Results 11 to 20 of about 7,890 (255)

Refractory Periorbital Necrobiotic Xanthogranuloma Treated With Plasma Cell-Directed Therapy. [PDF]

EJHaem
eJHaem, Volume 7, Issue 1, February 2026.
Trando A, Jeong AR, Goodman AM.
europepmc   +2 more sources

Uncommon Encounter in Urachus: A Rare Case of Xanthogranulomatous Urachitis With Review of Literature. [PDF]

Clin Case Rep
ABSTRACT Urachus is a fibrous remnant from embryologic development derived from the allantois, which is involved in waste elimination in the fetus. Typically, it extends from the dome of the bladder to the umbilicus. Xanthogranulomatous urachitis, or xanthogranulomatous inflammation of the urachus, is a highly unusual pathological entity characterized ...
Raja Iyub MJ, Dhineshkumar P, Bagalkot FS, Katiah A, S P, Jahangir K, Sanker V, Dave T.   +7 more
europepmc   +2 more sources

Scleredema Associated With IgG/κ Monoclonal Gammopathy of Clinical Significance Successfully Treated With Daratumumab Monotherapy: A Case Report. [PDF]

EJHaem
ABSTRACT Background Cutaneous monoclonal gammopathy of clinical significance (MGCS) is rare and may present with scleredema‐like fibrosing skin disease. Case A 59‐year‐old man developed progressive induration of the upper body. Laboratory studies revealed an IgG/κ monoclonal protein, and skin biopsy showed dermal thickening with mucin deposition.
Marcolongo D, Bressan A, Zanatta E, Alaibac MSA, Gianesello I, Binotto G, Pavan L, Tos APD, Trentin L, Vianello F.   +9 more
europepmc   +2 more sources

Xanthogranuloma of the Sellar Region: A Comprehensive Review of Neuroimaging in a Rare Inflammatory Entity

Journal of Personalized Medicine, 2022
Xanthogranuloma of the sellar region is a rare chronic inflammatory lesion resulting from secondary hemorrhage, inflammation, infarction, and necrosis of an existing Rathke’s cleft cyst, craniopharyngioma, or pituitary adenoma.
Vera Lozovanu, C. Georgescu, Lavinia Maria Florescu, C. Georgiu, H. Silaghi, Andrian Fratea, C. Silaghi   +6 more
semanticscholar   +1 more source

Rare diseases leading to childhood Glaucoma. epidemiology, pathophysiogenesis, and management [PDF]

, 2015
Noteworthy heterogeneity exists in the rare diseases associated with childhood glaucoma. Primary congenital glaucoma is mostly sporadic; however, 10% to 40% of cases are familial. CYP1B1 gene mutations seem to account for 87% of familial cases and 27% of
Abdolrahimzadeh, Solmaz, CONTESTABILE, Maria Teresa, FAMELI, VALERIA, Mollo, Roberto, Perdicchi, Andrea, RECUPERO, Santi Maria   +5 more
core   +7 more sources

Surgical Treatment for Adult-Onset Limbal Xanthogranuloma: A Case Report with 4-Year Follow-Up

Case Reports in Ophthalmology, 2022
Xanthogranuloma is a benign histiocytic disorder that generally appears in infants and children and often called juvenile xanthogranuloma (JXG). Typical reddish-yellow cutaneous papules or nodules are the most common presentation of JXG.
Pichaya Chuephanich, Warissara Kitsirilarp, Nutthaporn Laoharojvongsa, Theeratep Tantayakom   +3 more
doaj   +1 more source

Necrobiotic xanthogranuloma

Journal of Cutaneous and Aesthetic Surgery, 2012
Necrobiotic xanthogranuloma is a rare, chronic, progressive granulomatous disorder which manifests as yellowish plaques and nodules, most commonly in the periorbital region. The exact aetiology is not known. It is commonly associated with monoclonal gammopathy. Various treatment modalities used include chemotherapy, intralesional and systemic steroids,
Girisha, Banavasi S, Holla, Anantha Prasad, Fernandes, Michelle, Noronha, Tonita M   +3 more
openaire   +6 more sources

Disseminated juvenile xanthogranulomas with ocular involvement: A case report and literature review

SAGE Open Medical Case Reports, 2022
Cutaneous juvenile xanthogranuloma is an uncommon disorder usually arising during infancy. Systemic involvement of juvenile xanthogranuloma remains rare, and there are no published guidelines to date on screening extracutaneous manifestations in these ...
Nadine Sophie Maalouf, Akli Aouane, Patrick Hamel, Sara-Élizabeth Jean, Myrna Chababi-Atallah, Carolina Lucena Fernandes   +5 more
doaj   +1 more source

Solitary juvenile xanthogranuloma of temporal bone: a case report

BMC Pediatrics, 2022
Background Juvenile xanthogranuloma (JXG) is a kind of non-Langerhans cell histiocytosis, usually with skin lesions as the main manifestation. It rarely occurs in other tissues or organs and even more rarely is it found in the skull.
Shu-ni Wang, Ji Lu
semanticscholar   +1 more source

C.E. Credit. Xanthogranuloma of the Palate in an Adult: A Case Report with Differential Diagnosis

Journal of the California Dental Association, 2023
Background Solitary oral mucosal xanthogranuloma, previously termed juvenile xanthogranuloma, is exceedingly rare in adults. Extracutaneous lesions are similarly rarely seen; and the condition generally affects infants and children.Methods This case ...
Hardev M. Singh, Jeffrey A. Elo, Yoon-Jeong Kim, Ho-Hyun (Brian) Sun   +3 more
doaj   +1 more source