Results 1 to 10 of about 217 (121)

Homozygote drepanocytosis: Ferric status and inflammation in world and Africa: Review article and meta analysis [PDF]

open access: yesHealth Science Reports, 2023
Background and Aims Major sickle cell syndromes are subjected to a high frequency of hemolysis, infections, oxidative stress, and vasooclusive crises which promote inflammation and iron balance disorders. We aimed to systematically review and analyze the
Romaric Tuono De Manfouo   +5 more
doaj   +2 more sources

Aseptic necrosis of the femoral head after pregnancy: a case report [PDF]

open access: yesThe Pan African Medical Journal, 2016
A documented case of beginning aseptic necrosis of the femoral head associated with pregnancy together with a review of the literature about this rare complication of pregnancy is presented.
Kawtar Nassar   +3 more
doaj   +2 more sources

Pathological basis of symptoms and crises in sickle cell disorder: implications for counseling and psychotherapy

open access: yesHematology Reports, 2010
Sickle Cell Disorder (SCD) is a congenital hemoglobinopathy. There is little in literature regarding the psychological variables affecting individuals living with SCD and all of the significant people around them.
Oluwatoyin Olatundun Ilesanmi
doaj   +1 more source

ROLE OF STEM CELL FACTOR IN THE REACTIVATION OF HUMAN FETAL HEMOGLOBIN

open access: yesMediterranean Journal of Hematology and Infectious Diseases, 2009
In humans the switch from fetal to adult  hemoglobin (HbF→ HbA) takes place in the perinatal and postnatal period, determining the progressive replacement of HbF with HbA synthesis ( i.e., the relative HbF content in red blood cells decreases from 80-90%
Marco Gabbianelli, Ugo Testa
doaj   +3 more sources

Gender-Related Differences in Sickle Cell Disease in a Pediatric Cohort: A Single-Center Retrospective Study

open access: yesFrontiers in Molecular Biosciences, 2019
Sickle cell disease (SCD) is one of the most common monogenic disease worldwide. The incidence of SCD is not strictly gender-related as it is transmitted as an autosomal recessive disorder.
Giulia Ceglie   +10 more
doaj   +1 more source

Behavior of renal disorders in pediatric patients with drepanocytosis

open access: yesActa Médica del Centro, 2017
Introduction: the drepanocytosis is a disease with multisystem impact. Renal disease begins in childhood and chronic consequences are glomerulopathy sickle glomerular with evolution to chronic renal failure.
Marta Beatriz García Caraballoso   +5 more
doaj  

Anticuerpos naturales anti banda 3: Participan en el fenómeno de vasooclusión de la drepanocitosis Natural anti-band 3 antibodies: Do they take part in the phenomenon of vasoocclusion drepanocytosis

open access: yesRevista Cubana de Hematología, Inmunología y Hemoterapia, 2007
Se determinó la presencia de anticuerpos naturales anti banda 3 mediante un ensayo inmunoenzimático en microplacas acopladas con la proteína banda 3 en 14 pacientes con drepanocitosis, 4 con crisis vasooclusiva dolorosa y 10 en estado basal.
Rinaldo Villaescusa Blanco   +4 more
doaj  

Función de los anticuerpos naturales anti banda 3 en el fenómeno de vasooclusión de la drepanocitosis Function of the natural anti-band 3 antiodies in the phenomenon of drepanocytosis vasoocclusion

open access: yesRevista Cubana de Hematología, Inmunología y Hemoterapia, 2005
La vasooclusión en la drepanocitosis se considera una característica única entre las anemias hemolíticas, y aún cuando se han logrado avances en su conocimiento, las bases de su control y prevención permanecen parcialmente desconocidas. La idea de que el
Rinaldo Villaescusa Blanco   +1 more
doaj  

Investigaciones relevantes en el Instituto de Hematología e Inmunología en la década 2000-2009 Relevant researches in the Institute of Hematology and Immunology during 2000-2009

open access: yesRevista Cubana de Hematología, Inmunología y Hemoterapia, 2011
A partir de la creación en 1966 del Instituto de Hematología e Inmunología (IHI), se abrieron nuevas perspectivas para el desarrollo e integración de estas especialidades en Cuba.
Rosa M. Lam-Díaz   +2 more
doaj  

Purificación de anticuerpos naturales anti banda 3 de la clase IgG Purification of natural anti-band 3 IgG antibodies

open access: yesRevista Cubana de Hematología, Inmunología y Hemoterapia, 2007
Se purificaron anticuerpos naturales anti banda 3 de la clase IgG mediante cromatografía de afinidad con un aceptable nivel de pureza, rapidez y eficiencia, a partir de una mezcla de inmunoglobulinas humanas de uso parenteral.
Julio César Merlín Linares   +2 more
doaj  

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