Results 41 to 50 of about 9,594 (241)
Acquired prion disease: iatrogenic CJD, variant CJD, kuru [PDF]
British Medical Bulletin, 2003 Human prion diseases can be classified as sporadic, hereditary or acquired. The cause of sporadic Creutzfeldt-Jakob disease (CJD) is unknown, hereditary cases are associated with mutations of the prion protein gene (PRNP) and acquired forms are caused by the transmission of infection from human to human or, as a zoonosis, from cattle to human. Although
openaire +2 more sources
Biomedicines, 2021 Systemic inflammation and the host immune responses associated with certain viral infections may accelerate the rate of neurodegeneration in patients with Creutzfeldt–Jakob disease (CJD), a rare, transmissible neurodegenerative disease.
Dumitru Ciolac +13 more
doaj +1 more source
Alzheimer’s Research & Therapy, 2021 Background Blood neurofilament light (Nfl) and total-tau (t-tau) have been described to be increased in several neurological conditions, including prion diseases and other neurodegenerative dementias.
Inga Zerr +9 more
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Anesthetic management in patients suspected of Creutzfeldt-Jakob disease -A case report- [PDF]
Korean Journal of Anesthesiology, 2011 Creutzfeldt-Jakob disease (CJD) is a fatal neurodegenerative disorder in which accumulation of the pathogenic prion protein induces neuronal damage and results in distinct pathologic features. This abnormal prion is an infectious protein and resistant to
Chi Bum In +6 more
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Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective To characterize the demographic, clinical, and laboratory features of the Chinese patients of genetic Creutzfeldt‐Jakob disease with T188K variant (T188K‐gCJD), the most common subtype of genetic prion diseases (gPrDs) in China. Methods In this nationwide retrospective study, data from 98 genetically confirmed T188K‐gCJD patients ...
Chun‐Jie Li +11 more
wiley +1 more source
Unveiling a Diagnostic Odyssey: A Case Report on Delayed Diagnosis of Creutzfeldt Jakob Disease
Journal of Islamic International Medical CollegeCreutzfeldt Jakob Disease (CJD) is a rare prion infection causing rapid, progressive, invariably fatal neurodegenerative disorder. It is reported in 1 in a million people per year worldwide and only 12 cases have been reported over 21 years between 1994 ...
Shafaq Saleem
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Creutzfeldt-Jakob disease: literature review based on three case reports
Dementia & Neuropsychologia, 2022 . Creutzfeldt-Jakob disease (CJD) is one of the transmissible spongiform encephalopathies that lead to rapidly progressive dementia. CJD has a low prevalence, and the average survival is only 1 year after the onset of symptoms.
Amandha Alencar Maia Carneiro +3 more
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Early Recognition of Treatment‐Responsive Rapidly Progressive Dementia: The Modified STAM3mP Score
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Early identification of patients with treatment‐responsive rapidly progressive dementia (RPD) is important as early treatment improves outcomes. The STAM3P score identifies treatment‐responsive RPD using “high risk” presenting features. We optimized performance by adding a time component (i.e., dementia within 3 months) and validated the ...
R. W. van Steenhoven +16 more
wiley +1 more source
Biomedicines, 2022 Creutzfeldt–Jakob disease (CJD), the most common human prion disorder, may occur as “pure” neurodegeneration with isolated prion deposits in the brain tissue; however, comorbid cases with different concomitant neurodegenerative diseases have been ...
Nikol Jankovska +7 more
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Tailoring Phonon‐Driven Responses in α‐MoO3 through Isotopic Enrichment
Advanced Materials, EarlyView.ABSTRACT The implementation of polaritonic materials into nanoscale devices requires selective tuning of parameters to realize desired spectral or thermal responses. One robust material, α‐MoO3, an orthorhombic crystal boasting three distinct phonon dispersions, provides three polaritonic dispersions of hyperbolic phonon polaritons (HPhPs) across the ...
Thiago S. Arnaud +31 more
wiley +1 more source