[目的]观察一个肢带型肌营养不良伴心肌损害家系患者的临床病理特点。[方法]行家系调查,家系成员行心肌酶及肌钙蛋白T、心电图、肌电图、彩超检查;4位患者取肌肉标本进行组织化学的病理观察。[结果]系谱显示4代共有9位患者,每代都出现,男女均受累及。健在5位患者,均出现进行性肌肉无力、萎缩,以肩带及盆带部明显;心肌酶及肌钙蛋白T检查正常;部分患者出现心脏扩大、心律失常、心力衰竭。病理检查见明显肌萎缩、核内移、肌裂等现象,符合肌营养不良的典型表现,Dystrophin免疫组化结果为(+)。[结论 ...
袁沃亮 +6 more
doaj
急性冠状动脉综合征(acute coronary syndrome,ACS)是严重危害人类健康的常见病,其导致的死亡率近年来不断上升。ACS是一个从斑块破裂开始到冠状动脉完全或不完全阻塞的动态过程[1]。但如果早期确诊,并及时行再灌注治疗可以降低其死亡率。目前作为心肌缺血标志物在临床上广泛使用的实验室指标主要有心肌肌钙蛋白(cardiac troponin,cTn)及心肌肌酸激酶同工酶 ...
蔡丹 +5 more
doaj
[Isovitexin alleviates myocardial oxidative stress injury in diabetic mice by enhancing myocardial SIRT3 expression and reducing oxidative stress]. [PDF]
Peng Y +6 more
europepmc +1 more source
[Application of molecularly imprinted polymers-based sensors for determination of acute coronary syndrome biomarkers]. [PDF]
Zhang Y +6 more
europepmc +1 more source
[Overwork damages myocardial energy metabolism homeostasis in mice]. [PDF]
Cui J +6 more
europepmc +1 more source
目的】 研究AMP激活的蛋白激酶 (AMPK)及血红素氧合酶HO-1激活对心肌肥大的影响,以及HO-1在AMPK抑制心肌肥大中的作用?【方法】 以培养的新生大鼠心肌细胞为研究对象,采用蛋白免疫印迹杂交方法检测5-氨基-4甲酰胺咪唑核糖核苷酸(AICAR)对AMPK的磷酸化程度及对HO-1的影响,并测定心肌细胞 [3H]-亮氨酸掺入率及心肌细胞表面积,观察AMPK及HO-1心肌细胞肥大的影响?【结果】 AICAR对AMPK及HO-1均有激活作用,AICAR能阻断AngⅡ引起的心肌肥大效应;阻断HO ...
doaj
[Shihu Mixture alleviates diabetic cardiomyopathy in rats by Sirt3-mediated upregulation of myocardial mitochondrial mitophagy pathway]. [PDF]
Lin X, He Y, Shi H, Liu J, Hu H.
europepmc +1 more source
[Liver-bone axis: novel mechanisms and strategies for MAFLD regulation]. [PDF]
Wang YW, Yan XZ, You H, Yang AT.
europepmc +1 more source
Combination of sodium dimercaptosulfonate and high-dose hormone in treatment of interstitial pneumonia caused by acute mercury poisoning: clinical data of 2 cases [PDF]
XIAO Chunxia
core +1 more source
[Expression of the melanoma 2-mediated pyroptosis pathway in peripheral blood mononuclear cells of patients with idiopathic inflammatory myopathies]. [PDF]
Chu J +6 more
europepmc +1 more source

