Results 81 to 90 of about 6,257,191 (161)
Clinical Case Reports, Volume 14, Issue 10, October 2026.ABSTRACT A 7.6‐year‐old boy with hTTP had fever‐induced hemorrhagic rash, MAHA, cerebral infarction, and renal impairment. After plasma therapy, symptoms were partially relieved; 9‐year follow‐up showed regular plasma transfusion was needed, with CKD Stage 3.
Dai Xiaomei +5 more
wiley +1 more source
Pediatric Essential Thrombocythemia With a Novel CALR Mutation: A Case Report
eJHaem, Volume 7, Issue 5, October 2026.ABSTRACT Pediatric essential thrombocythemia (ET) is extremely rare and frequently lacks identifiable driver mutations. We report a case of a 5‐year‐old male with ET harboring a novel CALR exon 9 frameshift mutation complicated by acquired von Willebrand syndrome.
Kana Tsuji +10 more
wiley +1 more source
Clinical practice guidelines for the management of atypical haemolytic uraemic syndrome in the United Kingdom [PDF]
, 2010 Atypical haemolytic uraemic syndrome (aHUS) is associated with a poor prognosis with regard to survival at presentation, recovery of renal function and transplantation.
Sam Machin +8 more
core +1 more source
Acquired Von Willebrand’s Syndrome in Systemic Lupus Erythematosus
Case Reports in Hematology, 2014 Acquired von Willebrand syndrome (AVWS) is an uncommon, underdiagnosed, and heterogeneous disease which is increasingly recognized as a cause of bleeding diatheses. Systemic lupus erythematosus (SLE) is an infrequent cause of AVWS.
Sara Taveras Alam +6 more
doaj +1 more source
Proteoglycan Research, Volume 4, Issue 4, October 2026.ABSTRACT The extracellular matrix (ECM) is a dynamic and information‐rich network that integrates structural support with biochemical and mechanical signaling. Among its key regulatory components are the Small Leucine‐Rich Proteoglycans (SLRPs), a family of matrix molecules that coordinate extracellular architecture with cell signaling.
Alessandra Leone +2 more
wiley +1 more source
Research and Practice in Thrombosis and HaemostasisBackground: Combined von Willebrand disease (VWD) type 2A/2M is a rare phenotype characterized by overlapping qualitative defects affecting both multimer structure and von Willebrand factor (VWF) function. Key Clinical Question: How can congenital VWD be
Floor Derikx +5 more
doaj +1 more source
Acquired von Willebrand Syndrome and Chronic Anaemia: A Different Diagnostic Approach
European Journal of Case Reports in Internal Medicine, 2019 Heyde’s syndrome is a form of acquired von Willebrand syndrome that consists of bleeding from intestinal angiodysplasia in the presence of aortic stenosis (AS).
Nuno Zarcos Palma +5 more
doaj +1 more source
Small Bowel Lesions and Bleeding Risk in Hemodialysis Patients: A Narrative Review
Hemodialysis International, Volume 30, Issue 4, Page 665-678, October 2026.ABSTRACT Background Gastrointestinal bleeding is very common among hemodialysis patients. This high bleeding risk is caused by uremic platelet dysfunction, vascular fragility, intradialytic hemodynamic instability, and widespread antithrombotic therapy.
Andreas Smyrlis +3 more
wiley +1 more source
von Willebrand disease: an illustrated review
Research and Practice in Thrombosis and HaemostasisFirst described 100 years ago, von Willebrand disease (VWD) is the most common inherited bleeding disorder, characterized by a quantitative or qualitative deficiency of von Willebrand factor (VWF), a large multimeric glycoprotein central to hemostasis ...
Mouhamed Yazan Abou-Ismail +3 more
doaj +1 more source
An Automated Microfluidic System for Haemostasis Assessment in Cirrhosis With Thrombocytopenia
Liver International, Volume 46, Issue 10, October 2026.ABSTRACT Background & Aims Conventional laboratory tests do not capture platelet–vessel wall interactions (primary haemostasis) occurring in vivo, limiting guidance before invasive procedures. This is relevant in patients with thrombocytopenia, hallmark of advanced cirrhosis. Microfluidic assays may overcome these limitations.
Niccolò Bitto +14 more
wiley +1 more source