Results 31 to 40 of about 4,273 (136)
ABSTRACT Squamoid Eccrine Ductal Carcinoma (SEDC) is a rare cutaneous adenexal carcinoma first described in 1997. It has distinct biphasic features on histology which commonly result in misdiagnosis as Bowen disease or cutaneous squamous cell carcinomas (cSCC) if diagnostic skin biopsies are too superficial. This may lead to a delay in diagnosis. It is
Xiang Li Tan +15 more
wiley +1 more source
Background Lymphoplasmacytic lymphoma/Waldenström macroglobulinemia rarely transforms into diffuse large B-cell lymphoma, and there have been no reports of cases proving clonal identity when presenting as primary central nervous system lymphoma.
Yuko Tanaka +19 more
doaj +1 more source
Macroglobulinemia de Waldenström con transformación a Linfoma del manto
La Macroglobulinemia de Waldenström (MW) es una enfermedad infrecuente con una incidencia de tres casos por millón de habitantes al año aproximadamente1 y cuyo diagnóstico siempre plantea importantes dudas.
M. Martínez Gabarrón +3 more
doaj +1 more source
Lymphoplasmacytic lymphoma (LPL)/Waldenström macroglobulinemia (WM) is an uncommon mature B cell lymphoma usually involving the bone marrow and, less commonly, the spleen and/or lymph nodes.
Saša Anžej Doma, Andrej Doma
doaj +1 more source
Cutaneous amyloidosis as the first presentation of Waldenstrom macroglobulinemia
Background: Waldenstrom macroglobulinemia is a lymphoplasmacytic lymphoma with elevated serum immunoglobulin M and multi-organ involvement. Primary systemic amyloidosis usually develops due to immunoglobulin light chains depositions in different organs ...
Rana Rafiei +2 more
doaj
Increased glutathione utilization augments tumor cell proliferation in Waldenstrom Macroglobulinemia
Metabolic reprogramming is a hallmark of cancer cells. In Waldenstrom Macroglobulinemia (WM), the infiltration of IgM-secreting lymphoplamacytic cells into the bone marrow (BM) could shift the homeostasis of proteins and metabolites towards a permissive ...
Shahrzad Jalali +13 more
doaj +1 more source
Clinical and Laboratory Characterization of Acquired Von Willebrand Syndrome
ABSTRACT Acquired von Willebrand Syndrome (AVWS) is a rare bleeding disorder characterized by quantitative or qualitative defects of von Willebrand factor (VWF) in patients without a personal or family history of bleeding. It is frequently associated with systemic diseases, particularly lymphoproliferative disorders (LPDs) and myeloproliferative ...
Alessandro Ciavarella +10 more
wiley +1 more source
Current approach to Waldenström Macroglobulinemia
Waldenström Macroglobulinemia (WM) is a unique, low grade, IgM lymphoplasmacytic lymphoma with a heterogeneous clinical course. A paucity of high-grade evidence from large phase 3 trials remains a major issue in the field despite a rapidly expanding ...
Gayathri Ravi, Prashant Kapoor
doaj +1 more source
Cumulative Antigen Suppression Reduces Clonal Plasma Cell Evolution in Gaucher Disease
ABSTRACT Chronic antigenic stimulation is implicated in the pathogenesis of monoclonal gammopathy and multiple myeloma, yet longitudinal human evidence linking sustained antigen exposure to modifiable clonal plasma cell evolution remains limited. Gaucher disease (GD), caused by biallelic GBA1 pathogenic variants, is characterized by accumulation of ...
Noor Ul Ain +10 more
wiley +1 more source
MACROGLOBULINEMIA DE WALDENSTROM: RELATO DE CASO
Introdução: A Macroglobulinemia de Waldenstrom (MW) é uma neoplasia hematológica rara das células B caracterizada por gamopatia monoclonal IgM no sangue periférico e linfoma linfoplasmocítico na medula óssea, sendo uma enfermidade predominantemente ...
IR Daloy +7 more
doaj +1 more source

