Results 41 to 50 of about 8,926 (205)
Abstract Introduction Haemophilia A is an X‐linked bleeding disorder resulting from a deficiency of factor VIII (FVIII). To date, multiple gene therapies have entered clinical trials with the goal of providing durable haemostatic protection from a single dose. TAK 754 (BAX 888) is an investigational AAV8‐based gene therapy containing a FVIII transgene.
John Chapin +13 more
wiley +1 more source
La trombosis de las válvulas protésicas biológicas es una complicación infrecuente, que se asocia con mortalidad elevada. En este artículo se reporta el caso de un paciente de género masculino, de 72 años de edad, con prótesis valvular biológica en ...
Jairo A. Rendón, MD +1 more
doaj +1 more source
SÍNDROME DE PLAQUETAS PEGAJOSAS: REPORTE DE CASO
El Síndrome de Plaquetas Pegajosas es un trastorno autosómico dominante caracterizado por alteraciones de la agregación plaquetaria en respuesta a la epinefrina y/o el fosfato de adenosina, el cual favorece fenómenos trombóticos arteriales y venosos ...
Daniel Casares-Fallas +1 more
doaj +1 more source
Abstract Aim To evaluate the impact of haemophilia A without inhibitors on humanistic outcomes in patients and caregivers. Herein, we report a cross‐sectional analysis of the baseline data of persons with haemophilia (PWH) participating in the prospective study HEMOLIFE. Methods These data are part of a prospective, observational, and multicentre study
María Teresa Álvarez‐Román +11 more
wiley +1 more source
Este trabajo sintetiza el conocimiento de la enfermedad conocida como trombosis venosa profunda (TVP), a través de una revisión bibliográfica acerca de esta patología que proporciona información importante para el desarrollo del trabajo de investigación. Mediante el proceso de investigación se observa, que la trombosis venosa profunda es una enfermedad
Lisbeth Xiomara Valverde Barragán +3 more
openaire +1 more source
Le trombosi venose cerebrali rappresentano una rara varieta di accidente vascolare cerebrale che puo colpire persone di ogni eta. Tenuto conto della diversita delle loro eziologie, esse possono essere riscontrate in tutte le discipline. Hanno anche una presentazione clinica molto varia, che rende la loro diagnosi spesso difficile.
J. Mawet, I. Crassard, M.-G. Bousser
openaire +1 more source
Complement and transplant‐associated thrombotic microangiopathy: Current and future approaches
HemaSphere, Volume 10, Issue 4, April 2026.
Massimo Cugno +2 more
wiley +1 more source
Abstract Introduction Managing bleeding disorders (BDs) is complex, requiring a comprehensive approach coordinated by a multidisciplinary team (MDT). Haemophilia nurses (HNs) play a central role in the MDT, frequently coordinating care. As novel treatments bring change to the treatment landscape, ongoing education and development is key.
Greta Mulders +7 more
wiley +1 more source
Abstract Backgroud A huge amount of data about psychosocial issues of people with haemophilia (PwH) are available; however, these materials are fragmentary and largely outdated, failing to reflect the impact of current treatment strategies. Aim Describing the influence of illness on psychosocial aspects of adult PwH (≥18 years) and caregivers of ...
Arianna Fornari +15 more
wiley +1 more source
Trombosis venosa cerebral [PDF]
Itzel Ariadna Hernández Dehesa +2 more
openaire +1 more source

