Results 41 to 50 of about 15,869 (231)

Obliterative cholangiopathy in acquired cystic biliary atresia type III after cyst perforation: a case report

BMC Pediatrics, 2018
Background In biliary atresia, the disease process of obliterative cholangiopathy may begin in the perinatal period; however, no chronological evidence exists on how the cholangiopathy progresses to biliary obliteration.
Tsugumichi Koshinaga, Kensuke Ohashi, Kakou Ono, Hide Kaneda, Takeshi Furuya   +4 more
doaj   +1 more source

Association of biliary atresia with jejuno-ileal atresia: Case report

Journal of Pediatric Surgery Case Reports, 2023
Background: Jejuno‐ileal atresia (JIA) is a congenital anomaly characterized clinically by bilious vomiting and abdominal distension. The incidence of JIA is approximately between 1 in 5000 live births in different parts of the world.
Amru Abulkhair, Adel Albiety, Petros Valioulis, Khalid Eibani, Eshraq Omar, Amjad Tala't, Reem Mosalli, Omar Mansour   +7 more
doaj   +1 more source

EP300/YAP1-SERPINE1 Signaling Regulates Ductular Reaction and Liver Fibrosis in Biliary Atresia. [PDF]

Cell Mol Gastroenterol Hepatol
Zhu Z, Lu C, Lv X, Lu Y, Zhu W, Zhu Y, Zhang R, Ding Z, Xie H, Tang W.   +9 more
europepmc   +2 more sources

Variants in AKR1D1 and Infant Mortality: Should Bile Acid Screening be a Routine Part of Newborn Screening?

American Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Biallelic pathogenic variants in AKR1D1 cause Δ4‐3‐oxosteroid 5β‐reductase deficiency, disrupt bile acid synthesis, and result in Congenital Bile Acid Synthesis defect type 2 (CBAS2). CBAS2 presents in infancy with cholestasis, coagulopathy, and failure to thrive.
Jade Hudson, Stephanie Hyunh, Bojana Rakic, Cornelius Boerkoel   +3 more
wiley   +1 more source

Embryonic Biliary Atresia in a Very-low-birth-weight Premature Infant

Journal of the Formosan Medical Association, 2007
Two major forms of biliary atresia, the embryonic and perinatal type, are considered to have different pathogeneses and distinct prognoses. Embryonic biliary atresia is associated with worse prognosis.
Hung-Wen Chen, Wen-Ming Hsu, Mei-Hwei Chang, Chien-Yi Chen, Hung-Chieh Chou, Po-Nien Tsao, Wu-Shiun Hsieh   +6 more
doaj   +1 more source

Paediatric development of radiopharmaceutical imaging agents and radioligand therapeutics

British Journal of Clinical Pharmacology, EarlyView.
Abstract This review focuses on the development of radiopharmaceutical imaging agents and radioligand therapeutics for paediatric use. Nuclear medicine plays an important role in the diagnosis and treatment of various childhood conditions, including cancers, infections and brain disorders.
Justin L. Hay, Amandine Manon, Hunter Stephens, S. Y. Amy Cheung, Bart de Keizer, Erik T. te Beek   +5 more
wiley   +1 more source

Biliary Atresia

Seminars in Pediatric Surgery, 2000
Although the prognosis of biliary atresia has been dramatically improved in the era of liver transplantation, the Kasai operation is still the first line of surgical treatment. Successful hepatic portoenterostomy depends on early diagnosis and surgery, adequate surgical technique, prevention of cholangitis, and precise postoperative management.
M, Nio, R, Ohi
openaire   +2 more sources

Biliary Atresia - Clinical Series [PDF]

GE - Portuguese Journal of Gastroenterology, 2017
<b><i>Introduction:</i></b> Biliary atresia is the main cause of death by hepatic failure and the main indication for liver transplant in children. This study aims to analyze the population with this diagnosis, treated between 2000 and 2015 at Hospital de São João.
Neto, Bárbara, Borges-Dias, Mariana, Trindade, Eunice, Estevão-Costa, José, Campos, José Miguel   +4 more
openaire   +4 more sources

Maternal regulation of biliary disease in neonates via gut microbial metabolites

Nature Communications, 2022
The pathogenesis of biliary atresia remains poorly understood. Here, the authors report that maternal butyrate treatment alters the gut microbiome and glutamine/hypoxanthine metabolites similar to human subjects, and suppresses biliary atresia in newborn
Jai Junbae Jee, Li Yang, Pranavkumar Shivakumar, Pei-pei Xu, Reena Mourya, Unmesha Thanekar, Pu Yu, Yu Zhu, Yongkang Pan, Haibin Wang, Xufei Duan, Yongqin Ye, Bin Wang, Zhu Jin, Yuanmei Liu, Zhiqing Cao, Miki Watanabe-Chailland, Lindsey E. Romick-Rosendale, Michael Wagner, Lin Fei, Zhenhua Luo, Nicholas J. Ollberding, Shao-tao Tang, Jorge A. Bezerra   +23 more
doaj   +1 more source

First finding of Ciprofloxacin Resistant Campylobacter jejuni Bacteremia from an infant with biliary atresia in Surabaya, Indonesia

Journal of Zoonotic Diseases, 2023
Here we present a case of an infant with biliary atresia with bacteremia caused by Ciprofloxacin resistant C. jejuni. An eight-month-old boy - previously diagnosed with inoperable biliary atresia, was referred with fever.
Daniel Edbert, Amina Thayyiba, Dicky Bagus Widhyatmoko, Eddy Bagus Wasito   +3 more
doaj   +1 more source