Results 71 to 80 of about 1,857,276 (291)

Age‐Related Characteristics of SYT1‐Associated Neurodevelopmental Disorder

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objectives We describe the clinical manifestations and developmental abilities of individuals with SYT1‐associated neurodevelopmental disorder (Baker‐Gordon syndrome) from infancy to adulthood. We further describe the neuroradiological and electrophysiological characteristics of the condition at different ages, and explore the associations ...
Sam G. Norwitz, Josefine Eck, Joel S. Winston, Kate Baker   +3 more
wiley   +1 more source

Formation of field-induced breakdown precursors on metallic electrode surfaces

Frontiers in Physics
Understanding the underlying factors responsible for higher-than-anticipated local field enhancements required to trigger vacuum breakdown on pristine metal surfaces is crucial for the development of devices capable of withstanding intense operational ...
Soumendu Bagchi, Evgenya Simakov, Danny Perez   +2 more
doaj   +1 more source

Avalanches in Breakdown and Fracture Processes

, 1999
We investigate the breakdown of disordered networks under the action of an increasing external---mechanical or electrical---force. We perform a mean-field analysis and estimate scaling exponents for the approach to the instability.
A. A. Griffith, A. Buchel, A. Buchel, A. Garcimartín, A. Guarino, A. H. Thompson, A. Hansen, A. Hansen, A. Petri, Alessandro Vespignani, B. Gutenberg, B. K. Chakrabarti, B. Kahng, B. Suki, C. Maes, C. Unger, C. Unger, D. Heerman, D. Sornette, F. Tzschichholz, G. Caldarelli, G. Cannelli, G. Vasconcelos, H. A. Daniels, H. Eugene Stanley, J. B. Rundle, J. B. Rundle, J. B. Rundle, J. D. Gunton, J. P. Sethna, J. Weiss, K. Dahmen, K.-T. Leung, K.-T. Leung, L. de Arcangelis, L. de Arcangelis, L. Golubovic, L. Golubovic, L. Monette, L. Monette, M. Acharaya, M. Acharaya, M. Kloster, P. C. Hemmer, P. Diodati, P. Duxbury, P. Ray, Purusattam Ray, R. Englman, R. L. B. Selinger, R. L. B. Selinger, S. Ciliberto, S. Field, S. Kirkpatrik, S. L. Phoenix, S. Roux, S. Zapperi, S. Zapperi, S. Zapperi, Stefano Zapperi, T. Ray, V. I. Räisänen, W. H. Press, Z.-G. Wang   +63 more
core   +1 more source

Super‐Refractory Status Epilepticus (SRSE) in a Patient With Compound Heterozygous OPA1 Variants: Case Report and Literature Review

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Super‐Refractory Status Epilepticus (SRSE) is a rare, life‐threatening neurological emergency with unclear etiology in many cases. Mitochondrial dysfunction, often due to disease‐causing genetic variants, is increasingly recognized as a cause, with each gene producing distinct pathophysiological mechanisms.
Pouria Mohammadi, Lara Basovic, Christopher Michael McGraw   +2 more
wiley   +1 more source

Experimental Study on the Discharge Characteristics of a Dripping ‘Rod–Plane’ Air Gap at High Altitude Under DC Voltages

Energies
High-voltage transmission and substation projects at high altitudes are pivotal in realizing the objective of universal electricity access. However, the reduced air density at elevated heights facilitates the formation and propagation of discharges ...
Chuyan Zhang, Xi Wang, Xinzhe Yu, Kaixuan Qu, Yuxi Dong, Yu Deng   +5 more
doaj   +1 more source

Effect of Crystalline Morphology on Electrical Tree Growth Characteristics of High-Density and Low-Density Polyethylene Blend Insulation

IEEE Access, 2020
The electrical tree initiation and propagation behaviors are a key issue for the polyethylene-based cable insulation. This paper focuses on the effect of crystalline morphology on electrical tree growth characteristics of high-density and low-density ...
Zhonglei Li, Shuofan Zhou, Boxue Du, Mingsheng Fan, Jingang Su   +4 more
doaj   +1 more source

Brainstem and Cerebellar Volume Loss and Associated Clinical Features in Progressive Supranuclear Palsy

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Introduction Progressive Supranuclear Palsy (PSP) is a neurodegenerative ‘tauopathy’ with predominating pathology in the basal ganglia and midbrain. Caudal tau spread frequently implicates the cerebellum; however, the pattern of atrophy remains equivocal.
Chloe Spiegel, Timothy P. Siejka, Cassandra Marotta, Josh J. Y. Lee, Kelly Bertram, Terence J. O'Brien, Meng Law, Lucy Vivash, Ian H. Harding   +8 more
wiley   +1 more source

Deep Neural Network Using Transfer Learning Technique for MOSFETs With Different Gate Lengths in Avalanche Region

IEEE Access
In this paper, a transfer learning technique was first utilized to obtain deep neural network models for different gate lengths in the avalanche breakdown regime. Once the characteristics of a gate-length metal-oxide-semiconductor field-effect transistor
Chie-In Lee, Shi-Yan Zhang, Shih-Chieh Li, Jia-Han Yang, Jian Cheng Su   +4 more
doaj   +1 more source

Mass spectra of neutral particles released during electrical breakdown of thin polymer films [PDF]

, 1985
A special type of time-of-flight mass spectrometer triggered from the breakdown event was developed to study the composition of the neutral particle flux released during the electrical breakdown of polymer films problem. Charge is fed onto a metal-backed
Kendall, B. R. F.
core   +1 more source

Evidence of Iron Accumulation in Cerebral Adrenoleukodystrophy: A Potential Novel Disease Mechanism

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT In this first application of Quantitative Susceptibility Mapping Source Separation to cerebral adrenoleukodystrophy, we uncovered alterations in iron and myelin within lesions and normal appearing white matter. As validation, we demonstrate abnormal iron accumulation in those same compartments within primary brain tissue.
Christina L. Nemeth, Mert Sisman, Jinwei Zhang, Hyeong‐geol Shin, Xu Li, Bela Turk, Ali Fatemi, Thanh Nguyen, Eric Mallack   +8 more
wiley   +1 more source