Results 41 to 50 of about 2,400 (108)

Evaluation of clinical, epidemiological and electrophysiological variables for early diagnosis of amyotrophic lateral sclerosis [PDF]

open access: yes, 2020
Motor neuron disease (MND) is a systemic disease with a broad clinical spectrum. It is characterized by primary involvement of the lower or upper motor neuron (UMN), or both, simultaneously, represented by the most common form, amyotrophic lateral ...
Coutinho, Bruno Mattos   +5 more
core   +2 more sources

Apresentação clínica de SCA2 como uma síndrome ataxia-parkinsonismo-doença do neurônio motor [PDF]

open access: yes, 2011
Universidade Federal de São Paulo (UNIFESP) Department of Neurology and Neurosurgery Division of General Neurology and AtaxiasUNIFESP, Department of Neurology and Neurosurgery Division of General Neurology and ...
Abrahão, Agessandro   +6 more
core   +3 more sources

Therapeutic advances in 5q-linked spinal muscular atrophy

open access: yesArquivos de Neuro-Psiquiatria
Spinal muscular atrophy (SMA) is a severe and clinically-heterogeneous motor neuron disease caused, in most cases, by a homozygous mutation in the SMN1 gene.
Umbertina Conti Reed, Edmar Zanoteli
doaj   +1 more source

Benign monomelic amyotrophy: a study of twenty-one cases Amiotrofia monomélica benigna: estudo de 21 casos

open access: yesArquivos de Neuro-Psiquiatria, 2000
A consecutive series of 21 patients with single limb atrophy (monomelic amyotrophy) is reported. Sixteen had lower limb atrophy and five had upper limb involvement. The median age of the onset was 20 years.
MARCOS R.G. DE FREITAS   +1 more
doaj   +1 more source

Far beyond the motor neuron: the role of glial cells in amyotrophic lateral sclerosis [PDF]

open access: yes, 2016
Motor neuron disease is one of the major groups of neurodegenerative diseases, mainly represented by amyotrophic lateral sclerosis. Despite wide genetic and biochemical data regarding its pathophysiological mechanisms, motor neuron disease develops under
Oliveira, Acary Souza Bulle   +3 more
core   +1 more source

NEUROPATIA MOTORA MULTIFOCAL, REVISÃO E RELATO [PDF]

open access: yes, 2023
Em 1985, na reunião anual da Academia Americana de Medicina Neuromuscular e Eletrodiagnóstica, Gareth Parry e Stephen Clarke apresentaram casos de 3 pacientes com neuropatia exclusiva motora comprometendo os membros superiores.
Bottura PICHI, Juliano   +2 more
core   +1 more source

Neuromiopatia isquêmica em cinco cães (2008-2016)

open access: yesPesquisa Veterinária Brasileira
RESUMO: O objetivo deste estudo foi apresentar dados epidemiológicos, clínicos e anatomopatológicos de cinco cães com neuromiopatia isquêmica secundária a trombose ou tromboembolismo aórtico.
Angel Ripplinger   +6 more
doaj   +1 more source

Use of cyclic AMP on facial nerve regeneration of rats [PDF]

open access: yes, 2007
OBJETIVO: Estudar a possível influência neurotrófica do nucleotídeo cíclico adenosina monofosfato (AMPc) na regeneração do nervo facial de ratos Wistar.
Borin, Andrei
core   +1 more source

Processamento auditivo central e caracterização de aspectos cognitivos em mulheres pós-menopáusicas [PDF]

open access: yes, 2012
Introduction : The hormonal changes associated with menopause are able to modulate functions that are important for the central processing of verbal information.
Schlickmann, Ângela Flores
core  

Definitions, phenomenology, diagnosis, and management of the disorders of laughter and crying in amyotrophic lateral sclerosis (ALS): Consensus from ALS and Motor Neuron Disease Scientific Department of the Brazilian Academy of Neurology. [PDF]

open access: yesArq Neuropsiquiatr, 2023
Gondim FAA   +11 more
europepmc   +1 more source

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