Double-Lined Frontoparietal Scleroderma en coup de sabre
We describe a rare case of double-lined frontoparietal scleroderma en coup de sabre. The relationship to the distribution following the lines of Blaschko is discussed. In addition, we present a genetic hypothesis which is based on a mosaic state induced by postzygotic mosaicism.
Itin PH, Schiller P
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Co-occurrence of En Coup de Sabre, Parry-Romberg Syndrome, and Hemi Masticatory Spasm: A Case Report [PDF]
Introduction: En coup de sabre (ECDS) and Parry-Romberg syndrome (PRS) are rare, localised scleroderma subtypes, often considered to be overlapping variants of morphea.
Pooja Chaurasia +3 more
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Histological Changes of Linear Scleroderma “en Coup de Sabre”
Introduction. Scleroderma is a chronic disease of unknown aetiology characterized by skin fibrosis and is divided into two clinical entities: localized scleroderma and systemic sclerosis.
M. Мaтошвілі +3 more
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Introduction. Progressive facial hemiatrophy (Parry-Romberg syndrome)is a relatively rare disease of unclear aetiology. Some authorspostulate its relation with linear scleroderma.Objective.
Ligia Brzezińska-Wcisło +2 more
doaj +1 more source
Parry–Romberg syndrome (PRS) may overlap localized scleroderma (morphea) lesions with linear depression (en coup de sabre [ECDS]). Overlap case with PRS and ECDS was presented.
Hatice Atas +4 more
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Linear scleroderma en coup de sabre in an adult female: Ocular, adnexal and tomographic features [PDF]
Sushmita G Shah +4 more
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Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections [PDF]
Linear scleroderma “en coup de sabre” (LSCS) is a form of localized scleroderma presents as band-like sclerotic lesions of the frontoparietal area. It has been reported in association with diverse neurological manifestations like seizures, migraine ...
Carlos A. Cañas +3 more
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En coup de sabre accompanied by pachydermoperiostosis: a case report.
Scleroderma en coup de sabre, a variant of localized scleroderma is a disorder characterized by fibrosis of connective tissue. We report a 21-year-old female with scleroderma en coup de sabre accompanied by pachydermoperiostosis. She was born to consanguineous parents and her older sister also had pachydermoperiostosis characterized by clubbing of the ...
Ozdemir, M. +2 more
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Lichen sclerosus et atrophicans, scleroderma en coup de sabre and Lyme borreliosis
Lichen sclerosus et atrophicans (LSA) is a chronic, inflammatory skin disease of unknown etiology, characterized by atrophy. We report a case of LSA with frontoparietal distribution, mimicking scleroderma en coup de sabre, causing scarring alopecia. The
Serena Bonin +2 more
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Therapeutic and Reconstructive Management Options in Scleroderma (Morphea) en Coup de Sabre in Children and Adults. A Systematic Literature Review. [PDF]
Scleroderma (morphea) en coup de sabre is a localized subtype restricted to the frontoparietal region of the head. Current treatment paradigms rely on low levels of evidence, primarily case reports and case series-supported by expert opinions. The aim of
Ulc E +5 more
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