Results 261 to 270 of about 70,504 (293)

PRKAG2 cardiac syndrome: familial ventricular preexcitation, conduction system disease, and cardiac hypertrophy

Current Opinion in Cardiology, 2002
Genetic studies of families with inherited cardiac rhythm disturbances have established a molecular basis for ventricular arrhythmogenic disorders. Genes responsible for the long QT syndrome, Brugada syndrome, and polymorphic ventricular tachycardia have been identified.
Michael H, Gollob, Martin S, Green, Anthony S L, Tang, Robert, Roberts   +3 more
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Conduction system disease in cardiac amyloidosis

Trends in Cardiovascular Medicine
Cardiac amyloidosis (CA) has diverse and deleterious effects on the conductive system. Atrial fibrillation is by far the most common electrophysiological manifestation of CA and is associated with more mortality, morbidity, and hospitalizations. While AF increases the risk of thrombosis regardless of the CHA2DS2-VASc score, the risk of thromboembolism ...
Ala’ Assaf, Mario Mekhael, Charbel Noujaim, Nour Chouman, Hadi Younes, Omar Kreidieh, Nassir Marrouche, Eoin Donnellan   +7 more
openaire   +2 more sources

Cardiac conduction system disease after transcatheter aortic valve replacement

American Heart Journal, 2012
Transcatheter aortic valve replacement (TAVR) is a rapidly-evolving technology for patients with severe, calcific aortic stenosis. Although these procedures lessen many of the risks and complications of open surgical aortic valve replacement, there remain challenges with TAVR including electrophysiologic complications.
Benjamin A, Steinberg, J Kevin, Harrison, Camille, Frazier-Mills, G Chad, Hughes, Jonathan P, Piccini   +4 more
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Abstract P1144: Single-cell RNA-Sequencing Of The Murine Cardiac Conduction System Reveals Transcriptional Regulators Associated With Conduction Development And Disease

Circulation Research, 2023
Rhythmic beating of the heart is driven by a small subset of heart cells, altogether known as the cardiac conduction system (CCS). The CCS consists of unique components including the sinoatrial node (SAN), the atrioventricular node (AVN), the bundle of His, bundle branches and Purkinje fiber (PF) system.
Benjamin Beyersdorf, Felix Atzert, Sean M Wu, William R Goodyer   +3 more
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Cardiac transthyretin amyloidosis in patients with conduction system disease

European Heart Journal
Abstract Background/Introduction Cardiac amyloidosis (CA) is characterized by extracellular deposition of misfolded proteins in the heart. The data suggest that cardiac amyloidosis is underappreciated as a cause of common cardiac diseases or syndromes.
J Pudich, J Plasek, H Pudichova, J Seleng, E Kapsova, J Syler, K Musiolova, D Drienikova, J Pavlicek, J Vaclavik   +9 more
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Sodium channel kinetic changes that produce Brugada syndrome or progressive cardiac conduction system disease

American Journal of Physiology-Heart and Circulatory Physiology, 2007
Some mutations of the sodium channel gene NaV1.5 are multifunctional, causing combinations of LQTS, Brugada syndrome and progressive cardiac conduction system disease (PCCD). The combination of Brugada syndrome and PCCD is uncommon, although they both result from a reduction in the sodium current.
Zhu-Shan, Zhang, Joseph, Tranquillo, Valentina, Neplioueva, Nenad, Bursac, Augustus O, Grant   +4 more
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Electrophysiologic effects of intravenous magnesium in patients with normal conduction systems and no clinical evidence of significant cardiac disease

American Heart Journal, 1988
Parenteral magnesium has been used for several decades in the empiric treatment of various arrhythmias, but the data on its electrophysiologic effects in man are limited. We evaluated the electrophysiologic effects of magnesium sulfate (MgSO4) administration in eight normomagnesemic patients with normal mononuclear cell magnesium content, who had no ...
D L, Kulick, R, Hong, E, Ryzen, R K, Rude, J N, Rubin, U, Elkayam, S H, Rahimtoola, A K, Bhandari   +7 more
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Postmortem Studies of the Intertruncal Plexus and Cardiac Conduction System From Patients With Chagas Disease Who Died Suddenly☆

Progress in Cardiovascular Diseases, 2005
Throughout the cardiac conduction system of each heart there were numerous destructive lesions including focal inflammatory infiltration with lymphocytes and in neighboring regions extensive focal fibrotic degeneration. These lesions involved myocytes, nerves and blood vessels.
Thomas N, James, Marcos A, Rossi, Shoji, Yamamoto   +2 more
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A novel mutation of the LMNA gene in a family with dilated cardiomyopathy, conduction system disease, and sudden cardiac death of young females

Molecular and Cellular Biochemistry, 2013
The LMNA gene, which encodes the nuclear envelope protein lamin A/C, is considered to be the most common autosomal disease gene associated with familial dilated cardiomyopathy. To date, each mutation of the LMNA gene has been associated with a specific disease phenotype.
Wenting, Chen, Jianhua, Huo, Aiqun, Ma, Ling, Bai, Ping, Liu   +4 more
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[Steinert's disease with cardiac arrhythmia. Morphological findings in the heart conduction system].

Archivos del Instituto de Cardiologia de Mexico, 1975
This is a case report of a 63-year-old man with myotonic dystrophy in whom an ECG showed atrial flutter, complete A-V block, idioventricular rhythm with image of left bundle branch block and giant, wide and negative "T-U" waves. The microscopic study of the conduction system showed slight fibrosis of the SAN, fatty infiltration and cellular atrophy of ...
R, Drut, O, Velasco Vela, L, Maljar
openaire   +1 more source