Results 41 to 50 of about 19,725 (236)

Colonic Atresia Associated with Biliary Atresia

Journal of Indian Association of Pediatric Surgeons, 2023
Colonic atresia (CA) is an uncommon type of intestinal atresia commonly associated with other anomalies, while biliary atresia (BA) is also rare but usually an isolated anomaly. The pathogenesis for either of the anomalies is unclear. The co-occurrence of both pathologies has not been mentioned in the literature.
Shailesh Solanki, Jai Kumar Mahajan, Palak Singhai, Suvradeep Mitra   +3 more
openaire   +3 more sources

Cyclosporine Absorption Following Orthotopic Liver Transplantation [PDF]

, 1986
Blood concentrations of cyclosporine were determined in adult and pediatric patients following orthotopic liver transplantation to quantitate cyclosporine blood clearance and oral absorption.
Beveridge, Burckart, Burckart, Calne, Calne, Holt, Kahan, Kennedy, Malatack, Miles, Ptachcinski, Ptachcinski, Ptachcinski, Sawchuk, Starzl, Starzl, Starzl, Venkataramanan, Venkataramanan, Venkataramanan, Wood   +20 more
core   +2 more sources

Differential diagnosis of neonatal cholestasis by genetic testing: A case report

Journal of Pediatric Surgery Case Reports, 2023
Introduction: Alagille syndrome (ALGS) is a cholestasis disorder with multiple organ dysfunction, including heart and kidney. The causative genes of ALGS are JAG1 and NOTCH2.
Sakura Kawahara, Kazuo Imagawa, Shusuke Takeuchi, Tomoya Iwasaki, Yuki Okada, Yuri Nakamura, Shogo Saito, Takato Sasaki, Kouji Masumoto, Hidetoshi Takada   +9 more
doaj   +1 more source

The incidence of portal vein thrombosis at liver transplantation [PDF]

, 1992
The incidence of portal vein thrombosis was examined in 885 patients who received orthotopic liver transplantations for various end‐stage liver diseases between 1989 and 1990. The thrombosis was classified into four grades.
Iwatsuki, S, Nonami, T, Starzl, TE, Yokoyama, I   +3 more
core   +1 more source

Development and Validation of a Machine Learning–Based Prediction Model for Detection of Biliary Atresia

Gastro Hep Advances, 2023
Background and Aims: Biliary atresia is a rare and devastating bile duct disease that occurs during the neonatal period. Timely identification and prompt surgical intervention is critical for improving the outcome.
Ho Jung Choi, Yeong Eun Kim, Jung-Man Namgoong, Inki Kim, Jun Sung Park, Woo Im Baek, Byong Sop Lee, Hee Mang Yoon, Young Ah Cho, Jin Seong Lee, Jung Ok Shim, Seak Hee Oh, Jin Soo Moon, Jae Sung Ko, Dae Yeon Kim, Kyung Mo Kim   +15 more
doaj   +1 more source

Overview of Biliary Atresia

대한영상의학회지, 2022
Biliary atresia is a progressive, idiopathic, obliterative disease of the extrahepatic biliary tree that presents with biliary obstruction in the neonatal period. It is the most common indication for liver transplantation in children.
Tae Yeon Jeon
doaj   +1 more source

Obliterative cholangiopathy in acquired cystic biliary atresia type III after cyst perforation: a case report

BMC Pediatrics, 2018
Background In biliary atresia, the disease process of obliterative cholangiopathy may begin in the perinatal period; however, no chronological evidence exists on how the cholangiopathy progresses to biliary obliteration.
Tsugumichi Koshinaga, Kensuke Ohashi, Kakou Ono, Hide Kaneda, Takeshi Furuya   +4 more
doaj   +1 more source

Association of biliary atresia with jejuno-ileal atresia: Case report

Journal of Pediatric Surgery Case Reports, 2023
Background: Jejuno‐ileal atresia (JIA) is a congenital anomaly characterized clinically by bilious vomiting and abdominal distension. The incidence of JIA is approximately between 1 in 5000 live births in different parts of the world.
Amru Abulkhair, Adel Albiety, Petros Valioulis, Khalid Eibani, Eshraq Omar, Amjad Tala't, Reem Mosalli, Omar Mansour   +7 more
doaj   +1 more source

Liver transplantation before 1 year of age [PDF]

, 1987
Since 1981, 20 infants younger than 1 year of age received 26 orthotopic liver transplants. Immunosuppression was with cyclosporine and corticosteroids. Thirteen (65%) of the reciplents were discharged from the hospital.
Ascher, Baburao Koneru, Carlos O. Esquivel, Frederick Karrer, Gartner, Gordon, Iwatsuki, Kasai, Leonard Makowka, Robert D. Gordon, Rosenthal, Satoru Todo, Shunzaburo Iwatsuki, Starzl, Starzl, Starzl, Starzl, Thomas E. Starzl, Wallis J. Marsh   +18 more
core   +1 more source

From Multiple Congenital Anomalies to Pituitary Gland Malformation: Wide Spectrum of Clinical Features in a Family With FOXA2 Variant

American Journal of Medical Genetics Part A, EarlyView.
ABSTRACT FOXA2 (hepatocyte nuclear factor‐3β, HNF‐3β) encodes a transcriptional activator involved in early embryogenesis, particularly in the patterning and differentiation of midline structures such as the neural tube, foregut, and pituitary gland. Its role in human pathogenesis was first suspected when patients with deletion of chromosome 20p11.2 ...
Christopher Connolly, Hemant A. Parmar, Lauren Hipp, Tomoyasu Higashimoto   +3 more
wiley   +1 more source