Results 111 to 120 of about 792 (148)

Scleroderma en Coup de Sabre

Annals of Plastic Surgery, 1983
Five cases of scleroderma en coup de sabre are reported, along with a brief review of the literature [3, 10, 11]. Surgical management was tailored to the defects. Involved discolored skin was excised and the resultant wound repaired by direct closure (forehead, lower lip) or with full-thickness skin grafts.
M F, Milan, J E, Bennett
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Linear scleroderma “En Coup de Sabre” of the cheek

Journal of Oral and Maxillofacial Surgery, 2003
Linear scleroderma (LS) is a variant of localized scleroderma most commonly seen in the lower limbs and to a lesser extent in the arms and face.1 Systemic involvement in LS is extremely rare.1,2 The term “en coup de sabre” is used for linear scleroderma located in the temporoparietal region that produces sharp bordered furrowing with alopecia when ...
Demir, Y, Karaaslan, T, Aktepe, F, Yücel, A, Demir, S   +4 more
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Management Options for Linear Scleroderma (“En Coup de Sabre”)

Dermatologic Surgery, 2022
BACKGROUND En coup de sabre (ECDS) is a form of linear-scleroderma, primarily affecting the face. Despite effectiveness of pharmacological interventions in the management of lesions, sequelae of cutaneous deformities are common.
Ron, Skorochod, Gideon, Nesher, Yoav, Gronovich   +2 more
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Bilateral En Coup de Sabre—A Rare Entity

Pediatric Dermatology, 2000
Abstract: Linear scleroderma involving the frontal or frontoparietal region of the scalp (with or without associated facial hemiatrophy) is called “en coup de sabre” (like the stroke of a sabre). We report a case which to the best of our knowledge is only the fifth instance of this subset of localized morphea occurring in a bilateral distribution.
R, Rai, S, Handa, S, Gupta, B, Kumar
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Reversible alopecia in En Coup de Sabre morphea

Pediatric Dermatology, 2021
AbstractEn coup de sabre form of morphea often affects the scalp with thickening, sclerosis, dyspigmentation, and scarring alopecia. Traditionally, it has been thought that the alopecia is not responsive to treatment and permanent. This report presents two cases with extensive, apparent scarring alopecia that improved with medical treatment.
Hiba Zaaroura, Elena Pope, Ronald M. Laxer, Cathryn Sibbald   +3 more
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Atypical Cases of Scleroderma en Coup de Sabre

Journal of Child Neurology, 2014
Scleroderma en coup de sabre typically presents with a cutaneous induration, but involvement of the underlying bone, eye, and brain is common. We report on 4 pediatric cases with atypical initial clinical presentations. All cases were seen at the University of California San Francisco.
Verena, Kraus, Erica F, Lawson, Emily, von Scheven, Tarik, Tihan, Judith, Garza, Rani G, Nathan, Kelly M, Cordoro, Emmanuelle, Waubant   +7 more
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Linear scleroderma ‘en coup de sabre’

Practical Neurology
Linear scleroderma ‘en coup de sabre’ is a rare condition characterised by inflammation and fibrosis of the skin and underlying tissues; it rarely presents in adults. The adult-onset form seldom has extracutaneous manifestations, but those that occur are usually neurological. A 43-year-old woman with epilepsy had a scar-like lesion on her forehead. The
Patxi Zavala Gottau, Francisco Caiza-Zambrano, Luis Ariel Miquelini, Maria Sol Pacha, Diego Tripodi, Yemina Neme, Mauricio Agustin Benetti, Andrea Dolores Ezquiaga, Mauricio Jiménez, Andrea Gomez, Félix Vigovich, Oscar Adolfo Martínez   +11 more
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En coup de sabre.

Cutis, 2019
En coup de sabre (ECDS) is a rare form of localized scleroderma that typically manifests in children and women. It presents as a fibrous pansclerotic plaque extending in a bandlike distribution on the frontoparietal scalp with surrounding scarring alopecia.
Paul M, Graham, Naeha, Gupta, David A, Altman   +2 more
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Double-Lined Frontoparietal Scleroderma en coup de sabre

Dermatology, 1999
We describe a rare case of double-lined frontoparietal scleroderma en coup de sabre. The relationship to the distribution following the lines of Blaschko is discussed. In addition, we present a genetic hypothesis which is based on a mosaic state induced by postzygotic mosaicism.
Itin PH, Schiller P
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Linear scleroderma (morphoea) “en coup de sabre”

2008
Scleroderma is a rare connective tissue disorder of unknown etiology in which increased collagen deposition occurs and results in sclerosis of the skin and subcutaneous tissue (with dermal atrophy), often affecting the underlying muscle and bone (Sampaio et al. 2006).
PASCUAL CASTROVIEJO I, RUGGIERI, MARTINO
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