Results 1 to 10 of about 384,012 (260)
Biomedical Papers, 2017 Amyloidosis is a heterogeneous group of diseases characterized by the deposition of amyloid. It is caused by extracellular deposition of insoluble fibrils with beta-pleated sheet configuration.
Lucie Karafiatova, Tomas Pika
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Lysosomal dysfunction and impaired autophagy underlie the pathogenesis of amyloidogenic light chain‐mediated cardiotoxicity [PDF]
EMBO Molecular Medicine, 2014 AL amyloidosis is the consequence of clonal production of amyloidogenic immunoglobulin light chain (LC) proteins, often resulting in a rapidly progressive and fatal amyloid cardiomyopathy.
Jian Guan +12 more
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Hereditary transthyretin amyloid cardiomyopathy
Singapore Medical Journal, 2023 10.4103/singaporemedj.SMJ-2021-300 ; Singapore medical journal ; 64 ; 1 ; 74 ...
Yiliang Zheng +6 more
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Kidney Outcomes in Transthyretin Amyloid Cardiomyopathy.
JAMA CardiolImportanceTransthyretin amyloid cardiomyopathy (ATTR-CM) is a progressive cardiomyopathy that commonly presents with concomitant chronic kidney disease. Chronic kidney dysfunction is associated with worse outcomes, but the prognostic value of changes in kidney function over time has yet to be defined.ObjectiveTo assess the prognostic importance of a ...
Ioannou A +20 more
europepmc +4 more sources
Diagnosis of Transthyretin Amyloid Cardiomyopathy [PDF]
Cardiology and Therapy, 2020 Transthyretin amyloid cardiomyopathy (ATTR-CM) continues to be an easily overlooked, life-threatening, yet treatable cause of heart failure. Furthermore, its elusive diagnosis leads to late or misdiagnosis.
Adam S. Hafeez, Anthony A. Bavry
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Transthyretin amyloid cardiomyopathy: Treatment pipeline, clinical trials, and challenges
Journal of Public Health and Primary Care, 2021 Transthyretin amyloid cardiomyopathy (ATTR-CM) is potentially a fatal disease characterized by abnormal buildup of amyloid fibrils primarily in the heart causing progressive heart failure. It is categorized into two subtypes-hereditary ATTR and wild type
Sweety Sharma, Bhawna Sharma
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Speckle Tracking and Transthyretin Amyloid Cardiomyopathy
Arquivos Brasileiros de Cardiologia, 2016 Background: Amyloidosis is a disease caused by deposits of insoluble fibrils in extracellular spaces. The most common type of familial amyloidosis is mediated by mutation of transthyretin, especially Val30Met.
Alexandre Marins Rocha +5 more
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Transthyretin Amyloid Cardiomyopathy: The Role and Reach of SGLT2 Inhibitors. [PDF]
JACC AdvKarakasis P.
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AL-amyloidosis with cardiac involvement. Diagnostic capabilities of non-invasive methods
Терапевтический архив, 2021 There are presented the literature data and a description of the clinical course of the disease in isolated/predominant cardiac amyloidosis. Amyloid cardiomyopathy is the most common phenocopy of hypertrophic cardiomyopathy.
Alexandra Ya. Gudkova +13 more
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A new era in treatment of cardiac amyloidosis: an overview of the Congress of cardiology
Лечащий Врач, 2022 Amyloidosis is a group of diseases characterized by accumulation of a protein of a specific fibrillar structure in the interstitium of various organs and tissues.
I. E. Strelkova
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