Results 31 to 40 of about 9,331 (171)
La coagulopatía y la trombosis asociadas a la enfermedad por coronavirus 2019 (COVID-19) representan un problema importante en el manejo de esta enfermedad.
Cecilia Guillermo-Esposito +7 more
doaj +1 more source
Impact of Family History of Haemophilia on Diagnosis, Management and Outcomes in Severe Haemophilia
ABSTRACT Introduction Patients with severe haemophilia A (HA) with no family history of haemophilia will be diagnosed upon their first bleeding event. Methods Herein, we studied the effects of lack of family history in HA and the subsequent delay of diagnosis on bleeding pattern and early treatment, as well as on the risk of inhibitor development.
Ana Mendoza +9 more
wiley +1 more source
Arteritis de Takayasu y aneurisma gigante en escolar. Reporte de caso
La arteritis de Takayasu es una vasculitis de grandes vasos que afecta a la aorta y sus ramas principales, llevando a estenosis y trombosis, así como a la formación de aneurismas.
Ernesto Vallejo, MD +2 more
doaj +1 more source
Hughes–Stovin Syndrome: A Rare Cause of Pulmonary Artery Aneurysm and Thrombosis—A Case Report
ABSTRACT Hughes–Stovin Syndrome (HSS) is a rare, life‐threatening condition characterized by thrombophlebitis and pulmonary artery aneurysms, often viewed as a variant of Behçet's disease. Its diagnosis and management are challenging due to its rarity and overlapping symptoms with other vascular disorders.
Abdul Qadir +3 more
wiley +1 more source
SÍNDROME DE PLAQUETAS PEGAJOSAS: REPORTE DE CASO
El Síndrome de Plaquetas Pegajosas es un trastorno autosómico dominante caracterizado por alteraciones de la agregación plaquetaria en respuesta a la epinefrina y/o el fosfato de adenosina, el cual favorece fenómenos trombóticos arteriales y venosos ...
Daniel Casares-Fallas +1 more
doaj +1 more source
Abstract Introduction Haemophilia A is an X‐linked bleeding disorder resulting from a deficiency of factor VIII (FVIII). To date, multiple gene therapies have entered clinical trials with the goal of providing durable haemostatic protection from a single dose. TAK 754 (BAX 888) is an investigational AAV8‐based gene therapy containing a FVIII transgene.
John Chapin +13 more
wiley +1 more source
La trombosis de las válvulas protésicas biológicas es una complicación infrecuente, que se asocia con mortalidad elevada. En este artículo se reporta el caso de un paciente de género masculino, de 72 años de edad, con prótesis valvular biológica en ...
Jairo A. Rendón, MD +1 more
doaj +1 more source
Abstract Aim To evaluate the impact of haemophilia A without inhibitors on humanistic outcomes in patients and caregivers. Herein, we report a cross‐sectional analysis of the baseline data of persons with haemophilia (PWH) participating in the prospective study HEMOLIFE. Methods These data are part of a prospective, observational, and multicentre study
María Teresa Álvarez‐Román +11 more
wiley +1 more source
Trombosis venosas múltiples de instauración rápida [PDF]
61 year old male with rapid establishment of bilateral venous thrombosis and multiorgan failure.Varón de 61 años con trombosis venosa bilateral de rápida instauración y fracaso ...
Torres del Pliego, Elisa +5 more
core +2 more sources
Thrombocytopenic thrombotic purpura related to COVID-19 vaccine: apropos of 4 cases [PDF]
Célia Dos Santos +12 more
doaj +2 more sources

