes–Stovin Syndrome: A Rare Cause of Pulmonary Artery Aneurysm and Thrombosis—A Case Report

open access: yesInternational Journal of Rheumatic Diseases, Volume 28, Issue 4, April 2025.
ABSTRACT Hughes–Stovin Syndrome (HSS) is a rare, life‐threatening condition characterized by thrombophlebitis and pulmonary artery aneurysms, often viewed as a variant of Behçet's disease. Its diagnosis and management are challenging due to its rarity and overlapping symptoms with other vascular disorders.
Abdul Qadir   +3 more
wiley   +1 more source

SÍNDROME DE PLAQUETAS PEGAJOSAS: REPORTE DE CASO

open access: yesRevista Médica de la Universidad de Costa Rica, 2022
El Síndrome de Plaquetas Pegajosas es un trastorno autosómico dominante caracterizado por alteraciones de la agregación plaquetaria en respuesta a la epinefrina y/o el fosfato de adenosina, el cual favorece fenómenos trombóticos arteriales y venosos ...
Daniel Casares-Fallas   +1 more
doaj   +1 more source

A phase 1/2 safety and efficacy study of TAK‐754 gene therapy: The challenge of achieving durable factor VIII expression in haemophilia A clinical trials

open access: yesHaemophilia, Volume 31, Issue 1, Page 108-117, January 2025.
Abstract Introduction Haemophilia A is an X‐linked bleeding disorder resulting from a deficiency of factor VIII (FVIII). To date, multiple gene therapies have entered clinical trials with the goal of providing durable haemostatic protection from a single dose. TAK 754 (BAX 888) is an investigational AAV8‐based gene therapy containing a FVIII transgene.
John Chapin   +13 more
wiley   +1 more source

Trombosis de válvulas cardiacas biológicas. Presentación de dos casos evaluados con ecocardiografía 3D en tiempo real

open access: yesRevista Colombiana de Cardiología, 2011
La trombosis de las válvulas protésicas biológicas es una complicación infrecuente, que se asocia con mortalidad elevada. En este artículo se reporta el caso de un paciente de género masculino, de 72 años de edad, con prótesis valvular biológica en ...
Jairo A. Rendón, MD   +1 more
doaj   +1 more source

Humanistic burden of haemophilia A without inhibitors: A cross‐sectional analysis of the HemoLIFE study

open access: yesHaemophilia, Volume 30, Issue 4, Page 950-958, July 2024.
Abstract Aim To evaluate the impact of haemophilia A without inhibitors on humanistic outcomes in patients and caregivers. Herein, we report a cross‐sectional analysis of the baseline data of persons with haemophilia (PWH) participating in the prospective study HEMOLIFE. Methods These data are part of a prospective, observational, and multicentre study
María Teresa Álvarez‐Román   +11 more
wiley   +1 more source

Trombosis venosas múltiples de instauración rápida [PDF]

open access: yes, 2019
61 year old male with rapid establishment of bilateral venous thrombosis and multiorgan failure.Varón de 61 años con trombosis venosa bilateral de rápida instauración y fracaso ...
Torres del Pliego, Elisa   +5 more
core   +2 more sources

Thrombocytopenic thrombotic purpura related to COVID-19 vaccine: apropos of 4 cases [PDF]

open access: yesHematology, Transfusion and Cell Therapy
Célia Dos Santos   +12 more
doaj   +2 more sources

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