iNOS Expression In Dystrophinopathies Can Be Reduced By Somatic Gene Transfer of Dystrophin or Utrophin [PDF]
, 2001 Jean‐Pierre Louboutin +4 more
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Utrophin, MHC and M1/M2 macrophages in GRMD dogs
Ciência Animal Brasileira, 2020 Muscular dystrophies are hereditary diseases that lead to progressive degeneration of the skeletal musculature. Golden Retriever dogs are used as animal models because they show a hereditary muscle disease similar to muscular dystrophy in humans.
Gabriela Noronha de Toledo +1 more
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The role of basal and myogenic factors in the transcriptional activation of utrophin promoter A: implications for therapeutic up-regulation in Duchenne muscular dystrophy [PDF]
, 2001 Kathleen J. Perkins
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Utrophin Binds Laterally along Actin Filaments and Can Couple Costameric Actin with Sarcolemma When Overexpressed in Dystrophin-deficient Muscle [PDF]
, 2002 Inna N. Rybakova +4 more
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Comparative Analysis of the Human Dystrophin and Utrophin Gene Structures [PDF]
, 2002 Uberto Pozzoli +5 more
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Prevention of pathology in mdx mice by expression of utrophin: analysis using an inducible transgenic expression system [PDF]
, 2002 Sarah Squire +7 more
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Utrophin upregulation in Duchenne muscular dystrophy.
Acta myologica : myopathies and cardiomyopathies : official journal of the Mediterranean Society of Myology, 2006 Duchenne Muscular Dystrophy (DMD) is a devastating, progressive muscle wasting disease for which there is currently no effective treatment. DMD is caused by mutations in the dystrophin gene many of which result in the absence of the large cytoskeletal protein dystrophin at the sarcolemma.
Hirst, R, McCullagh, K, Davies, K
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Compensation for dystrophin-deficiency: ADAM12 overexpression in skeletal muscle results in increased 7 integrin, utrophin and associated glycoproteins [PDF]
, 2003 Behzad Moghadaszadeh
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Role of dystrophin and utrophin for assembly and function of the dystrophin glycoprotein complex in non-muscle tissue [PDF]
, 2018 .: The dystrophin glycoprotein complex (DGC) is a multimeric protein assembly associated with either the X-linked cytoskeletal protein dystrophin or its autosomal homologue utrophin. In striated muscle cells, the DGC links the extracellular matrix to the
Fritschy, J., Haenggi, T.
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