Results 21 to 30 of about 7,890 (255)
JAAD Case Reports, 2022 IVIg: intravenous immunoglobulin JAK: janus kinase NXG: necrobiotic xanthogranuloma INTRODUCTION Necrobiotic xanthogranuloma (NXG) is a nonLangerhans cell histiocytosis occurring in association with paraproteinemia.
N. Shahriari, D. Mazori, J. Merola
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An analysis of clinical and pathological features of 32 cases of juvenile xanthogranuloma
Pifu-xingbing zhenliaoxue zazhi, 2020 Objective: To summarize the clinical and histopathological features of juvenile xanthogranuloma (JXG). Methods: The clinical manifestations and histopathological findings of 32 children with juvenile xanthogranuloma diagnosed and treated in our hospital ...
Cui HU +6 more
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Long-standing necrobiotic xanthogranuloma limited to the skin: A case report
SAGE Open Medical Case Reports, 2021 Necrobiotic xanthogranuloma is a rare non-Langerhans cell histiocytosis with a known association with monoclonal gammopathies and malignant conditions. There is a lack of consensus regarding the management of necrobiotic xanthogranuloma.
Anne-Sophie Smilga +3 more
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Neuroimaging in Pediatric Patients with Juvenile Xanthogranuloma of the CNS
American Journal of Neuroradiology, 2022 BACKGROUND AND PURPOSE: Juvenile xanthogranuloma is a rare clonal, myeloid, neoplastic disorder. Typically, juvenile xanthogranuloma is a self-limited disorder of infancy, often presenting as a solitary red-brown or yellow skin papule/nodule.
B. Serrallach +11 more
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Archive of Clinical Cases, 2022 Juvenile Xanthogranuloma (XG) is a rare disorder that belongs to the heterogeneous group of histiocytic neoplasms, characterized by a clonal expansion of non-Langerhans cell histiocytes that share a dermal macrophage phenotype. Although the head and neck
Gianluca Velletrani +5 more
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Journal of cutaneous pathology, 2021 Line‐field confocal optical coherence tomography (LC‐OCT) is a new noninvasive technique for a real‐time, vertical, and horizontal imaging of the skin at cellular resolution.
F. Lacarrubba +5 more
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JAMA dermatology, 2020 Importance Necrobiotic xanthogranuloma (NXG) is a non-Langerhans cell histiocytosis classically associated with paraproteinemia attributable to plasma-cell dyscrasias or lymphoproliferative disorders.
C. Nelson +11 more
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BMC Oral Health, 2022 Background Juvenile Xanthogranuloma (JXG) is a non-hereditary, self-limiting disease which is usually presented in infancy or early childhood and in males over females.
Long Chen, Lin Feng, Lingling E
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Dermoscopic Patterns in Juvenile Xanthogranuloma Based on the Histological Classification
Frontiers in Medicine, 2021 Background: Several dermoscopic features of juvenile xanthogranuloma (JXG) have been previously described in single cases or small case series and need to be further verified in a large sample.
Jiaosheng Xu, Lin Ma
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Clinical outcome of a patient with lysosomal acid lipase deficiency and first results after initiation of treatment with Sebelipase alfa: A case report [PDF]
, 2019 We report on a case of very rare autosomal recessive cholesteryl ester storage disease due to lysosomal acid lipase deficiency (LALD). LALD is caused by mutations in the lysosomal acid lipase A (LIPA) gene resulting in cholesteryl ester accumulation in
Bobbert, Thomas +8 more
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