Results 51 to 60 of about 2,884 (194)

The Mechanobiology of Endothelial-to-Mesenchymal Transition in Cardiovascular Disease. [PDF]

, 2021
Endothelial cells (ECs) lining the cardiovascular system are subjected to a highly dynamic microenvironment resulting from pulsatile pressure and circulating blood flow.
Boström, Kristina, Di Carlo, Dino, Hsu, Jeffrey, Islam, Shahrin, Simmons, Craig, Tintut, Yin, Yao, Yucheng   +6 more
core   +1 more source

Natural history of valve disease in patients with mucopolysaccharidosis II and the impact of enzyme replacement therapy

Journal of Inherited Metabolic Disease, Volume 48, Issue 1, January 2025.
Abstract Mucopolysaccharidosis II (MPS II, Hunter syndrome) is a rare, X‐linked lysosomal storage disease caused by reduced activity of iduronate‐2‐sulfatase (I2S), with subsequent cellular accumulation of the glycosaminoglycans (GAGs), heparan sulfate, and dermatan sulfate (DS).
Christoph Kampmann, Christina Lampe, Christiane M. Wiethoff, Laila Arash‐Kaps, Eugen Mengel, Joerg Reinke, Michael Beck, Julia B. Hennermann, Tariq Abu‐Tair   +8 more
wiley   +1 more source

Endocardial fibroelastosis causing sudden death in an infant: Autopsy case report of an unusual lesion

Indian Journal of Pathology and Microbiology
Endocardial fibroelastosis is characterized by proliferation of both elastic and collagenous fibers within the endocardium, causing diffuse or localized thickening.
Bhavya P. Mohan, V. K. Rajendraprasad, K. S. Parthasarathy, Togy Thomas Zacharia   +3 more
doaj   +1 more source

Maternal and infant outcomes of pregnancy associated with anti-SSA/RO antibodies: a systematic review and meta-analysis

Pediatric Rheumatology Online Journal, 2023
Objective The relationship between anti-SSA/RO antibodies and pregnancy has been reported previously, and we aim to visualize the rates of maternal and infant outcomes with anti-SSA/RO.
Xiangrui Sheng, Xiaohui Song, Yue Xiong, Tian Ren, Xin Chang, Jian Wu, Jing Cao, Tao Cheng, Mingjun Wang   +8 more
doaj   +1 more source

Transposition of the Great Arteries With Intact Ventricular Septum and Fetal‐Onset Dilated Cardiomyopathy in a Neonate With a Homozygous NEXN Variant

Case Reports in Pediatrics, Volume 2025, Issue 1, 2025.
NEXN variants have previously been described as a cause of both pediatric‐ and adult‐onset dilated cardiomyopathy but are not known to be associated with complex congenital heart disease. We report a case of an antenatal diagnosis of transposition of the great arteries with intact ventricular septum and fetal‐onset dilated cardiomyopathy in a neonate ...
Daniel Geer, Emma Wakeling, Ewa Goljan, Hannah Robinson, Justine Swain, Craig Laurence, Nikhat Kaura   +6 more
wiley   +1 more source

Resolution of Neonatal Hypertrophic Cardiomyopathy Presumed Secondary to Acquired Maternal Ribonucleoprotein and Smith Autoantibodies

American Journal of Perinatology Reports, 2013
Severe asymmetrical hypertrophic cardiomyopathy without heart block accompanied by neuromuscular hypotonia and feeding difficulties was evident shortly after birth in the second child of a mother with systemic lupus erythematosus who had no indication of
A. Shah, A. Winrow, R. Fulljames, N. Naqvi, R. A. Bansal, A. S. Bansal   +5 more
doaj   +1 more source

Impact of early detection and steroid treatment on fetal ventricular heart rate and pacemaker implantation in anti‐Ro/SSA positive congenital heart block

Acta Obstetricia et Gynecologica Scandinavica, Volume 103, Issue 12, Page 2433-2441, December 2024.
Ventricular heart rate (HR) in fetal immune‐mediated third‐degree atrioventricular block (AVB III) is higher at diagnosis than later in gestation and has also been shown to decrease as a function of gestation. Our data confirms that AVB III cases detected earlier in gestation have a higher HR, and suggests that this higher HR can be successfully ...
Sven‐Erik Sonesson, Aurelie Ambrosi, Felicia Nordenstam, Håkan Eliasson, Marie Wahren‐Herlenius   +4 more
wiley   +1 more source

Aortic, mitral and tricuspid valvular dysplasia in a 7‐month‐old colt

Equine Veterinary Education, Volume 36, Issue 11, Page e288-e294, November 2024.
Summary A 7‐month‐old Warmblood cross colt was presented for the assessment of a laceration of the right hind pastern of 4‐days duration. At presentation, the colt was in poor body condition and had a rough, dull coat. Cardiac auscultation revealed a grade 5/6 pansystolic murmur on the left side and grade 4/6 continuous murmur on the left and right ...
Jillian Bell, Patrick Shearer, Josephine Hale, Kristopher J. Hughes   +3 more
wiley   +1 more source

Histopathologic, Immunohistochemical Features and Profile of Viral Antigens in Patients with Myocarditis [PDF]

, 2015
We studied medical records and endomyocardial biopsies of patients with morphological confirmed lymphocytic myocarditis. The patients were divided into two groups: 1 - patients with arrhythmias; group 2 - patients with predominance syndrome heart failure.
Botalov, Roman, Rogovskaya, Yuliya V., Ryabov, Vyacheslav V.   +2 more
core   +2 more sources

Postnatal outcome following fetal aortic valvuloplasty for critical aortic stenosis

Ultrasound in Obstetrics &Gynecology, Volume 64, Issue 3, Page 339-347, September 2024.
ABSTRACT Objective To report our experience of fetal aortic valvuloplasty (FAV) for critical aortic stenosis (AS), with a focus on the postnatal evolution of the patients. Methods This was a retrospective study including all fetuses with critical AS which underwent FAV in a single center between January 2011 and June 2022.
R. Corroenne, M. Meot, L. J. Salomon, I. Szezepanski, H. Baghdadi, B. Stos, M. Levy, J. Le Bidois, D. Laux, R. Gaudin, O. Raisky, Y. Ville, D. Bonnet, J. Stirnemann, S. Malekzadeh‐Milani   +14 more
wiley   +1 more source