Results 91 to 100 of about 21,508 (259)
NEMO‐NDAS: Case Report and Review of the Literature
ABSTRACT NEMO‐deleted exon 5 autoinflammatory syndrome (NEMO‐NDAS) is the result of a gain‐of‐function IKBKG pathogenic variant leading to dysregulated NF‐κB signaling and systemic inflammation. We present a case of NEMO‐NDAS in a 2‐year‐old female presenting with recurrent fevers, subcutaneous nodules, lymphadenopathy, and splenomegaly.
Angela Yang +5 more
wiley +1 more source
Abstract Background Standardized post‐graduate education in pediatric transfusion medicine remains limited. The objective of this study was to adapt an adult transfusion education program, Transfusion Camp, to include pediatric content and assess knowledge improvement in pediatric subspecialty trainees.
Ines Zuna +14 more
wiley +1 more source
Paediatric‐onset autoimmune cytopenia: How can we reduce the long‐term mortality?
British Journal of Haematology, EarlyView.
Nathalie Aladjidi +21 more
wiley +1 more source
Abstract Background The monocyte monolayer assay (MMA) uses monocytes, but it is known that antibody‐mediated hemolysis occurs in macrophages. Whether the use of macrophages would improve the predictive capacity of the MMA is unclear. Also, it is unclear if RBC alloantibodies contribute to hemolysis via antibody‐dependent cellular cytotoxicity (ADCC ...
Yeniley Ruiz Noa +6 more
wiley +1 more source
Concurrent Atypical Hemolytic Uremic Syndrome and Autoimmune Hemolytic Anemia: a case report
Background: Atypical hemolytic uremic syndrome (aHUS) is a life-threatening and scarce disorder characterized by acute renal failure and disease, non-immune microangiopathic hemolytic anemia and thrombocytopenia, leading to end-stage renal failure or ...
Sayed Yousef Mojtahedi +1 more
doaj
Background Urgent splenectomy is recommended for the management of highly transfusion-dependent life-threatening warm autoimmune hemolytic anemia, while for individuals unfit for surgery, splenic embolization is an alternative treatment option.
Aya Egbaria, Naiel Bisharat
doaj +1 more source
ABSTRACT A 3‐year‐old female‐intact German Shepherd presented for the evaluation of progressive shifting leg lameness, carpal swelling, and weight loss with a poor appetite since adoption about three months prior. Routine blood smear evaluation, lymph node, and synovial fluid cytologies all revealed rare neutrophils with cytoplasmic inclusions ...
Samantha L. Braman +3 more
wiley +1 more source
Reports from the literature have discussed patients presenting Hepatitis A virus infection with hemolytic anemia, specifically with glucose-6-phosphate dehydrogenase deficiency. However, autoimmune hemolytic anemia (AIHA) has been rarely reported.
Habiba Debbabi +6 more
doaj +1 more source

