Results 11 to 20 of about 12,403 (234)

Eosinophilic Granulomatosis With Polyangiitis: Dissecting the Pathophysiology [PDF]

Frontiers in Medicine, 2021
Eosinophilic Granulomatosis with Polyangiitis (EGPA) is a rare multisystemic disease classified both amongst hypereosinophilic disorders and ANCA-associated vasculitis.
Bello, F., Emmi, G., Fagni, F.
core   +2 more sources

Eosinophilic Granulomatosis with Polyangiitis

New England Journal of Medicine, 2022
A 42-year-old man presented with red, painful eyes, facial-nerve palsy on the left side, a large oral ulcer, and petechiae. Tests for antibodies against perinuclear antineutrophil cytoplasmic antibody and proteinase 3 were positive. Skin biopsy revealed leukocytoclastic vasculitis with perivascular eosinophils.
Geng-Yi Yong, Amelia L.-S. Lim
  +11 more sources

Mepolizumab versus benralizumab for eosinophilic granulomatosis with polyangiitis (EGPA): A European real-life retrospective comparative study [PDF]

Journal of Autoimmunity
BACKGROUND Following the results of the MANDARA trial, this real-life study aimed at comparing the effectiveness and safety profile of mepolizumab versus benralizumab in a European EGPA cohort.
Negrini, Simone, Roccatello, Dario
core   +2 more sources

Genome-wide association study of eosinophilic granulomatosis with polyangiitis reveals genomic loci stratified by ANCA status

Nature Communications, 2019
Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare inflammatory disorder characterised by asthma, eosinophilia and vasculitis. Here, the authors describe a genome-wide association study of EGPA that reveals clinical and genetic differences ...
Paul A Lyons, James E Peters, Federico Alberici, James Liley, Richard M. R. Coulson, William Astle, Chiara Baldini, Francesco Bonatti, Maria C Cid, Heather Elding, Giacomo Emmi, Jörg Epplen, Loïc Guillevin, David R. W. Jayne, Tao Jiang, Iva Gunnarsson, Peter Lamprecht, Stephen Leslie, Mark A. Little, Davide Martorana, Frank Moosig, Thomas Neumann, Sophie Ohlsson, Stefanie Quickert, Giuseppe A. Ramirez, Barbara Rewerska, Georg Schett, Renato A. Sinico, Wojciech Szczeklik, Vladimir Tesar, Damjan Vukcevic, The European Vasculitis Genetics Consortium, Benjamin Terrier, Richard A Watts, Augusto Vaglio, Julia U Holle, Chris Wallace, Kenneth G. C. Smith   +37 more
doaj   +2 more sources

Eozinofilna granulomatoza s poliangiitisom izazvana montelukastom [PDF]

Acta Clinica Croatica
Leukotriene receptor antagonists are a class of drugs used in maintenance therapy of asthma. Among the adverse effects induced by them, particularly by montelukast, is eosinophilic granulomatosis with polyangiitis (EGPA), which manifests as a form of ...
Bocsan, Ioana Corina, Buzoianu, Anca Dana, Grama, Paul, Ureche, Corina, Zah, Corina Adelina   +4 more
core   +5 more sources

Prevasculitic Eosinophilic Granulomatosis With Polyangiitis [PDF]

Cureus, 2021
Eosinophilic granulomatosis with polyangiitis (EGPA) is an exceptionally rare systemic necrotizing vasculitis. The disease is clinically characterized by asthma with concomitant blood and tissue eosinophilia, often progressing to eosinophilic vasculitis. From the onset of asthma, there is usually a three to nine year delay of EGPA diagnosis.
Burtson, Kathryn M, Bishop, Jonathan
openaire   +2 more sources

Wells’ syndrome associated with eosinophilic granulomatosis with polyangiitis − A case report [PDF]

Vojnosanitetski Pregled, 2021
Introduction. Wells` syndrome (eosinophilic cellulitis) is a chronic, recurrent disease characterized by episodes of erythematous and edematous plaques or nodules with occasional development of hemorrhagic bullae on the trunk and limbs.
Radević Tatjana, Kandolf-Sekulović Lidija, Ristić Gorica G., Mijušković Željko P.   +3 more
doaj   +1 more source

Overlapping forms of granulomatosis with polyangiitis and eosinophilic granulomatosis with polyangiitis: Insights from a European multicenter study. [PDF]

J Intern Med
Background Granulomatosis with polyangiitis (GPA) and eosinophilic granulomatosis with polyangiitis (EGPA) are distinct forms of antineutrophil cytoplasm antibody (ANCA)‐associated vasculitis (AAV).
Pallotti F, Mettler C, Papo M, Iudici M, Padoan R, Sorin B, Regola F, Franceschini F, Moiseev S, Novikov P, Piga MA, Moroncini G, Brix SR, Kafagi AH, Deshayes S, Aouba A, Campagne J, Delvino P, Tervaert JWC, Brussino L, Michaud M, Venhoff N, Alberici F, Iannone C, Rosenstingl S, Moutel M, Galempoix JM, Cottin V, Jaccard C, Riehl D, Legendre P, Billet AC, Parronchi P, Quartuccio L, Teixeira V, Egan A, Jayne D, Tombetti E, Caminati M, Pagnoux C, Regent A, Ruivard M, Guillevin L, Puéchal X, Terrier B, French Vasculitis Study Group (FVSG).   +45 more
europepmc   +3 more sources

2022 American College of Rheumatology/European Alliance of Associations for Rheumatology Classification Criteria for Eosinophilic Granulomatosis with Polyangiitis

Annals of the Rheumatic Diseases, 2022
Objective To develop and validate revised classification criteria for eosinophilic granulomatosis with polyangiitis (EGPA). Methods Patients with vasculitis or comparator diseases were recruited into an international cohort.
P. Grayson, C. Ponte, R. Suppiah, J. Robson, A. Craven, A. Judge, S. Khalid, A. Hutchings, R. Luqmani, R. Watts, P. Merkel   +10 more
semanticscholar   +1 more source

Eosinophilic Granulomatosis with Polyangiitis

, 2018
Eosinophilic granulomatosis with polyangiitis (EGPA) formerly Churg-Strauss syndrome is an autoimmune disease of small vessel vasculitis characterized by eosinophilic granulomatosis that manifests as asthma, eosinophilia, granuloma formation, and eventual systemic vasculitis.
M. Zakowski, J. Murphy, J. Ross, L. Coleman   +3 more
  +6 more sources