Frontiers in Genetics, 2023 Enlarged vestibular aqueduct is an autosomal genetic disease mainly caused by mutations in the SLC26A4 gene and includes non-syndromic and syndromic types.
Yunhua Huang +13 more
doaj +1 more source
Dosimetric Analysis of Neural and Vascular Structures in Skull Base Tumors Treated with Stereotactic Radiosurgery. [PDF]
, 2017 Objective To examine the relationship between the prescribed target dose and the dose to healthy neurovascular structures in patients with vestibular schwannomas treated with stereotactic radiosurgery (SRS).
Bhatt, Jay M +6 more
core +1 more source
International Archives of Otorhinolaryngology, 2015 Introduction Large vestibular aqueduct syndrome (LVAS) is characterized by the enlargement of the vestibular aqueduct associated with sensorineural hearing loss.
Rabindra Pradhananga +3 more
doaj +1 more source
The Development of a Single Frequency Place in the Mammalian Cochlea: The Cochlear Resonance in the Mustached Bat Pteronotus parnellii [PDF]
, 2003 Cochlear microphonic potentials (CMs) were recorded from the sharply tuned, strongly resonant auditory foveae of 1- to 5-week-old mustached bats that were anesthetized with Rompun and Ketavet.
Drexl, Markus +4 more
core +2 more sources
Synchronization of a Nonlinear Oscillator: Processing the Cf Component of the Echo-Response Signal in the Cochlea of the Mustached Bat [PDF]
, 2003 Cochlear microphonic potential (CM) was recorded from the CF2 region and the sparsely innervated zone (the mustached bat's cochlea fovea) that is specialized for analyzing the Doppler-shifted echoes of the first-harmonic (~61 kHz) of the constant ...
, +5 more
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Direct administration of 2-Hydroxypropyl-Beta-Cyclodextrin into guinea pig cochleae: Effects on physiological and histological measurements. [PDF]
PLoS ONE, 2017 2-Hydroxypropyl-Beta-Cyclodextrin (HPβCD) can be used to treat Niemann-Pick type C disease, Alzheimer's disease, and atherosclerosis. But, a consequence is that HPβCD can cause hearing loss. HPβCD was recently found to be toxic to outer hair cells (OHCs)
J T Lichtenhan +4 more
doaj +1 more source
Cochlear Implant Outcomes and Genetic Mutations in Children with Ear and Brain Anomalies [PDF]
, 2015 Background. Specific clinical conditions could compromise cochlear implantation outcomes and drastically reduce the chance of an acceptable development of perceptual and linguistic capabilities.
Aimoni, C +8 more
core +4 more sources
Acta Médica Portuguesa, 1993 In this review of cochlear malformations, 17 cases were studied by CT scan (high resolution-target program) including 10 males and 7 females. The anomaly was bilateral in 12 cases and unilateral in 7 (the latter included 2 Mondini type aplasias and one ...
J C Maurício, L Biscoito, G Branco
doaj +1 more source
E-ABR in patients with cochlear implant: A comparison between patients with malformed cochlea and normal cochlea [PDF]
, 2019 OBJECTIVES: This study aims to compare the electrical auditory brainstem response (EABR) following cochlear implant (CI) surgery in pediatric subjects with cochlear malformation and a normal cochlea, in order to assess the sensitivity of EABR and to ...
de Lucia A. +7 more
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The Egyptian Journal of Radiology and Nuclear Medicine, 2018 Objectives: Evaluating the value of MRI for assessing congenital anomalies of the inner ear in children with congenital sensorineural hearing loss (SNHL) before cochlear implantation.
Kareem Mohsen Moussa +2 more
doaj +1 more source