Results 41 to 50 of about 67,511,782 (172)

New Insights into Pathogenesis and Treatment of ANCA-Associated Vasculitis: Autoantibodies and Beyond

Antibodies, 2023
Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis is a group of rare systemic diseases affecting small-caliber vessels. The damage caused by AAV mainly involves the lung and kidneys. AAV includes three different types: granulomatosis with
Marino Paroli, Chiara Gioia, Daniele Accapezzato   +2 more
doaj   +1 more source

Effective Performance of the 2022 American College of Rheumatology/EULAR Classification Criteria for Antineutrophil Cytoplasmic Antibody–Associated Vasculitis in Pediatric Patients: An ARChiVe Study

Arthritis &Rheumatology, EarlyView.
Objective To assess the 2022 American College of Rheumatology (ACR)/EULAR classification criteria for antineutrophil cytoplasmic antibody–associated vasculitis (AAV) in children with chronic small‐to‐medium vessel vasculitis. Methods A cohort of 574 patients, identified by physician's diagnosis (MD‐diagnosis) in A Registry of Childhood Vasculitis, was ...
David A. Cabral, Else S. Bosman, Nick McPhate, Simranpreet K. Mann, Kirandeep K. Toor, Kimberly A. Morishita, Raashid Luqmani, Michael W. Beresford, James Bistolarides, Sarah Campillo, Sirirat Charuvanij, Kathryn Cook, Paul Dancey, Marietta de Guzman, Samundeeswari Deepak, Barbara Eberhard, Melissa Elder, Samuel Gagne, Katie Harrison, Adam Huber, Archana Khan, Susan Kim, Marisa S. Klein‐Gitelman, Tzielan C. Lee, Suzanne C. Li, Neil Martin, Flora McErlane, L. Nandini Moorthy, Alvaro H. Orjuela, Jonathan Park, Phil Riley, Alan M. Rosenberg, Susan Shenoi, Vidya Sivaraman, Sodality Sutnga, Tamara Tanner, Stacey E. Tarvin, Marinka Twilt, Linda Wagner‐Weiner, Rae S. M. Yeung, Kelly L. Brown, for the ARChiVe Investigators Network within the PedVas Initiative   +41 more
wiley   +1 more source

Relationship between serum periostin and disease activity in eosinophilic granulomatosis with polyangiitis.

, 2018
Relationship between serum periostin and disease activity in eosinophilic granulomatosis with polyangiitis.
David Cuthbertson (188652), Nader A. Khalidi (188685), Peter A. Merkel (188721), Simon Carette (188665), Steven R. Ytterberg (188716), Kit Wong (5849114), Christian Pagnoux (676178), Paul A. Monach (188628), Rennie L. Rhee (5849108), Curry L. Koening (5849117), Larry W. Moreland (373814), Carol A. McAlear (5849120), Philip Seo (188695), Cecile T. J. Holweg (5849111), Carol A. Langford (188690), Ulrich Specks (972), Antoine G. Sreih (5849123)   +16 more
core   +1 more source

Onset of eosinophilic granulomatosis with polyangiitis in a patient treated with an IL-5 pathway inhibitor for severe asthma

, 2020
Onset of eosinophilic granulomatosis with polyangiitis in a patient treated with an IL-5 pathway inhibitor for severe ...
Nalin, Francesca, Lunardi, Claudio, Senna, Gianenrico, Maule, Matteo, Caminati, Marco   +4 more
core   +1 more source

A presentation of recurrent cerebral ischemic stroke in eosinophilic granulomatosis with polyangiitis: a case report

Journal of Medical Case Reports
Background Eosinophilic granulomatosis with polyangiitis is characterized as a small vessel vasculitis with the propensity to have a myriad of presentations due to the targeting of several different organ systems. More often than not, it is the pulmonary
Bryan Gregory, Ahmed Dawood Al Mahrizi, Harman Gill, Fatima Mossolem, Song Ang Peng, Randy Rueda, Eunseuk Lee   +6 more
doaj   +1 more source

Refractory diffuse alveolar hemorrhage caused by eosinophilic granulomatosis with polyangiitis in the absence of elevated biomarkers treated successfully by rituximab and mepolizumab: A case report

Respiratory Medicine Case Reports, 2019
Here we report on a 61-year-old man with refractory eosinophilic granulomatosis with polyangiitis (EGPA) who presented with dyspnea. Despite treatment with glucocorticoids, intravenous cyclophosphamide, and plasma exchange, his symptoms worsened despite ...
Akihiro Shiroshita, Kei Nakashima, Shinji Motojima, Masahiro Aoshima   +3 more
doaj   +1 more source

An immunogenetic perspective of ANCA-associated vasculitides

Egyptian Rheumatology and Rehabilitation, 2022
Background Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitides (AAV) are a group of small vessel vasculitides characterized by necrotizan vasculitis and inflammation.
A. Kocaaga, M. Kocaaga
doaj   +1 more source

Benralizumab monotherapy was insufficient to induce remission in patients with active eosinophilic granulomatosis with polyangiitis

Respiratory Medicine Case Reports, 2022
Eosinophils play an important pathogenetic role in the development of eosinophilic granulomatosis with polyangiitis (EGPA). EGPA has long been treated with systemic corticosteroids and immunosuppressive agents.
Osamu Matsuno, Seijiro Minamoto
doaj   +1 more source

Renal involvement in eosinophilic granulomatosis with polyangiitis [PDF]

, 2023
Eosinophilic granulomatosis with polyangiitis (EGPA) is a necrotizing vasculitis, which typically affects small-to medium-sized blood vessels. It is characterized by the presence of tissue infiltrates rich in eosinophils, along with the formation of ...
Fabio Pagni, Marta Calatroni, Vincenzo L’Imperio, Francesco Reggiani, Renato Alberto Sinico   +4 more
core   +1 more source

A case of Eosinophilic Granulomatosis with Polyangiitis (Churg-Strauss, EGPA) presenting with relapsed Mononeuritis multiplex [PDF]

, 2014
We report a case of eosinophilic granulomatosis with polyangiitis (EGPA), a rare multisystem disorder characterized by difficult-to-control asthma, hypereosinophilia and polyneuropathy.
Lydia Iryani Binti Mohamed Khairul Banks
core   +3 more sources