Results 121 to 130 of about 5,299 (208)

Transcriptomic and functional responses of the cystic fibrosis airway epithelium to CFTR modulator therapy. [PDF]

JCI Insight
Vladar EK, Gillen AE, Yadav S, Murphree MR, Baraghoshi D, Harris JK, Pruesse E, Niemiec SS, Wilson AW, Hisert KB, Humphries SM, Strand M, Lynch DA, Seibold MA, Beswick DM, Taylor-Cousar JL.   +15 more
europepmc   +1 more source

Quantitative Systems Toxicology Predicts Ivacaftor-Induced Oxidative Stress Contributes to CFTR Modulator Hepatotoxicity. [PDF]

Clin Pharmacol Ther
Shi A, Cornwell C, Yang K, Beringer PM.
europepmc   +1 more source

Long-Term Follow-Up of Health-Related Quality of Life and Short-Term Intervention with CFTR Modulator Therapy in Adults with Cystic Fibrosis: Evaluation of Changes over Several Years with or without 33 Weeks of CFTR Modulator Therapy. [PDF]

Healthcare (Basel), 2023
Gruber W, Welsner M, Blosch C, Dillenhoefer S, Olivier M, Brinkmann F, Koerner-Rettberg C, Sutharsan S, Mellies U, Taube C, Stehling F.   +10 more
europepmc   +1 more source

Functional, Cohort-Level Assessment of CFTR Modulator Responses Using Biobanked Nasal Epithelial Cells from Individuals with Cystic Fibrosis. [PDF]

J Pers Med
Aalbers BL, Amatngalim GD, Aarts EM, Rodenburg LW, den Hertog-Oosterhoff LA, Heijerman HGM, Beekman JM.   +6 more
europepmc   +1 more source

RFFL-mediated protein quality control limits functional rescue of TRID-CFTR modulator combination therapy for cystic fibrosis nonsense mutations. [PDF]

Cell Mol Life Sci
Tateishi H, Doi Y, Kamada Y, Okiyoneda T.   +3 more
europepmc   +1 more source

The impact of CFTR modulator triple therapy on type 2 inflammatory response in patients with cystic fibrosis. [PDF]

Allergy Asthma Clin Immunol, 2023
Mehta AM, Lee I, Li G, Jones MK, Hanson L, Lonabaugh K, List R, Borish L, Albon DP.   +8 more
europepmc   +1 more source

Short-term monitoring of CFTR modulator therapy in adults and children with cystic fibrosis using low and ultra-low-dose lung CT. [PDF]

Radiol Med
Maccioni F, Cimino G, Longhi A, Busato L, Valenti A, Bottino L, Rutigliano M, Alessandrelli R, Landini N, Catalano C.   +9 more
europepmc   +1 more source

Real-life impact of highly effective CFTR modulator therapy in children with cystic fibrosis. [PDF]

Front Pharmacol, 2023
Olivier M, Kavvalou A, Welsner M, Hirtz R, Straßburg S, Sutharsan S, Stehling F, Steindor M.   +7 more
europepmc   +1 more source

Evolving nutrition therapy in cystic fibrosis: Adapting to the CFTR modulator era. [PDF]

Nutr Clin Pract
Vavrina K, Griffin TB, Jones AM, Schindler T, Bui TN, Sankararaman S.   +5 more
europepmc   +1 more source

Personalizing CFTR modulator therapies [PDF]

, 2021
openaire   +1 more source