Results 31 to 40 of about 792 (148)
Neurologic Involvement in Scleroderma en Coup de Sabre [PDF]
Autoimmune Diseases, 2012 Localized scleroderma is a rare disease, characterized by sclerotic lesions. A variety of presentations have been described, with different clinical characteristics and specific prognosis. In scleroderma en coup de sabre (LScs) the atrophic lesion in frontoparietal area is the disease hallmark. Skin and subcutaneous are the mainly affected tissues, but
Tiago Nardi Amaral +5 more
openaire +3 more sources
Parry-Romberg Syndrome with En Coup de Sabre [PDF]
Annals of Dermatology, 2011 Parry-Romberg syndrome (PRS) is a relatively rare degenerative disorder that is poorly understood. PRS is characterized by slowly progressing atrophy affecting one side of the face, and is frequently associated with localized scleroderma, especially linear scleroderma, which is known as en coup de sabre.
Jae Hun Jun +7 more
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Brain cavernomas associated with en coup de sabre linear scleroderma: Two case reports
Pediatric Rheumatology Online Journal, 2011 Linear scleroderma is a form of localized scleroderma that primarily affects the pediatric population. When it occurs on the scalp or forehead, it is termed "en coup de sabre".
Laxer Ronald M +5 more
doaj +1 more source
BMC Neurology, 2009 Background Hemifacial atrophy (Parry-Romberg syndrome) is a relatively rare disease. The etiology of the disease is not clear. Some authors postulate its relation with limited scleroderma linearis.
Brzezińska-Wcisło Ligia +2 more
doaj +1 more source
Pediatrics and Neonatology, 2009 Linear scleroderma is a form of localized scleroderma characterized by sclerotic lesions distributed in a linear, band-like pattern. The “en coup de sabre” subtype of linear scleroderma is more often associated with systemic morbidity, including ocular ...
Kuo-Liang Chiang +3 more
doaj +1 more source
Linear Scleroderma and Neurological Complications
Pediatric Neurology Briefs, 2006 Three patients with linear scleroderma en coup de sabre who presented with neurologic abnormalities before or concurrent with the dermatologic diagnosis are reported from the Medical College of Wisconsin, Milwaukee, WI.
J Gordon Millichap
doaj +1 more source
British and Irish Orthoptic Journal, 2010 Aim: To present a case of linear scleroderma (LS) involving the extraocular muscles and periorbita with follow-up over an 18-year period. Method: Initial presentation was of a female aged 9 years with progressive left unilateral ptosis which ultimately
Claire Taylor +2 more
doaj +1 more source
Extragenital lichen sclerosus et atrophicus
Indian Journal of Dermatology, 2015 Lichen sclerosus et atrophicus (LSA) is a chronic inflammatory dermatosis with anogenital and extragenital presentations. Extragenital lichen sclerosus is most common on the neck, shoulders and upper trunk. Linear lesions are uncommon in LSA. We report a
Leelavathy Ganesan +3 more
doaj +1 more source
Face Lesions in En Coup De Sabre Scleroderma in Children: Modern Treatment and Outcomes Improvement
Вопросы современной педиатрии, 2022 Localized scleroderma (LS) is an inflammatory sclerosing disease of the skin and subcutaneous tissues associated with its atrophy. Commonly, LS is a benign self-limited disease, although, the chronic form of this disease is recurrent.
Nikolay N. Murashkin +2 more
doaj +1 more source
Neurology International, 2016 We describe a case of Parry Romberg syndrome/ en coupe de sabre in a woman whose disease started as seizures at age 8 but was diagnosed at the age 39.
Karan Seegobin +4 more
doaj +1 more source