Utrophin, MHC and M1/M2 macrophages in GRMD dogs
Ciência Animal Brasileira, 2020 Muscular dystrophies are hereditary diseases that lead to progressive degeneration of the skeletal musculature. Golden Retriever dogs are used as animal models because they show a hereditary muscle disease similar to muscular dystrophy in humans.
Gabriela Noronha de Toledo +1 more
doaj
Characterisation of alpha-dystrobrevin in muscle [PDF]
, 1998 Dystrophin-related and associated proteins are important for the formation and maintenance of the mammalian neuromuscular junction. Initial studies in the electric organ of Torpedo californica showed that the dystrophin-related protein dystrobrevin (87K)
Blake, D. J. +4 more
core
The role of basal and myogenic factors in the transcriptional activation of utrophin promoter A: implications for therapeutic up-regulation in Duchenne muscular dystrophy [PDF]
, 2001 Kathleen J. Perkins
openalex +1 more source
Prevention of pathology in mdx mice by expression of utrophin: analysis using an inducible transgenic expression system [PDF]
, 2002 Sarah Squire +7 more
openalex +1 more source
Utrophin Binds Laterally along Actin Filaments and Can Couple Costameric Actin with Sarcolemma When Overexpressed in Dystrophin-deficient Muscle [PDF]
, 2002 Inna N. Rybakova +4 more
openalex +1 more source
Functional role of downstream utrophin enhancer for utrophin expression in the skeletal muscle [PDF]
, 2008 制度:新 ; 報告番号:甲2676号 ; 学位の種類:博士(人間科学) ; 授与年月日:2008/7/16 ; 早大学位記番号 ...
谷端 淳
core +2 more sources
Comparative Analysis of the Human Dystrophin and Utrophin Gene Structures [PDF]
, 2002 Uberto Pozzoli +5 more
openalex +1 more source
Compensation for dystrophin-deficiency: ADAM12 overexpression in skeletal muscle results in increased 7 integrin, utrophin and associated glycoproteins [PDF]
, 2003 Behzad Moghadaszadeh
openalex +1 more source
Social stress is lethal in the mdx model of Duchenne muscular dystrophy
EBioMedicine, 2020 Background: Duchenne muscular dystrophy (DMD) is caused by the loss of dystrophin. Severe and ultimately lethal, DMD progresses relatively slowly in that patients become wheelchair bound only around age twelve with a survival expectancy reaching the ...
Maria Razzoli +10 more
doaj