Results 51 to 60 of about 3,364 (172)

Pathology reporting of hepatoblastoma resections: recommendations from the international collaboration on cancer reporting

Histopathology, Volume 87, Issue 6, Page 802-814, December 2025.
This is the first international dataset for the reporting of hepatoblastoma resection specimens produced by the International Collaboration on Cancer Reporting (ICCR). The aim is to standardize pathology reports, facilitating international data comparisons and improving management of hepatoblastoma on a global level.
Dolores H López‐Terrada, Fleur Webster, Rita Alaggio, Jonathan W Bush, Soo‐Jin Cho, Ronald R de Krijger, Takeshi Inoue, Allison F O'Neill, Antonio R Perez‐Atayde, Sarangarajan Ranganathan, Jens Stahlschmidt, Yukichi Tanaka, Marta Cohen, Miguel Reyes‐Múgica   +13 more
wiley   +1 more source

Intermediate familial intrahepatic cholestasis: phenotypic spectrum within the BRIC-PFIC spectum

, 2015
In genetic hepatocellular cholestasis, among the spectrum going from benign recurrent intrahepatic cholestasis (BRIC) and profressive familial intrahepatic cholestasis, intermediate phenotypes ...
Nobili, V, Boldrini, R, Francalanci, P., De Ville de Goyet, J, Torre, G, Callea, F, Belacchio, E, MAGGIORE, GIUSEPPE, Giovannoni, I   +8 more
core   +1 more source

Nasobiliary drainage induces long-lasting remission in benign recurrent intrahepatic cholestasis

, 2006
Benign recurrent intrahepatic cholestasis (BRIC) is characterized by episodic cholestasis and pruritus without anatomical obstruction. Effective medical treatment is not available.
Stapelbroek, JM, Schwartz, TP, Devlin, J, Venneman, NG, van Nieuwkerk, CMJ, Henegouwen, GPV, van Erpecum, KJ, Klomp, LWJ, Knisely, AS, Houwen, RHJ   +9 more
core   +1 more source

Nasobiliary Drainage for Benign Recurrent Intrahepatic Cholestasis in Patients Refractory to Standard Therapy

, 2016
Purpose: Benign recurrent intrahepatic cholestasis (BRIC) is characterized by episodic cholestasis and pruritus without anatomical obstruction. The aim of this study was to evaluate the safety and efficacy of nasobiliary drainage (NBD) in patients with ...
Ozer, Birol, Kanat, Ayse G. Unler, DEMİR, MEHMET, Ayse G Unler Kanat, Serin, Ender, Alper Parlakgumus, Ender Serin, Gokturk, Huseyin S., Yakar, Tolga, Mehmet Demir, Tolga Yakar, Parlakgumus, Alper, Huseyin S Gokturk, Birol Ozer   +13 more
core   +2 more sources

Benign recurrent intrahepatic cholestasis (BRIC):evidence of genetic heterogeneity and delimitation of the BRIC locus to a 7-cM interval between D18S69 and D18S64 [PDF]

, 1997
Benign recurrent intrahepatic cholestasis (BRIC) is an autosomal recessive liver disease characterized by multiple episodes of cholestasis without progression to chronic liver disease.
Bull, L, Pearson, PL, Keller, KM, Knol, IE, Freimer, NB, Juijn, JA, Carlton, VEH, Sinaasappel, M, vanAmstel, HKP, Sinke, RJ, Houwen, RHJ, Delhaas, T, Berger, R, Bijleveld, CMA, vanHattum, J, Henegouwen, GPV   +15 more
core   +2 more sources

The Roles and Clinical Significance of Major Hepatic‐Derived Metabolites in Hepatocellular Carcinoma

Journal of Gastroenterology and Hepatology, Volume 40, Issue 10, Page 2435-2448, October 2025.
ABSTRACT Hepatocellular carcinoma (HCC) is increasingly recognized as a metabolically orchestrated malignancy, in which hepatic‐derived metabolites function not only as byproducts of liver physiology but also as active modulators of tumor biology.
Rui Sun, Xiaoru Wang, Jiayi Ma, Yuying Cai, Lei Li, Shanshan Wang   +5 more
wiley   +1 more source

Long-Term Therapy of a Patient with Summerskill-Walshe-Tygstrup Syndrome by Applying Prometheus® Liver Dialysis: A Case Report

Case Reports in Gastroenterology, 2012
Summerskill-Walshe-Tygstrup syndrome is a rare benign chronic liver disease characterized by recurring cholestasis with jaundice and severe pruritus. Due to insufficient conservative treatment, liver dialysis by Prometheus® was applied to a 45-year-old ...
Mikolaj Walensi, Ali Canbay, Oliver Witzke, Guido Gerken, Alisan Kahraman   +4 more
doaj   +1 more source

Recurrent Nonobstructive Cholangitis After Pancreaticoduodenectomy: Prevalence, Risk Factors, and Treatment

World Journal of Surgery, Volume 49, Issue 9, Page 2570-2577, September 2025.
Recurrent nonobstructive cholangitis (RNOC) due to enterobiliary reflux is a late complication of pancreaticoduodenectomy (PD) that should be differentiated from obstructive cholangitis. The risk factors (RFs) of RNOC are poorly known. The goal of this study was to estimate the prevalence, to identify the RF, and to describe the management of RNOC ...
Anaïs Choquet, Aurélien Sokal, Safi Dokmak, Audrey Le Bot, Fanny Delahaye, Jeanne Dembinski, Béatrice Aussilhou, Vinciane Rebours, Victoire de Lastours, Alain Sauvanet   +9 more
wiley   +1 more source

Phospholipase D2 mediates signaling by ATPase class I type 8B membrane 1[S]

Journal of Lipid Research, 2013
Functional defects in ATPase class I type 8B membrane 1 (ATP8B1 or familial intrahepatic cholestasis 1, FIC1) lead to cholestasis by mechanism(s) that are not fully understood.
Frank Chen, Ayantika Ghosh, Benjamin L. Shneider   +2 more
doaj   +1 more source

Phenotypic Divergence of JAG1‐ and NOTCH2‐Associated Alagille Syndrome & Disease‐Specific NOTCH2 Variant Classification Guidelines

Liver International, Volume 45, Issue 9, September 2025.
ABSTRACT Background & Aims Alagille syndrome (ALGS) is a rare, autosomal dominant disorder with high phenotypic heterogeneity. Disease‐causing variants are primarily identified in Jagged1 (JAG1), with fewer reported in NOTCH2. JAG1 variants cause disease through a mechanism of haploinsufficiency, but the mechanism for NOTCH2 variants is not completely ...
Shannon M. Vandriel, Li‐Ting Li, Huiyu She, Jian‐She Wang, Kathleen M. Loomes, David A. Piccoli, Irena Jankowska, Piotr Czubkowski, Dorota Gliwicz‐Miedzińska, Lorenzo D'Antiga, Emanuele Nicastro, Florence Lacaille, Dominique Debray, Étienne M. Sokal, Tanguy Demaret, Rima L. Fawaz, Silvia Nastasio, Kyung Mo Kim, Seak Hee Oh, Björn Fischler, Henrik Arnell, Catherine Larson‐Nath, Winita Hardikar, Sahana Shankar, Shikha S. Sundaram, Alexander Chaidez, Pinar Bulut, Pier Luigi Calvo, Mureo Kasahara, Niviann Blondet, Eberhard Lurz, Anna‐Maria Kavallar, Emmanuel M. Gonzales, Emmanuel Jacquemin, Jérôme Bouligand, Noelle H. Ebel, Jeffrey A. Feinstein, Susan M. Siew, Michael O. Stormon, Saul J. Karpen, Rene Romero, M. Kyle Jensen, Catalina Jaramillo, James E. Squires, Sarah M. Bedoyan, Deirdre A. Kelly, Jane Hartley, Henkjan J. Verkade, Way Seah Lee, Chatmanee Lertudomphonwanit, Ryan T. Fischer, Henry C. Lin, Nathalie Rock, Yael Mozer‐Glassberg, Amin J. Roberts, Helen M. Evans, Wikrom Karnsakul, Gabriella Nebbia, Victorien M. Wolters, Pamela L. Valentino, Jesus Quintero Bernabeu, Amal A. Aqul, Cigdem Arikan, María Legarda Tamara, Cristina Molera Busoms, Thomas Damgaard Sandahl, Giuseppe Indolfi, Andréanne N. Zizzo, Aglaia Zellos, Ruben E. Quiros‐Tejeira, Ermelinda Santos‐Silva, Kathleen B. Schwarz, Jernej Brecelj, Maria Camila Sanchez, Maria Lorena Cavalieri, Christos Tzivinikos, Sabina Wiecek, John Eshun, Nanda Kerkar, Quais Mujawar, Zerrin Önal, Cristina Gonçalves, Jennifer Garcia, Seema Alam, Carolina Jimenez‐Rivera, Luis Bujanda, Richard J. Thompson, Bettina E. Hansen, Nancy B. Spinner, Melissa A. Gilbert, Binita M. Kamath, The Global ALagille Alliance (GALA) Study Group   +91 more
wiley   +1 more source