Results 81 to 90 of about 28,817 (265)
Clinical phenotype and prognosis of real‐world patients with wild‐type transthyretin amyloid cardiomyopathy treated with tafamidis
European Journal of Heart Failure, EarlyView.Aims
Tafamidis reshaped the treatment paradigm in transthyretin amyloid cardiomyopathy (ATTR‐CM) based on a phase‐3 randomized controlled trial, but real‐world data on its use remain limited. This study aimed to assess in a large, contemporary, real‐world cohort of patients with wild‐type ATTR‐CM (ATTRwt‐CM) (i) the clinical phenotype of patients ...Aldostefano Porcari, Paolo Milani, Simone Longhi, Francesco Cappelli, Fabio Vagnarelli, Alberto Aimo, Alberto Cipriani, Elisa Gardini, Stefania Marazia, Emanuele Monda, Giacomo Tini, Beatrice Musumeci, Matteo Serenelli, Anna Cantone, Carla Lofiego, Marco Marini, Giuseppe Vergaro, Grazia Foti, Francesco Musca, Daniela Tomasoni, Giacomo Bonacchi, Federica Colio, Giulio Sinigiani, Laura De Michieli, Francesca Sturdà, Marco Pozzan, Piero Gentile, Samuela Carigi, Michela Bartolotti, Giuseppe Sena, Irene Ruotolo, Giuseppe Damiano Sanna, Margherita Zanoletti, Marco Canepa, Massimo Di Marco, Emilia D'Elia, Gianluca Di Bella, Mauro Driussi, Massimo Imazio, Federico Perfetto, Elena Biagini, Giuseppe Limongelli, Marco Metra, Michele Emdin, Giampaolo Merlini, Stefano Perlini, Marco Merlo, Giovanni Palladini, Gianfranco Sinagra +48 morewiley +1 more sourceArtificial intelligence‐based echocardiographic assessment for monitoring disease progression in transthyretin cardiac amyloidosis
European Journal of Heart Failure, EarlyView.Artificial intelligence (AI)‐based estimation of stroke volume for risk prediction in amyloid transthyretin cardiomyopathy (ATTR‐CM). ATTRv, hereditary transthyretin amyloidosis; ATTRwt, wild‐type transthyretin amyloidosis; CI, confidence interval; HR, hazard ratio; IQR, interquartile range; LVOT‐VTI, left ventricular outflow tract velocity‐time ...Lucia Venneri, Alberto Aimo, Aldostefano Porcari, Irem Sezer, Adam Ioannou, Awais Sheikh, Josephine Mansell, Yousuf Razvi, Surabhi Bhaskar Iyer, Ana Martinez‐Naharro, Francesco Bandera, Sze Chi Lim, Matthew Frost, Justin Ezekowitz, Carolyn S.P. Lam, William Moody, Carol Whelan, Helen Lachmann, Ashutosh Wechelakar, Michele Emdin, Philip N. Hawkins, Scott David Solomon, Julian D. Gillmore, Marianna Fontana +23 morewiley +1 more source325 Dealing with cardiac amyloidosis diagnosis: keep calm and use the magnifying glasses! [PDF]
, 2021 Laura De Michieli, Luca Licchelli, Giulio Sinigiani, Tamara Berno, Mila Della Barbera, Stefania Rizzo, Cristina Basso, Martina Perazzolo Marra, Sabino Iliceto, Alberto Cipriani +9 moreopenalex +1 more sourceMicrovascular obstruction in cardiac amyloidosis
European Journal of Heart Failure, EarlyView.Lucrezia Netti, Adam Ioannou, Ana Martinez‐Naharro, Yousuf Razvi, Aldostefano Porcari, Lucia Venneri, Viviana Maestrini, Dan Knight, Ruta Virsinskaite, Muhammad U. Rauf, Tushar Kotecha, Rishi K. Patel, Ashutosh Wechelakar, Helen Lachmann, Peter Kellman, Charlotte Manisty, James Moon, Philip N. Hawkins, Julian D. Gillmore, Marianna Fontana +19 morewiley +1 more sourceLeft ventricular transthyretin amyloid load and apical sparing in patients with newly confirmed transthyretin amyloid cardiomyopathy
European Journal of Heart Failure, EarlyView.In a large cohort of patients with newly diagnosed transthyretin amyloid cardiomyopathy (ATTR‐CM), echocardiographic apical sparing was associated with increased left ventricular amyloid load and atrial remodelling. Quantitative biopsy analysis revealed that Perugini scores often failed to accurately reflect myocardial amyloid burden.Thomas Krammer, Maria J. Baier, Vanessa Lutz, Anna‐Christina Hübner, Tilman Zschiedrich, David Lukas, Christian Le Phu, Matthias Wolf, Claire Maassen, Michael Wester, Stefan Neef, Christian Schach, Can‐Martin Sag, Katja Evert, Michael Paulus, Christine Meindl, Maria Tafelmeier, Kurt Debl, Lars S. Maier, Stefan Wagner, Christoph Röcken, Julian Mustroph +21 morewiley +1 more sourceThe scintigraphic diagnosis of cardiac amyloidosis. An expert opinion endorsed by the Section of Nuclear Medicine of the Polish Cardiac Society and the Polish Nuclear Medicine Society
, 2022 Katarzyna Holcman, Mirosław Dziuk, Jacek Grzybowski, Anna Teresińska, Bogdan Małkowski, Diana Jędrzejuk, Bogna Brockhuis, Rafał Czepczyński, Lidia Tomkiewicz−Pająk, Magdalena Kostkiewicz +9 moreopenalex +2 more sources