Results 81 to 90 of about 4,302 (188)

NMES‐Facilitated Mandibular Rehabilitation for Spasticity‐Related Trismus in ALS

Muscle &Nerve, EarlyView.
Kelly Salmon, Hristelina Ilieva, Daniel Kelly   +2 more
wiley   +1 more source

The Flail Limb Syndrome

Muscle &Nerve, Volume 74, Issue 2, Page 281-292, August 2026.
ABSTRACT The flail limb syndrome is primarily a lower motor neuron disorder that initially affects proximal arm muscles (flail arm syndrome—FAS) or distal leg muscles (flail leg syndrome—FLS). Both were recognized early on (1886 for FAS and 1918 for FLS) as somewhat distinct from classic amyotrophic lateral sclerosis (ALS).
Mark B. Bromberg
wiley   +1 more source

Epidemiological survey of X-linked bulbar and spinal muscular atrophy, or Kennedy disease, in the province of Reggio Emilia, Italy [PDF]

, 2001
Commencing with the work carried out during the epidemiological survey of amyotrophic lateral sclerosis in the period 1980–1992 and the pathology follow-up, we carried out a perspective incidence, prevalence and mortality survey of X-linked bulbar and ...
FERLINI, Alessandra, TORRENTE I., SABADINI R, GUIDETTI D   +3 more
core   +1 more source

Effects of Meal Consumption on Isotonic Lingual Endurance in Healthy Adults: A Multi‐Institutional Study

Journal of Oral Rehabilitation, Volume 53, Issue 8, Page 1436-1446, August 2026.
Isotonic tongue endurance was measured pre‐ and post‐meal using the Iowa Oral Performance Instrument (IOPI) in healthy younger (18–35 years) and older (≥ 65 years) adults. Older adults demonstrated greater isotonic endurance and longer mealtimes, with no sex differences in endurance.
Yvette M. McCoy, Kristine E. Galek, Ed M. Bice, Rachel Roberts, Anna Hopkins, Blake Schuck, Claudia Vollman Breen, Devin Wright, Brittany N. Krekeler   +8 more
wiley   +1 more source

Late-onset and acute presentation of Brown-Vialetto-Van Laere syndrome in a Brazilian family [PDF]

, 2018
Riboflavin transporter deficiency (formerly known as Brown-Vialetto-Van Laere [BVVL] or Fazio-Londe syndrome) is a neurodegenerative disorder characterized by progressive bulbar palsy with sensorineural deafness or bulbar hereditary neuropathy.1 It is ...
Luis Sergio Mageste, Mageste, LS, Sarah Teixeira Camargos, Jose Bras, Guerreiro, R, Rita Guerreiro, Camargos, S, Bras, J, Sarah Camargos   +8 more
core   +1 more source

Pharyngeal-cervical-brachial variant of Guillain-Barré syndrome: a rare cause of acute bulbar dysfunction in children [PDF]

, 2014
AIMS: To report a case of pharyngeal-cervical-brachial variant of Guillain-Barré syndrome, which is characterized by rapidly progressive bulbar palsy with upper limb, neck and oropharyngeal involvement.
Furtado, Fatima, Quintas, Sofía, Abecasis, Francisco, Coelho, Joana, Azevedo, Sara, Levy, Antonin   +5 more
core   +3 more sources

GUILLAIN-BARRÉ SYNDROME ASSOCIATED WITH ACUTE HEV HEPATITIS

IMC Journal of Medical Science, 2008
Guillain-Barré Syndrome (GBS) otherwise known as Acute Inflammatory Polyneuritis, characterized by acute progressive limb weakness and aretlexia, is the prototype of a post infectious autoimmune disease.
Rawshan Ara Khanam, Mohammad Omar Faruq, Rawshan Ali Basunia, ASM Areef Ahsan   +3 more
doaj  

A case report of riboflavin transporter deficiency: A novel heterozygous pathogenic variant in the SLC52A3 gene

Molecular Genetics and Metabolism Reports
Riboflavin transporter deficiency (RTD) is a neurodegenerative disorder that presents from infancy to adulthood with a progressive axonal neuropathy characterized by a variety of neurologic symptoms including hearing loss, weakness, bulbar palsy, and ...
Elizabeth S. Tranel, Bridget McGowan, Andy Drackley, Leon G. Epstein, Vamshi K. Rao, Nancy L. Kuntz, Abigail N. Schwaede   +6 more
doaj   +1 more source

Audiological findings in Brown Vialetto-Van-Laere Syndrome: A scoping review

Brazilian Journal of Otorhinolaryngology
Objective: This study aimed to characterize audiological porfile in inviduals with Brown-Vialetto-Van Laere syndrome (BVVLS). Methods: This is a scoping review following the methodological structure developed by the Joana Briggs Institute (JBI).
Débora de Oliveira Rolim, Leticia Cristina Vicente, Hugo Amilton Santos de Carvalho, Rebeca Lorrane Santana Santos, Rivadávio Fernandes Batista de Amorim, Fayez Bahmad, Jr   +5 more
doaj   +1 more source

Visible Tongue Fasciculations With Electromyographic Denervation in Autopsy‐Proven Progressive Supranuclear Palsy Mimicking Amyotrophic Lateral Sclerosis

Muscle &Nerve, Volume 74, Issue 2, Page 496-499, August 2026.
Hiroyasu Inoue, Yoshihiko Horimoto, Yo Tsuda, Yuta Madokoro, Shoji Kawashima, Akio Akagi, Yasushi Iwasaki, Noriyuki Matsukawa   +7 more
wiley   +1 more source